GUCY2D (guanylate cyclase 2D, retinal)

2006-10-01  

Identity

HGNC
LOCATION
17p13.1
LOCUSID
ALIAS
CACD1,CG-E,CORD5,CORD6,CSNB1I,CYGD,GUC1A4,GUC2D,LCA,LCA1,RCD2,RETGC-1,ROS-GC1,ROSGC,retGC

Other Information

Locus ID:

NCBI: 3000
MIM: 600179
HGNC: 4689
Ensembl: ENSG00000132518

Variants:

dbSNP: 3000
ClinVar: 3000
TCGA: ENSG00000132518
COSMIC: GUCY2D

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000132518ENST00000254854Q02846

Expression (GTEx)

0
1
2
3

Pathways

PathwaySourceExternal ID
Purine metabolismKEGGko00230
Olfactory transductionKEGGko04740
Purine metabolismKEGGhsa00230
Olfactory transductionKEGGhsa04740
PhototransductionKEGGko04744
PhototransductionKEGGhsa04744
Signal TransductionREACTOMER-HSA-162582
Visual phototransductionREACTOMER-HSA-2187338
The phototransduction cascadeREACTOMER-HSA-2514856
Inactivation, recovery and regulation of the phototransduction cascadeREACTOMER-HSA-2514859

References

Pubmed IDYearTitleCitations
365099962023Phenotypic characterization of autosomal dominant progressive cone dystrophies associated with a heterozygous variant c.2512C>T of GUCY2D gene in a large kindred.0
373279592023Comprehensive Genotyping and Phenotyping Analysis of GUCY2D-Associated Rod- and Cone-Dominated Dystrophies.2
377756462023A natural history study of autosomal dominant GUCY2D-associated cone-rod dystrophy.0
365099962023Phenotypic characterization of autosomal dominant progressive cone dystrophies associated with a heterozygous variant c.2512C>T of GUCY2D gene in a large kindred.0
373279592023Comprehensive Genotyping and Phenotyping Analysis of GUCY2D-Associated Rod- and Cone-Dominated Dystrophies.2
377756462023A natural history study of autosomal dominant GUCY2D-associated cone-rod dystrophy.0
364902682022The impact of modifier genes on cone-rod dystrophy heterogeneity: An explorative familial pilot study and a hypothesis on neurotransmission impairment.26
364902682022The impact of modifier genes on cone-rod dystrophy heterogeneity: An explorative familial pilot study and a hypothesis on neurotransmission impairment.26
336707722021Leber Congenital Amaurosis Due to GUCY2D Mutations: Longitudinal Analysis of Retinal Structure and Visual Function.5
340487772021Novel variants in GUCY2D causing retinopathy and the genotype-phenotype correlation.3
344709212021Homozygosity mapping coupled with whole-exome sequencing and protein modelling identified a novel missense mutation in GUCY2D in a consanguineous Pakistani family with Leber congenital amaurosis.1
345372442021Retinal degeneration-3 protein attenuates photoreceptor degeneration in transgenic mice expressing dominant mutation of human retinal guanylyl cyclase.4
336707722021Leber Congenital Amaurosis Due to GUCY2D Mutations: Longitudinal Analysis of Retinal Structure and Visual Function.5
340487772021Novel variants in GUCY2D causing retinopathy and the genotype-phenotype correlation.3
344709212021Homozygosity mapping coupled with whole-exome sequencing and protein modelling identified a novel missense mutation in GUCY2D in a consanguineous Pakistani family with Leber congenital amaurosis.1

Citation

Dessen P

GUCY2D (guanylate cyclase 2D, retinal)

Atlas Genet Cytogenet Oncol Haematol. 2006-10-01

Online version: http://atlasgeneticsoncology.org/gene/43304/gucy2d