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DDX43 (DEAD (Asp-Glu-Ala-Asp) box polypeptide 43)

Identity

Other namesHAGE (for Helicase AntiGEn)
DKFZp434H2114
HGNC (Hugo) DDX43
Location 6q13
Location_base_pair Starts at 74161006 and ends at 74184003 bp from pter ( according to hg18-Mar_2006)  [Mapping]
Local_order between markers GATA11B08 and D6S284
Note This gene was isolated as a cDNA by applying a subtraction approach named representational difference analysis (RDA). Rhabdomyosarcoma LB23-SAR was used as the source of tester cDNA that was subtracted with driver cDNA, a mixture of human uterus, breast, heart, and colon cDNA.

DNA/RNA

Transcription The transcript is about 2.2 kb. Gene HAGE is weakly transcribed in normal tissues: the level of expression was estimated to represent only 0.2% of the level found in the LB23-SAR reference cell line. The only exception is testis, which shows a level of expression comparable to that of LB23-SAR. Gene HAGE was found to be expressed in 90 out of 383 tumor samples of different histological types, well above the level in normal tissues; about 5% of the positive samples showed a level of expression above 10% of the level of LB23-SAR, and 7% showed a level of expression between 1-10%. Expression of HAGE was induced in fibroblasts after treatment with the demethylating agent, 5-aza-2¹-deoxycytidine.

Protein

Description The largest open reading frame comprises 1,944 nucleotides and encodes a protein of 648 amino acids (72,871 Da). The pKi of the protein is 9.29.
Function Comparison with databases revealed that HAGE shows 55% similarity with the human p68 protein, an ATP-dependent RNA helicase that is a member of the DEAD-box proteins. Four motifs that are present in members of the DEAD box family are conserved in the HAGE protein. However, ATPase and helicase activities of HAGE were not demonstrated.

Mutations

Note No mutation was observed in the HAGE cDNA isolated from LB23-SAR.

Implicated in

Entity Tumors
Note HAGE expression can be induced by demethylating agent 5-azadeoxycytidine, suggesting that demethylation plays a role in the activation of these genes in tumors. Activation of HAGE in tumor cells most likely results therefore from the genome-wide demethylation process that is known to occur in these cells.
Oncogenesis HAGE is not the first case of a DEAD-box protein that is overexpressed in tumors. Moreover, it worth noting that one out of 42 discovered mutated human tumor antigens is produced by a point mutation in a gene named MUM-3. This gene encodes a protein with homology with members of the RNA helicase family. These observations suggest that mutated or overexpressed helicases may contribute to tumoral transformation or progression.
  

External links

Nomenclature
HGNC (Hugo)DDX43   18677
Entrez_Gene (NCBI)DDX43  55510  DEAD (Asp-Glu-Ala-Asp) box polypeptide 43
Cards
AtlasDDX43ID40288ch6q13
GeneCards (Weizmann)DDX43
Ensembl (Hinxton)ENSG00000080007 [Gene_View]  DDX43 [Vega]
AceView (NCBI)DDX43
Genatlas (Paris)DDX43
euGene (Indiana)55510
SOURCE (Stanford)NM_018665
Gene Expression (Array Express) ENSG00000080007
Genomic and cartography
GoldenPath (UCSC)DDX43  -  6q13   chr6:74161006-74184003 +  6q12-q13   [Description]    (hg18-Mar_2006)
EnsemblDDX43 - 6q12-q13 [CytoView]
Mapping of homologs : NCBIDDX43 [Mapview]
OMIM606286   
Gene and transcription
Gene : Genbank (Entrez)AJ278110 AK303324 AK313686 AL136751 AM393499
Reference sequence (RefSeq transcript) :SRSNM_018665
Reference transcript : EntrezNM_018665
RefSeq genomic : SRSAC_000049 AC_000138 NC_000006 NT_007299 NW_001838987 NW_923184
RefSeq genomic : EntrezAC_000049 AC_000138 NC_000006 NT_007299 NW_001838987 NW_923184
Consensus coding sequences : CCDS NCBIDDX43
Cluster EST : UnigeneHs.125507 [ SRS ] Hs.125507 [ NCBI ]
Alternative Splicing : Fast-db (Paris)14443
Protein : pattern, domain, 3D structure
Protein : UniProt/SwissProtQ9NXZ2 (SRS) Q9NXZ2 (Expasy) Q9NXZ2 (Uniprot)
With graphics : InterProQ9NXZ2
Splice isoforms : VarSplice FASTAQ9NXZ2(VarSplice FASTA)
Domaine pattern : Prosite (SRS)DEAD_ATP_HELICASE (PS00039)    HELICASE_ATP_BIND_1 (PS51192)    HELICASE_CTER (PS51194)    KH_TYPE_1 (PS50084)    Q_MOTIF (PS51195)   
Domain pattern : Prosite (Expaxy)DEAD_ATP_HELICASE (PS00039)    HELICASE_ATP_BIND_1 (PS51192)    HELICASE_CTER (PS51194)    KH_TYPE_1 (PS50084)    Q_MOTIF (PS51195)   
Domains : Interpro (SRS)DEAD-like_N    DNA/RNA_helicase_C    DNA/RNA_helicase_DEAD/DEAH_N    Helicase_SF1/SF2_ATP-bd    KH    KH_type_1    KH_type_1_subgr    RNA-helicase_DEAD-box_CS    RNA_helicase_DEAD_Q_motif   
Domains : Interpro (EBI)DEAD-like_N    DNA/RNA_helicase_C    DNA/RNA_helicase_DEAD/DEAH_N    Helicase_SF1/SF2_ATP-bd    KH    KH_type_1    KH_type_1_subgr    RNA-helicase_DEAD-box_CS    RNA_helicase_DEAD_Q_motif   
Related proteins : CluSTrQ9NXZ2
Domain families : Pfam SRSDEAD (PF00270)    Helicase_C (PF00271)    KH_1 (PF00013)   
Domain families : Pfam SangerDEAD (PF00270)    Helicase_C (PF00271)    KH_1 (PF00013)   
Domain families : Pfam NCBIpfam00270    pfam00271    pfam00013   
Domain families : Smart EMBLDEXDc (SM00487)  HELICc (SM00490)  KH (SM00322)  
Blocks (Seattle)Q9NXZ2
Crystal structure of protein : PDB SRS
Crystal structure of protein : PDBSum
Crystal structure of protein : IMB
Crystal structure of protein : PDB RSDB
HPRD10448
Protein Interaction databases
DIP (DOE-UCLA)Q9NXZ2
IntAct (EBI)Q9NXZ2
Polymorphism : SNP, mutations, diseases
Single Nucleotide Polymorphism (SNP) : dbSNP NCBIDDX43
SNP : GeneSNP UtahDDX43
SNP : HGBaseDDX43
Genetic variants : HAPMAPDDX43
Somatic Mutations in Cancer : COSMICDDX43 
Mutations and Diseases : HGMDDDX43
Hereditary diseases : OMIM606286   
Hereditary diseases : GENETests606286   
Diseases : Genetic AssociationDDX43
General knowledge
Homologs : HomoloGeneDDX43
Homology/Alignments : Family Browser UCSCDDX43
Phylogenetic Trees/Animal Genes : TreeFamDDX43
Catalytic activity : Enzyme3.6.1.- [ Enzyme-Expasy ]   3.6.1.- [ Enzyme-SRS ]   3.6.1.- [ IntEnz-EBI ]   3.6.1.- [ BRENDA ]   3.6.1.- [ KEGG ]   
Chemical/Protein Interactions : CTD55510
Keywords Ontology : AmiGOnucleotide binding  RNA binding  ATP-dependent RNA helicase activity  helicase activity  ATP binding  intracellular  hydrolase activity  
Keywords Ontology : EGO-EBInucleotide binding  RNA binding  ATP-dependent RNA helicase activity  helicase activity  ATP binding  intracellular  hydrolase activity  
Pathways : BIOCARTA
Pathways : KEGG
Other databases
Probes
Probes : ImagenesDDX43 Related clones (RZPD - Berlin)
Literature
PubMed12 Pubmed reference(s) in Entrez
PubGeneDDX43

Bibliography

Identification on a human sarcoma of two new genes with tumor-specific expression.
Martelange V, De Smet C, De Plaen E, Lurquin C, Boon T
Cancer research. 2000 ; 60 (14) : 3848-3855.
PMID 10919659
 
High frequency of autologous anti-melanoma CTL directed against an antigen generated by a point mutation in a new helicase gene.
Baurain JF, Colau D, van Baren N, Landry C, Martelange V, Vikkula M, Boon T, Coulie PG
Journal of immunology (Baltimore, Md. : 1950). 2000 ; 164 (11) : 6057-6066.
PMID 10820291
 
Frequent expression of HAGE in presentation chronic myeloid leukaemias.
Adams SP, Sahota SS, Mijovic A, Czepulkowski B, Padua RA, Mufti GJ, Guinn BA
Leukemia : official journal of the Leukemia Society of America, Leukemia Research Fund, U.K. 2002 ; 16 (11) : 2238-2242.
PMID 12399967
 
Analysis of the tumour suppressor genes, FHIT and WT-1, and the tumour rejection genes, BAGE, GAGE-1/2, HAGE, MAGE-1, and MAGE-3, in benign and malignant neoplasms of the salivary glands.
Nagel H, Laskawi R, Eiffert H, Schlott T
Molecular pathology : MP. 2003 ; 56 (4) : 226-231.
PMID 12890744
 
REVIEW articlesautomatic search in PubMed
Last year publicationsautomatic search in PubMed

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Contributor(s)

Written01-2007Etienne De Plaen

Citation

This paper should be referenced as such :
De Plaen E . DDX43 (DEAD (Asp-Glu-Ala-Asp) box polypeptide 43). Atlas Genet Cytogenet Oncol Haematol. January 2007 .
URL : http://AtlasGeneticsOncology.org/Genes/DDX43ID40288ch6q13.html

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