| 9540/0 | Neurofibroma, NOS |
| | Nervous System: Neurofibroma |
| 9540/1 | Neurofibromatosis, NOS |
| | Multiple neurofibromatosis |
| | Von Recklinghausen disease (except of bone) |
| | Recklinghausen disease (except of bone) |
| 9540/3 | Malignant peripheral nerve sheath tumor |
| | MPNST, NOS |
| | Neurofibrosarcoma [obs] |
| | Neurogenic sarcoma [obs] |
| | Neurosarcoma [obs] |
| | MPNST with glandular differentiation |
| | Epithelioid MPNST |
| | MPNST with mesenchymal differentiation |
| | Melanotic MPNST |
| | Melanotic psammomatous MPNST |
| 9541/0 | Melanotic neurofibroma |
| 9550/0 | Plexiform neurofibroma |
| | Plexiform neuroma |
| 9560/0 | Neurilemoma, NOS |
| | Schwannoma, NOS |
| | Neurinoma |
| | Acoustic neuroma (C72.4) |
| | Pigmented schwannoma |
| | Melanotic schwannoma |
| | Plexiform schwannoma |
| | Cellular schwannoma |
| | Degenerated schwannoma |
| | Ancient schwannoma |
| | Psammomatous schwannoma |
| 9560/1 | Neurinomatosis |
| 9560/3 | Neurilemoma, malignant [obs] |
| | Malignant schwannoma, NOS [obs] |
| | Neurilemosarcoma [obs] |
| 9561/3 | Malignant peripheral nerve sheath tumor with rhabdomyoblastic differentation |
| | MPNST with rhabdomyoblastic differentiation |
| | Triton tumor, malignant |
| | Malignant schwannoma with rhabdomyoblastic differentiation |
| 9562/0 | Neurothekeoma |
| | Nerve sheath myxoma |
| 9570/0 | Neuroma, NOS |
| 9571/0 | Perineurioma, NOS |
| | Intraneural perineurioma |
| | Soft tissue perineurioma |
| 9571/3 | Perineurioma, malignant |
| | Perineural MPNST |