Atlas classification and Phylum | Atlas_ID | ICD-O3_TOPO (code) | ICD-O3_TOPO (organ) | ICD-O3_MORPH (short code) | Pathology basic description | ICD-O3_MORPH (complete code) | ICD-O3_MORPH (detailed pathology) |
Soft Tissues: an Overview |
5042 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
|
|
|
|
Soft Tissues: Adipocytic tumors |
6376 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
|
|
|
|
Soft Tissues: Benign Lipomatous (Lipoma, Lipoblastoma, Angiolipoma, Chondroid lipoma, Spindle cell lipoma/Pleomorphic lipoma, Hibernoma, Angiomyo-lipoma) |
5050 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
|
|
|
|
Soft Tissues: Benign Lipomatous: Angiolipoma |
5163 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
886 |
ANGIOLIPOMA |
8861/0 |
Angiolipoma |
Soft Tissues: Benign Lipomatous: Angiomyo-lipoma |
5134 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
886 |
ANGIOLIPOMA |
8860/0 |
Extrarenal angiomyolipoma |
Soft Tissues: Benign Lipomatous: Chondroid lipoma |
5164 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
886 |
ANGIOLIPOMA |
8862/0 |
Chondroid lipoma |
Soft Tissues: Benign Lipomatous: Chondrolipoangioma |
5417 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
|
|
|
|
Soft Tissues: Benign Lipomatous: Hibernoma |
5166 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
888 |
- |
8880/0 |
Hibernoma |
Soft Tissues: Benign Lipomatous: Lipoblastoma |
5155 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
888 |
- |
8881/0 |
Lipoblastoma / Lipoblastomatosis |
Soft Tissues: Benign Lipomatous: Lipoblastoma: t(1;8)(p31;q12) |
5666 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
888 |
- |
8881/0 |
Lipoblastoma / Lipoblastomatosis |
Soft Tissues: Benign Lipomatous: Lipoblastoma: t(8;15)(q12;q25) |
5674 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
888 |
- |
8881/0 |
Lipoblastoma / Lipoblastomatosis |
Soft Tissues: Benign Lipomatous: Lipoblastoma: t(8;8)(q11;q12) |
5432 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
888 |
- |
8881/0 |
Lipoblastoma / Lipoblastomatosis |
Soft Tissues: Benign Lipomatous: Lipoma |
5162 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
885 |
LIPOSARCOMA NEOPLASMS |
8850/0 |
Lipoma |
Soft Tissues: Benign Lipomatous: Lipoma: t(12;13)(q14;q13) |
5436 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
885 |
LIPOSARCOMA NEOPLASMS |
8850/0 |
Lipoma |
Soft Tissues: Benign Lipomatous: Lipoma: t(2;12)(q37;q14) |
5437 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
885 |
LIPOSARCOMA NEOPLASMS |
8850/0 |
Lipoma |
Soft Tissues: Benign Lipomatous: Lipoma: t(2;8)(q32-33;q12) |
5668 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
885 |
LIPOSARCOMA NEOPLASMS |
8850/0 |
Lipoma |
Soft Tissues: Benign Lipomatous: Lipoma: t(5;12)(q33;q14) |
5672 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
885 |
LIPOSARCOMA NEOPLASMS |
8850/0 |
Lipoma |
Soft Tissues: Benign Lipomatous: Lipoma: t(9;12)(p22-23;q14) |
5463 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
885 |
LIPOSARCOMA NEOPLASMS |
8850/0 |
Lipoma |
Soft Tissues: Benign Lipomatous: Parosteal Lipoma |
5268 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
|
|
|
|
Soft Tissues: Benign Lipomatous: Spindle cell lipoma/Pleomorphic lipoma |
5165 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
885 |
LIPOSARCOMA NEOPLASMS |
8857/0;8854/0 |
Spindle cell lipoma Pleomorphic lipoma |
Soft Tissues: Chondro-Osseous tumors: Extraskeletal osteosarcoma |
5200 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
918 |
OSTEOSARCOMA, NOS |
9180/3 |
Extraskeletal osteosarcoma |
Soft Tissues: Chondro-Osseous tumors: Soft tissue chondroma |
5199 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
922 |
CHONDROSARCOMA, NOS |
9220/0 |
Soft tissue chondroma |
Soft Tissues: Chondro-Osseous tumors: Soft tissue chondroma: t(3;12)(q27;q15) |
5428 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
|
|
|
|
Soft Tissues: Ectomesenchymoma: t(1;12)(p32;p13) |
6421 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
|
|
|
|
Soft Tissues: Fibroblastic/Myofibroblastic tumors: Adult fibrosarcoma |
5183 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
881 |
FIBROMATOUS NEOPLASMS |
8810/3 |
Fibrosarcoma, NOS |
Soft Tissues: Fibroblastic/Myofibroblastic tumors: Angiofibroma: t(5;8)(p15;q13) |
6395 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
916 |
HEMANGIOBLASTOMA |
9160/0 |
Cellular angiofibroma Giant cell angiofibroma |
Soft Tissues: Fibroblastic/Myofibroblastic tumors: Dermatofibrosarcoma protuberans (Darier Ferrand) |
5059 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
883 |
FIBROUS HISTIOCYTOMA, MAL. |
8832/3 |
Dermatofibrosarcoma, NOS |
Soft Tissues: Fibroblastic/Myofibroblastic tumors: Desmoid-type fibromatoses |
5179 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
882 |
- |
8821/1 |
Desmoid-type fibromatoses |
Soft Tissues: Fibroblastic/Myofibroblastic tumors: Desmoplastic fibroblastoma |
5175 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
881 |
FIBROMATOUS NEOPLASMS |
8810/0 |
Desmoplastic fibroblastoma |
Soft Tissues: Fibroblastic/Myofibroblastic tumors: Elastofibroma |
5173 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
882 |
- |
8820/0 |
Elastofibroma |
Soft Tissues: Fibroblastic/Myofibroblastic tumors: Extrapleural solitary fibrous tumor |
5180 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
881 |
FIBROMATOUS NEOPLASMS |
8815/1 |
Solitary fibrous tumor |
Soft Tissues: Fibroblastic/Myofibroblastic tumors: Fibroma of the tendon sheath |
5174 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
881 |
FIBROMATOUS NEOPLASMS |
8810/0 |
Fibroma of tendon sheath |
Soft Tissues: Fibroblastic/Myofibroblastic tumors: fibromyxoid sarcoma: t(11;16)(p11;p11) |
5473 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
881 |
FIBROMATOUS NEOPLASMS |
8811/3 |
Fibromyxosarcoma |
Soft Tissues: Fibroblastic/Myofibroblastic tumors: Giant cell angiofibroma |
5177 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
916 |
HEMANGIOBLASTOMA |
9160/0 |
Giant cell angiofibroma |
Soft Tissues: Fibroblastic/Myofibroblastic tumors: Hemangiopericytoma |
5181 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
915 |
HEMANGIOPERICYTOMA |
9150/1 |
Hemangiopericytoma, NOS |
Soft Tissues: Fibroblastic/Myofibroblastic tumors: Hemosiderotic fibrolipomatous tumor (HFLT) |
6392 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
|
|
|
|
Soft Tissues: Fibroblastic/Myofibroblastic tumors: Infantile fibrosarcoma: t(12;15) ETV6/NTRK3 |
5182 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
881 |
FIBROMATOUS NEOPLASMS |
8814/3 |
Infantile fibrosarcoma |
Soft Tissues: Fibroblastic/Myofibroblastic tumors: Inflammatory myofibroblastic tumor |
5073 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
882 |
- |
8825/1 |
Inflammatory myofibroblastic tumor |
Soft Tissues: Fibroblastic/Myofibroblastic tumors: Inflammatory myofibroblastic tumor: t(1;2)(q25;p23) |
5129 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
882 |
- |
8825/1 |
Inflammatory myofibroblastic tumor |
Soft Tissues: Fibroblastic/Myofibroblastic tumors: Inflammatory myofibroblastic tumor: t(2;11)(p23;p15) |
5213 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
882 |
- |
8825/1 |
Inflammatory myofibroblastic tumor |
Soft Tissues: Fibroblastic/Myofibroblastic tumors: Inflammatory myofibroblastic tumor: t(2;17)(p23;q23) |
5127 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
882 |
- |
8825/1 |
Inflammatory myofibroblastic tumor |
Soft Tissues: Fibroblastic/Myofibroblastic tumors: Inflammatory myofibroblastic tumor: t(2;19)(p23;p13.1) |
5128 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
882 |
- |
8825/1 |
Inflammatory myofibroblastic tumor |
Soft Tissues: Fibroblastic/Myofibroblastic tumors: Inflammatory myofibroblastic tumor: t(2;2)(p23;q13) |
5214 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
882 |
- |
8825/1 |
Inflammatory myofibroblastic tumor |
Soft Tissues: Fibroblastic/Myofibroblastic tumors: Inflammatory myofibroblastic tumor: t(2;4)(p23;q21) |
5444 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
882 |
- |
8825/1 |
Inflammatory myofibroblastic tumor |
Soft Tissues: Fibroblastic/Myofibroblastic tumors: Low grade fibromyxoid sarcoma |
5185 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
881 |
FIBROMATOUS NEOPLASMS |
8811/3 |
Fibromyxosarcoma |
Soft Tissues: Fibroblastic/Myofibroblastic tumors: Low grade myofibroblastic sarcoma (Myofibrosarcoma) |
6365 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
882 |
- |
8825/3 |
Low grade myofibroblastic sarcoma |
Soft Tissues: Fibroblastic/Myofibroblastic tumors: Mammary-type fibroblastoma |
5176 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
882 |
- |
8825/0 |
Mammary-type myofibroblastoma |
Soft Tissues: Fibroblastic/Myofibroblastic tumors: Myxofibrosarcoma |
5184 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
881 |
FIBROMATOUS NEOPLASMS |
8811/3 |
Fibromyxosarcoma |
Soft Tissues: Fibroblastic/Myofibroblastic tumors: Myxoinflammatory fibroblastic sarcoma (MIFS) |
6390 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
|
|
|
|
Soft Tissues: Fibroblastic/Myofibroblastic tumors: Myxoinflammatory fibroblastic sarcoma: t(1;10)(p22;q24) |
6369 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
|
|
|
|
Soft Tissues: Fibroblastic/Myofibroblastic tumors: Nodular fasciitis |
5171 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
|
|
|
|
Soft Tissues: Fibroblastic/Myofibroblastic tumors: Proliferative fasciitis and proliferative myositis |
5172 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
|
|
|
|
Soft Tissues: Fibroblastic/Myofibroblastic tumors: Sclerosing epitheliod fibrosarcoma |
5186 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
|
|
|
|
Soft Tissues: Fibroblastic/Myofibroblastic tumors: Superficial fibromatoses |
5178 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
|
|
|
|
Soft Tissues: Fibrohistiocytic tumors: Diffuse-type giant cell tumors |
5188 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
925 |
GT. CELL TUMOR OF BONE, MAL. |
9251/0 |
Diffuse-type giant cell tumor |
Soft Tissues: Fibrohistiocytic tumors: Giant cell tumor of tendon sheath |
5187 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
925 |
GT. CELL TUMOR OF BONE, MAL. |
9252/0 |
Giant cell tumor of tendon sheath |
Soft Tissues: Fibrohistiocytic tumors: Giant cell tumor of tendon sheath / of diffuse_type: t(1;2)(p13;q37) voir 5187 et 5188 |
5452 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
|
|
|
|
Soft Tissues: Fibrohistiocytic tumors: Pleomorphic malignant fibrous histiocytoma |
5190 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
883 |
FIBROUS HISTIOCYTOMA, MAL. |
8830/3 |
Fibrous histiocytoma, malignant |
Soft Tissues: Fibrohistiocytic tumors: Plexiform fibrohistiocytic tumor |
5189 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
883 |
FIBROUS HISTIOCYTOMA, MAL. |
8835/1 |
Plexiform fibrohistiocytic tumor |
Soft Tissues: Liposarcoma (Well-differentiated + Myxoid + Pleomorphic) |
5029 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
885 |
LIPOSARCOMA NEOPLASMS |
8850/3 |
Liposarcoma, NOS |
Soft Tissues: Liposarcoma: Atypical lipomatous tumor/Well-differentiated liposarcoma |
5167 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
885 |
LIPOSARCOMA NEOPLASMS |
8851/3 |
Liposarcoma, well differentiated |
Soft Tissues: Liposarcoma: Dedifferentiated liposarcoma |
5168 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
885 |
LIPOSARCOMA NEOPLASMS |
8858/3 |
Dedifferentiated liposarcoma |
Soft Tissues: Liposarcoma: Myxoid liposarcoma |
5169 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
885 |
LIPOSARCOMA NEOPLASMS |
8852/3 |
Myxoid liposarcoma |
Soft Tissues: Liposarcoma: Pleomorphic liposarcoma |
5170 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
885 |
LIPOSARCOMA NEOPLASMS |
8854/3 |
Pleomorphic liposarcoma |
Soft Tissues: Lymphangioleiomyoma |
5868 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
|
|
|
Neoplasms with perivascular epithelioid cell differentiation (PEComa) |
Soft Tissues: melanoma soft parts (Clear cell sarcoma)/t(12;22)(q13;q12) |
5024 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
904 |
SYNOVIAL SARCOMA, NOS |
9044/3 |
Clear cell sarcoma,NOS (except of kidney M-8964/3) |
Soft Tissues: Pericytic (Perivascular) tumors |
5192 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
871 |
PERICYTIC (PERIVASCULAR) TUMOURS |
|
|
Soft Tissues: Skeletal Muscle tumors (Rhabdomyosarcoma) |
5004 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
890 |
RHABDOMYOSARCOMA, NOS |
8900/3 |
Rhabdomyosarcoma, NOS |
Soft Tissues: Skeletal Muscle tumors: Alveolar rhabdomyosarcoma |
5194 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
892 |
ALVEOLAR RHABDOMYOSARCOMA |
8920/3 |
Alveolar rhabdomyosarcoma |
Soft Tissues: Skeletal Muscle tumors: Alveolar rhabdomyosarcoma: t(1;13)(p36;q14) |
5012 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
892 |
ALVEOLAR RHABDOMYOSARCOMA |
8920/3 |
Alveolar rhabdomyosarcoma |
Soft Tissues: Skeletal Muscle tumors: Alveolar rhabdomyosarcoma: t(2;13)(q35;q14) |
5013 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
892 |
ALVEOLAR RHABDOMYOSARCOMA |
8920/3 |
Alveolar rhabdomyosarcoma |
Soft Tissues: Skeletal Muscle tumors: Alveolar rhabdomyosarcoma: t(2;2)(q35;p23) |
5445 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
892 |
ALVEOLAR RHABDOMYOSARCOMA |
8920/3 |
Alveolar rhabdomyosarcoma |
Soft Tissues: Skeletal Muscle tumors: Anaplastic rhabdomyosarcoma |
6290 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
891 |
EMBRYONAL RHABDOMYOSARCOMA |
8910/3 |
Embryonal rhabdomyosarcoma |
Soft Tissues: Skeletal Muscle tumors: Botryoid rhabdomyosarcoma |
6288 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
891 |
EMBRYONAL RHABDOMYOSARCOMA |
8910/3 |
Embryonal rhabdomyosarcoma |
Soft Tissues: Skeletal Muscle tumors: Embryonal rhabdomyosarcoma |
5193 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
891 |
EMBRYONAL RHABDOMYOSARCOMA |
8910/3 |
Embryonal rhabdomyosarcoma |
Soft Tissues: Skeletal Muscle tumors: Embryonal rhabdomyosarcoma: t(4;22)(q35;q12) |
6280 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
891 |
EMBRYONAL RHABDOMYOSARCOMA |
8910/3 |
Embryonal rhabdomyosarcoma |
Soft Tissues: Skeletal Muscle tumors: Pleomorphic rhabdomyosarcoma |
5195 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
890 |
RHABDOMYOSARCOMA, NOS |
8901/3 |
Pleomorphic rhabdomyosarcoma, adult type |
Soft Tissues: Skeletal Muscle tumors: Rhabdomyosarcoma: t(11;22)(q24;q12) |
6285 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
890 |
RHABDOMYOSARCOMA, NOS |
8902/3 |
Mixed type rhabdomyosarcoma |
Soft Tissues: Skeletal Muscle tumors: Spindle cell rhabdomyosarcoma |
6289 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
891 |
EMBRYONAL RHABDOMYOSARCOMA |
8912/3 |
Spindle cell rhabdomyosarcoma |
Soft Tissues: Skeletal Muscle tumors: Undifferentiated rhabdomyosarcoma |
6291 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
|
|
|
|
Soft Tissues: Smooth Muscle tumors: Angioleiomyoma |
5191 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
889 |
MYOMATOUS NEOPLASMS |
8894/0 |
Angioleiomyoma |
Soft Tissues: Smooth Muscle tumors: Leiomyosarcoma |
5122 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
889 |
MYOMATOUS NEOPLASMS |
8890/3 |
Leiomyosarcoma, NOS |
Soft Tissues: t(2;12)(q31.1;q13) EWS-ATF2 in clear cell sarcoma |
5563 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
904 |
SYNOVIAL SARCOMA, NOS |
9044/3 |
Clear cell sarcoma,NOS (except of kidney M-8964/3) |
Soft Tissues: t(2;22)(q33;q12) in clear cell sarcoma |
5522 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
904 |
SYNOVIAL SARCOMA, NOS |
9044/3 |
Clear cell sarcoma,NOS (except of kidney M-8964/3) |
Soft Tissues: Uncertain differentiation: Alveolar soft part sarcoma |
5125 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
958 |
GRANULAR CELL TUMOR |
9581/3 |
Alveolar soft part sarcoma |
Soft Tissues: Uncertain differentiation: Angiomatoid fibrous histiocytoma |
5204 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
883 |
FIBROUS HISTIOCYTOMA, MAL. |
8836/1 |
Angiomatoid fibrous histiocytoma |
Soft Tissues: Uncertain differentiation: Angiomatoid fibrous histiocytoma: t(12;16)(q13;p11) |
6292 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
883 |
FIBROUS HISTIOCYTOMA, MAL. |
8836/1 |
Angiomatoid fibrous histiocytoma |
Soft Tissues: Uncertain differentiation: Angiomatoid fibrous histiocytoma: t(12;22)(q13;q12) |
6286 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
883 |
FIBROUS HISTIOCYTOMA, MAL. |
8836/1 |
Angiomatoid fibrous histiocytoma |
Soft Tissues: Uncertain differentiation: Angiomatoid fibrous histiocytoma: t(2;22)(q34;q12) |
5670 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
883 |
FIBROUS HISTIOCYTOMA, MAL. |
8836/1 |
Angiomatoid fibrous histiocytoma |
Soft Tissues: Uncertain differentiation: Clear cell sarcoma of the soft tissue |
5074 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
904 |
SYNOVIAL SARCOMA, NOS |
9044/3 |
Clear cell sarcoma,NOS (except of kidney M-8964/3) |
Soft Tissues: Uncertain differentiation: Deep 'aggressive' angiomyxoma with t(11;12)(q23;q15) |
5203 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
884 |
MYXOSARCOMA |
8841/0 |
Deep (¥aggressive) angiomyxoma |
Soft Tissues: Uncertain differentiation: Desmoplastic small round cell tumor |
6316 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
880 |
SARCOMA, NOS |
8806/3 |
Desmoplastic small round cell tumor |
Soft Tissues: Uncertain differentiation: Desmoplastic small round cell tumor/t(11;22)(p13;q12) |
5023 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
880 |
SARCOMA, NOS |
8806/3 |
Desmoplastic small round cell tumor |
Soft Tissues: Uncertain differentiation: Desmoplastic small round cell tumor/t(21;22)(q21;q12) |
6317 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
880 |
SARCOMA, NOS |
8806/3 |
Desmoplastic small round cell tumor |
Soft Tissues: Uncertain differentiation: Epithelioid sarcoma |
5207 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
880 |
SARCOMA, NOS |
8804/3 |
Epithelioid sarcoma |
Soft Tissues: Uncertain differentiation: Ewing sarcoma / Primitive neurectodermal tumors (PNET) |
5010 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
936 |
PERIPHERAL NEUROECTODERMAL TUMOR |
9364/3 9260/3 |
Peripheral neuroectodermal tumor |
Soft Tissues: Uncertain differentiation: Ewing sarcoma: inv(22)(q12q12) |
6323 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
936 |
PERIPHERAL NEUROECTODERMAL TUMOR |
9364/3 9260/3 |
Peripheral neuroectodermal tumor |
Soft Tissues: Uncertain differentiation: Ewing sarcoma: t(11;22)(q24;q12) |
6318 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
936 |
PERIPHERAL NEUROECTODERMAL TUMOR |
9364/3 9260/3 |
Peripheral neuroectodermal tumor |
Soft Tissues: Uncertain differentiation: Ewing sarcoma: t(16;21)(p11;q22) |
5329 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
936 |
PERIPHERAL NEUROECTODERMAL TUMOR |
9364/3 9260/3 |
Peripheral neuroectodermal tumor |
Soft Tissues: Uncertain differentiation: Ewing sarcoma: t(17;22)(q21;q12) |
5475 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
936 |
PERIPHERAL NEUROECTODERMAL TUMOR |
9364/3 9260/3 |
Peripheral neuroectodermal tumor |
Soft Tissues: Uncertain differentiation: Ewing sarcoma: t(2;16)(q35;p11) |
5669 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
936 |
PERIPHERAL NEUROECTODERMAL TUMOR |
9364/3 9260/3 |
Peripheral neuroectodermal tumor |
Soft Tissues: Uncertain differentiation: Ewing sarcoma: t(2;22)(q36;q12) |
6319 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
936 |
PERIPHERAL NEUROECTODERMAL TUMOR |
9364/3 9260/3 |
Peripheral neuroectodermal tumor |
Soft Tissues: Uncertain differentiation: Ewing sarcoma: t(20;22)(q13;q12) |
6321 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
936 |
PERIPHERAL NEUROECTODERMAL TUMOR |
9364/3 9260/3 |
Peripheral neuroectodermal tumor |
Soft Tissues: Uncertain differentiation: Ewing sarcoma: t(21;22)(q21;q12) |
6322 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
936 |
PERIPHERAL NEUROECTODERMAL TUMOR |
9364/3 9260/3 |
Peripheral neuroectodermal tumor |
Soft Tissues: Uncertain differentiation: Ewing sarcoma: t(7;22)(p22;q12) |
6320 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
936 |
PERIPHERAL NEUROECTODERMAL TUMOR |
9364/3 9260/3 |
Peripheral neuroectodermal tumor |
Soft Tissues: Uncertain differentiation: Ewing-like sarcoma: t(4;19)(q35;q13) |
5714 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
936 |
PERIPHERAL NEUROECTODERMAL TUMOR |
9364/3 9260/3 |
Peripheral neuroectodermal tumor |
Soft Tissues: Uncertain differentiation: Extrarenal rhabdoid tumor |
5208 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
896 |
CLEAR CELL SARC/NEPHROBLASTOMA |
8963/3 |
Extra-renal rhabdoid tumor |
Soft Tissues: Uncertain differentiation: Extraskeletal myxoid chondrosarcoma/t(9;22)(q22;q12) |
5025 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
923 |
CHONDROBLASTOMA, MALIGNANT |
9231/3 |
Extraskeletal myxoid chondrosarcoma (chordoid type) |
Soft Tissues: Uncertain differentiation: Intramuscular myxoma |
5201 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
884 |
MYXOSARCOMA |
8840/0 |
Intramuscular myxoma (incl. cellular variant) |
Soft Tissues: Uncertain differentiation: Juxta-articular myxoma |
5202 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
884 |
MYXOSARCOMA |
8840/0 |
Juxta-articular myxoma |
Soft Tissues: Uncertain differentiation: Mixed tumor/Myoepithelioma/Parachordoma |
5206 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
937 |
CHORDOMA |
9373/1;8940/1;8982/1 |
Parachordoma Mixed tumor Myoepithelioma |
Soft Tissues: Uncertain differentiation: Mixed tumor/Myoepithelioma/Parachordoma: Myoepithelial carcinoma |
6366 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
937 |
CHORDOMA |
9373/1;8940/1;8982/1 |
Parachordoma Mixed tumor Myoepithelioma |
Soft Tissues: Uncertain differentiation: Mixed tumor/Myoepithelioma/Parachordoma: t(1;22)(q23;q12) |
6277 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
937 |
CHORDOMA |
9373/1;8940/1;8982/1 |
Parachordoma Mixed tumor Myoepithelioma |
Soft Tissues: Uncertain differentiation: Mixed tumor/Myoepithelioma/Parachordoma: t(19;22)(q13;q12) |
6287 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
937 |
CHORDOMA |
9373/1;8940/1;8982/1 |
Parachordoma Mixed tumor Myoepithelioma |
Soft Tissues: Uncertain differentiation: Ossifying fibromyxoid tumor |
5205 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
884 |
MYXOSARCOMA |
8842/0 |
Ossifying fibromyxoid tumor (incl. atypical / malignant) |
Soft Tissues: Uncertain differentiation: PEComas |
5209 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
|
|
|
|
Soft Tissues: Uncertain differentiation: Synovial sarcoma |
5044 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
904 |
SYNOVIAL SARCOMA, NOS |
9040/3 |
Synovial sarcoma, NOS |
Soft Tissues: Uncertain differentiation: Synovial sarcoma: t(X;20)(p11;q13) |
5464 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
904 |
SYNOVIAL SARCOMA, NOS |
9040/3 |
Synovial sarcoma, NOS |
Soft Tissues: Uncertain differentiation: t(2;22)(q31;q12) in a small round cell tumor |
6278 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
800 |
NEOPLASM |
8002/3 |
Malignant tumor, small cell type |
Soft Tissues: Vascular tumors: Angiosarcoma of the soft tissue |
5198 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
912 |
BLOOD VESSEL TUMORS |
9120/3 |
Hemangiosarcoma |
Soft Tissues: Vascular tumors: Epithelioid hemangioendothelioma |
5197 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
913 |
HEMANGIOENDOTHELIOMA |
9133/3 |
Epithelioid hemangioendothelioma, malignant |
Soft Tissues: Vascular tumors: Epithelioid hemangioendothelioma: t(1;3)(p36;q25) |
6371 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
913 |
HEMANGIOENDOTHELIOMA |
9133/3 |
Epithelioid hemangioendothelioma, malignant |
Soft Tissues: Vascular tumors: Haemangiomas of the soft tissue |
5742 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
912 |
BLOOD VESSEL TUMORS |
9120/0 |
Haemangiomas of subcut/deep soft tissue |
Soft Tissues: Vascular tumors: Kaposi sarcoma |
5196 |
C470-C476,C478-C479,C490-C496,C498-C499 |
CONNECTIVE & SOFT TISSUE |
914 |
KAPOSI SARCOMA |
9140/3 |
Kaposi sarcoma |