Myeloid malignancies Section Editor - Robert S. Ohgami ( rohgami@stanford.edu )

Table of Content Classification of acute myeloid leukemias Classification of myelodysplasic syndromes 1999 Classification of myelodysplasic syndromes 2015   Acute basophilic leukemia Acute Erythroid leukaemias Acute megakaryoblastic leukemia (AMegL) Acute myeloid leukemia with myelodysplasia related changes Acute promyelocytic leukemia (APL) Acute promyelocytic leukemia (APL) PML/RARA Agnogenic myeloid metaplasia Atypical Chronic Myeloid Leukemia (aCML) Biphenotypic Acute Leukaemia (BAL) Blastic Plasmacytoid Dendritic Cell Neoplasm (BPDCN) Childhood myelodysplastic syndromes Chronic Eosinophilic Leukemia-Not Otherwise Specified (CEL-NOS) Chronic myelogenous leukaemia (CML) Chronic Myelomonocytic Leukemia (CMML) Congenital leukaemias Essential Thrombocythemia (ET) Idiopathic Hypereosinophilic Syndrome (IHES) Idiopathic myelofibrosis Infant leukaemias Juvenile Chronic Myelogenous Leukemia (JCML) M0 acute myeloid leukemia (M0-AML) M3/M3v acute myeloid leukemia (AML M3/M3v) M7 acute myeloid leukemia (M7-AML) Mixed phenotype acute leukemia (MPAL) Monosomal karyotype (MK) in myeloid malignancies Myelodysplastic/myeloproliferative neoplasms Myelodysplastic/myeloproliferative neoplasm with ring sideroblasts and thrombocytosis (MDS/MPN-RS-T) Myelodysplastic syndrome with excess blasts Myelofibrosis with Myeloid Metaplasia (MMM) Myeloid/Lymphoid neoplasms with abnormalities of PDGFRA Myeloid/Lymphoid neoplasms with abnormalities of PDGFRB Myeloid sarcoma Neonatal leukaemias Polycythemia Vera (PV) Refractory anemia (RA) Refractory anemia with excess blasts (RAEB) in 2003 Refractory anemia with ringed sideroblasts (RARS) Systemic mast cell disease (SMCD) t(X;6)(p11;q23) MYB/GATA1

Phylum and Thesaurus of Hematological malignancies (full table) detailed description ICD-O3 code Myeloproliferative neoplasms   Chronic myelogenous leukaemia, BCR-ABL1 positive 9975/3 Chronic neutrophilic leukaemia 9963/3 Polycythaemia vera 9950/3 Primary myelofibrosis 9961/3 Essential thrombocythaemia 9962/3 Chronic eosinophilic leukaemia, NOS 9964/3 Cutaneous mastocytosis 9740/3 Systemic mastocytosis 9741/3 Mast cell leukaemia 9742/3 Mast cell sarcoma 9740/3 Extracutaneous mastocytoma 9740/1 Myeloproliferative neoplasm, unclassifiable 9975/3 Myeloid and lymphoid neoplasms with eosinophilia and abnormalities of PDGFRA, PDGFRB or FGFR1   Myeloid and lymphoid neoplasms with PDGFRA rearrangement 9965/3 Myeloid and lymphoid neoplasms with PDGFRB rearrangement 9966/3 Myeloid and lymphoid neoplasms with FGFR1 rearrangement 9967/3 Myelodysplastic/myeloproliferative neoplasms   Chronic myelomonocytic leukaemia 9945/3 Atypical chronic myeloid leukaemia, BCR-ABL1 negative 9876/3 Juvenile myelomonocytic leukaemia 9946/3 Myelodysplastic/myeloproliferative neoplasm, unclassifiable 9975/3 Refractory anemia with ring sideroblasts associated with marked thrombocytosis 9982/3 Myelodysplastic syndromes   Refractory anemia 9980/3 Refractory neutropenia 9991/3 Refractory thrombocytopemia 9992/3 Refractory anaemia with ring sideroblasts 9982/3 Refractory cytopenia with multilineage dysplasia 9985/3 Refractory anaemia with excess blasts 9983/3 Myelodysplastic syndrome with isolated del(5q) 9986/3 Myelodysplastic syndrome, unclassifiable 9989/3 Childhood myelodysplastic syndrome NS Refractory cytopenia of childhood 9985/3 Acute myeloid leukaemia (AML) and related precursor neoplasms   AML with t(8;21)(q22;q22); RUNX1-RUNX1T1 9896/3 AML with inv(16)(p13.1q22) or t(16;16)(p13.1;q22); CBFB-MYH11 9871/3 Acute promyelocytic leukaemia with t(15;17)(q22;q12); PML-RARA 9866/3 AML with t(9;11)(p22;q23); MLLT3-MLL 9897/3 AML with t(6;9)(p23;q34); DEK-NUP214v 9865/3 AML with inv(3)(q21q26.2) or t(3;3)(q21;q26.2);RPN1-EVI1 9869/3 AML (megakaryoblastic) with t(1;22)(p13;q13);RBM15-MKL1 9911/3 AML with mutated NPM1 9861/3 AML with mutated CEBPA 9861/3 AML with myelodysplasia-related changes 9895/3 Therapy-related myeloid neoplasms 9920/3 Acute myeloid leukaemia, NOS 9861/3 AML with minimal differentiation 9872/3 AML without maturation 9873/3 AML with maturation 9874/3 Acute myelomonocytic leukaemia 9867/3 Acute monoblastic and monocytic leukaemia 9891/3 Acute erythroid leukaemia 9840/3 Acute megakaryoblastic leukaemia 9910/3 Acute basophilic leukaemia 9870/3 Acute panmyelosis with myelofibrosis 9931/3 Myeloid sarcoma 9872/3 Transient abnormal myelopoiesis 9898/1 Myeloid leukaemia associated with Down syndrome 9898/3 Blastic plasmacytoid dendritic cell neoplasm 9727/3 Acute leukaemias of ambiguous lineage   Acute undifferentiated leukaemia 9801/3 Mixed phenotype acute leukaemia with t(9;22)(q34;q11.2); BCR-ABL1 9806/3 Mixed phenotype acute leukaemia with t(v;11q23); MLL rearranged 9807/3 Mixed phenotype acute leukaemia, B/myeloid, NOS 152 9808/3 Mixed phenotype acute leukaemia, T/myeloid, NOS 153 9809/3 Mixed phenotype acute leukaemia, NOS - rare types NS Other ambiguous lineage leukaemias NS Natural killer (NK)-cell lymphoblastic leukaemia/lymphoma NS

© Atlas of Genetics and Cytogenetics in Oncology and Haematology

indexed on : Thu Feb 14 18:21:58 CET 2019