SCN8A (sodium voltage-gated channel alpha subunit 8)

2009-05-01  

Identity

HGNC
LOCATION
12q13.13
LOCUSID
ALIAS
BFIS5,CERIII,CIAT,DEE13,EIEE13,MED,MYOCL2,NaCh6,Nav1.6,PN4
FUSION GENES

Other Information

Locus ID:

NCBI: 6334
MIM: 600702
HGNC: 10596
Ensembl: ENSG00000196876

Variants:

dbSNP: 6334
ClinVar: 6334
TCGA: ENSG00000196876
COSMIC: SCN8A

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000196876ENST00000354534Q9UQD0
ENSG00000196876ENST00000548086A0A590UJP2
ENSG00000196876ENST00000551216F8W0Q0
ENSG00000196876ENST00000636945A0A1B0GVM8
ENSG00000196876ENST00000637709A0A1B0GVD4
ENSG00000196876ENST00000638820A0A1W2PQI5
ENSG00000196876ENST00000667214A0A590UK68
ENSG00000196876ENST00000668547A0A590UK43

Expression (GTEx)

0
5
10
15
20
25
30

Pathways

PathwaySourceExternal ID
Muscle contractionREACTOMER-HSA-397014
Developmental BiologyREACTOMER-HSA-1266738
Axon guidanceREACTOMER-HSA-422475
L1CAM interactionsREACTOMER-HSA-373760
Interaction between L1 and AnkyrinsREACTOMER-HSA-445095
Cardiac conductionREACTOMER-HSA-5576891
Phase 0 - rapid depolarisationREACTOMER-HSA-5576892

References

Pubmed IDYearTitleCitations
382337702024Expanding the genotype-phenotype spectrum in SCN8A-related disorders.0
382893382024Coupling of Slack and Na(V)1.6 sensitizes Slack to quinidine blockade and guides anti-seizure strategy development.0
383115552024[Clinical features and genetic analysis of five children with epilepsies due to variants of SCN8A gene].0
382337702024Expanding the genotype-phenotype spectrum in SCN8A-related disorders.0
382893382024Coupling of Slack and Na(V)1.6 sensitizes Slack to quinidine blockade and guides anti-seizure strategy development.0
383115552024[Clinical features and genetic analysis of five children with epilepsies due to variants of SCN8A gene].0
375853672023Clinical severity is correlated with age at seizure onset and biophysical properties of recurrent gain of function variants associated with SCN8A-related epilepsy.1
375853672023Clinical severity is correlated with age at seizure onset and biophysical properties of recurrent gain of function variants associated with SCN8A-related epilepsy.1
344319992022Genotype-phenotype correlations in SCN8A-related disorders reveal prognostic and therapeutic implications.39
353483082022Commonalities and distinctions between two neurodevelopmental disorder subtypes associated with SCN2A and SCN8A variants and literature review.2
357531352022Nav1.6 promotes the progression of human follicular thyroid carcinoma cells via JAK-STAT signaling pathway.6
344319992022Genotype-phenotype correlations in SCN8A-related disorders reveal prognostic and therapeutic implications.39
353483082022Commonalities and distinctions between two neurodevelopmental disorder subtypes associated with SCN2A and SCN8A variants and literature review.2
357531352022Nav1.6 promotes the progression of human follicular thyroid carcinoma cells via JAK-STAT signaling pathway.6
334288242021Gain-of-function mutation Met136Val in SCN8A may not be a common cause of trigeminal neuralgia.1

Citation

Dessen P

SCN8A (sodium voltage-gated channel alpha subunit 8)

Atlas Genet Cytogenet Oncol Haematol. 2009-05-01

Online version: http://atlasgeneticsoncology.org/gene/50930/scn8a