inv(1)(q21q23)TPM3::NTRK1

Genes involved

TPM3 (1q21.3)

NTRK1 (1q23.1)

Oncogenic mechanisms

Constitutive activation of TRK pathway

Targeted therapy

Larotrectinib

entrectinib

Tumor type

Thyroid carcinoma

Highly cited references

Pubmed IDYearTitleCitations
255271972015TRKing down an old oncogene in a new era of targeted therapy.90
327374492020Clinicopathologic features of kinase fusion-related thyroid carcinomas: an integrative analysis with molecular characterization.67
351724742021Development of an RNA sequencing panel to detect gene fusions in thyroid cancer.66
315671892020Colonic Adenocarcinomas Harboring NTRK Fusion Genes: A Clinicopathologic and Molecular Genetic Study of 16 Cases and Review of the Literature.59
389672202024Neurotrophic tyrosine receptor kinase gene fusions in adult and pediatric patients with solid tumors: a clinicogenomic biobank and record linkage study of expression frequency and patient characteristics from Finland.52
375341902023Overcoming MET-mediated resistance in oncogene-driven NSCLC.51
249627922014The TPM3-NTRK1 rearrangement is a recurring event in colorectal carcinoma and is associated with tumor sensitivity to TRKA kinase inhibition.50
347905772021Anti-Tumor Activity of AZD4547 Against NTRK1 Fusion Positive Cancer Cells Through Inhibition of NTRKs.48
291252332017In vivo imaging xenograft models for the evaluation of anti-brain tumor efficacy of targeted drugs.48
389234282024Induction of resistance to neurotrophic tropomyosin-receptor kinase inhibitors by HMGCS2 via a mevalonate pathway.45
389840282024Poor outcome in congenital mesoblastic nephroma with TPM3::NTRK1 fusion: a case report from multi-disciplinary treatment to molecular tumor board.42
268924432016The landscape of fusion transcripts in spitzoid melanoma and biologically indeterminate spitzoid tumors by RNA sequencing.42
267164142016NTRK1 fusions for the therapeutic intervention of Korean patients with colon cancer.38
352378892022Gene fusions and oncogenic mutations in MLH1 deficient and BRAFV600E wild-type colorectal cancers.35
314427442019Cancer Panel Assay for Precision Oncology Clinic: Results from a 1-Year Study.34
272590112016Recurrent NTRK1 Gene Fusions Define a Novel Subset of Locally Aggressive Lipofibromatosis-like Neural Tumors.33
339237282021NTRK Fusion Genes in Thyroid Carcinomas: Clinicopathological Characteristics and Their Impacts on Prognosis.32
370758102023LOGGIC Core BioClinical Data Bank: Added clinical value of RNA-Seq in an international molecular diagnostic registry for pediatric low-grade glioma patients.32
295683952018Merestinib (LY2801653) inhibits neurotrophic receptor kinase (NTRK) and suppresses growth of NTRK fusion bearing tumors.30
288770622018Recurrent BRAF Gene Fusions in a Subset of Pediatric Spindle Cell Sarcomas: Expanding the Genetic Spectrum of Tumors With Overlapping Features With Infantile Fibrosarcoma.29
337687102021Identification of NTRK gene fusions in lung adenocarcinomas in the Chinese population.28
400119002025NTRK rearranged spindle cell neoplasm of the uterine cervix: a rare case report and literature review.28
295539552018NTRK Fusions Define a Novel Uterine Sarcoma Subtype With Features of Fibrosarcoma.27
337075742021NTRK fusion in Japanese colorectal adenocarcinomas.26
346595252021TRK inhibitors block NFKB and induce NRF2 in TRK fusion-positive colon cancer.26
398028762024TPM3::NTRK1-rearranged uterine sarcoma: case report and literature review.24
400217572025An accurate DNA and RNA based targeted sequencing assay for clinical detection of gene fusions in solid tumors.24
347238482022NTRK-Fusion Sarcoma of the Uterine Cervix: Report of 2 Cases With Comparative Clinicopathologic Features.23
383572022024Case report: Adult NTRK-rearranged spindle cell neoplasms with TPM3-NTRK1 fusion in the pelvic.22
296103912018Application of genomics to identify therapeutic targets in recurrent pediatric papillary thyroid carcinoma.22
388357422024Difficulties of Preoperative Diagnosis of Cribriform Morular Thyroid Carcinoma.22
264720212015NTRK1 rearrangement in colorectal cancer patients: evidence for actionable target using patient-derived tumor cell line.19
352516412022A rare case of recurrent ovarian cancer with TPM3-NTRK1 gene rearrangement: A case report.13
332194932022Infantile fibrosarcoma with TPM3-NTRK1 fusion in a boy with Bloom syndrome.12
265633552016Sensitivity to Entrectinib Associated With a Novel LMNA-NTRK1 Gene Fusion in Metastatic Colorectal Cancer.12
329393442020TMP3-NTRK1 rearranged uterine sarcoma: A case report.11
366526662023Marked Response to Larotrectinib in Pelvic Spindle Cell Sarcoma With Concurrent TPM3-NTRK1 Fusion and CDK4/MDM2 Amplification: A Case Report.6
321699932020TPM3-NTRK1 fusion in a pleomorphic xanthoastrocytoma presenting with haemorrhage in a child.5
253840852014Anchored multiplex PCR for targeted next-generation sequencing.0
301711972019Molecular characterization of cancers with NTRK gene fusions.0
75907421995A sequence analysis of the genomic regions involved in the rearrangements between TPM3 and NTRK1 genes producing TRK oncogenes in papillary thyroid carcinomas.0
336310442021NTRK fusion-positive colorectal cancer in Japanese population.0
371424532023Elaboration of NTRK-rearranged colorectal cancer: Integration of immunoreactivity pattern, cytogenetic identity, and rearrangement variant.0
365864212023CANTRK: A Canadian Ring Study to Optimize Detection of NTRK Gene Fusions by Next-Generation RNA Sequencing.0
287515392017Mechanisms of Resistance to NTRK Inhibitors and Therapeutic Strategies in NTRK1-Rearranged Cancers.0
385258232024Primary NTRK -rearranged Spindle Cell Neoplasm of the Gastrointestinal Tract: A Clinicopathological and Molecular Analysis of 8 Cases.0
351497692022Adult NTRK-rearranged spindle cell neoplasms of the viscera: with an emphasis on rare locations and heterologous elements.0
100749151999NTRK1 re-arrangement in papillary thyroid carcinomas of children after the Chernobyl reactor accident.0
260019712015Chromosomal rearrangements involving the NTRK1 gene in colorectal carcinoma.0
393166502024Recurrent CLTC::SYK fusions and CSF1R mutations in juvenile xanthogranuloma of soft tissue.0
355430762022Histologic characterization of paediatric mesenchymal neoplasms treated with kinase-targeted therapy.0
350078532022Pan-tumor screening for NTRK gene fusions using pan-TRK immunohistochemistry and RNA NGS fusion panel testing.0
354041932023Infant-Type Hemispheric Glioma in a Chinese Girl: A Newly Defined Entity.0
326103772020[Clinicopathological characteristics of NTRK-rearranged mesenchymal tumors in childhood].0
331287802021Chromosomal imbalances detected in NTRK-rearranged sarcomas by the use of comparative genomic hybridisation.0
306685252019Targetable gene fusions identified in radioactive iodine refractory advanced thyroid carcinoma.0
344025292021NTRK oncogenic fusions are exclusively associated with the serrated neoplasia pathway in the colorectum and begin to occur in sessile serrated lesions.0
326696122021Mesenchymal tumors of the gastrointestinal tract with NTRK rearrangements: a clinicopathological, immunophenotypic, and molecular study of eight cases, emphasizing their distinction from gastrointestinal stromal tumor (GIST).0
388662552024Feasibility of two-step approach for screening NTRK fusion in two major subtypes of non-small cell lung cancer within a large cohort.0
359775942022Pan-tropomyosin receptor kinase immunohistochemistry is a feasible routine screening strategy for NTRK fusions in mismatch repair-deficient colorectal carcinomas.0
340917602021Correlating SS18-SSX immunohistochemistry (IHC) with SS18 fluorescent in situ hybridization (FISH) in synovial sarcomas: a study of 36 cases.0
262002692015Unique Genetic and Survival Characteristics of Invasive Mucinous Adenocarcinoma of the Lung.0
397209932024A phase II trial of larotrectinib in tumors with NTRK fusions or extremes of NTRK mRNA overexpression identified by comprehensive genomic profiling.0
339864602021Re-evaluating tumors of purported specialized prostatic stromal origin reveals molecular heterogeneity, including non-recurring gene fusions characteristic of uterine and soft tissue sarcoma subtypes.0
294635552018Foretinib Overcomes Entrectinib Resistance Associated with the NTRK1 G667C Mutation in NTRK1 Fusion-Positive Tumor Cells in a Brain Metastasis Model.0
308772732019Uterine and vaginal sarcomas resembling fibrosarcoma: a clinicopathological and molecular analysis of 13 cases showing common NTRK-rearrangements and the description of a COL1A1-PDGFB fusion novel to uterine neoplasms.0
325914652020U.S. Phase I First-in-human Study of Taletrectinib (DS-6051b/AB-106), a ROS1/TRK Inhibitor, in Patients with Advanced Solid Tumors.0
371062862023[Clinicopathological features of gastric carcinomas with NTRK-rearrangement/amplification: report of four cases].0
352203542022Primary NTRK-rearranged Spindle Cell Neoplasm of the Lung: A Clinicopathologic and Molecular Analysis of 3 Cases.0
398635282025[NTRK gene fusion and molecular pathological characteristics of mismatch repair deficient colorectal cancer].0
319712782020NTRK fusion cervical sarcoma: a report of three cases, emphasising morphological and immunohistochemical distinction from other uterine sarcomas, including adenosarcoma.0

Bibliography

Pubmed IDPublication YearTitleAuthors
75907421995A sequence analysis of the genomic regions involved in the rearrangements between TPM3 and NTRK1 genes producing TRK oncogenes in papillary thyroid carcinomas.Butti MG, et al
13846731992Cytogenetic and molecular genetic characterization of papillary thyroid carcinomas.Sozzi G, et al
252044152014The landscape of kinase fusions in cancer.Stransky N, et al
255005442015The landscape and therapeutic relevance of cancer-associated transcript fusions.Yoshihara K, et al