KCNQ3 (potassium voltage-gated channel subfamily Q member 3)

2003-05-01  

Identity

HGNC
LOCATION
8q24.22
LOCUSID
ALIAS
BFNC2,EBN2,KV7.3
FUSION GENES

Other Information

Locus ID:

NCBI: 3786
MIM: 602232
HGNC: 6297
Ensembl: ENSG00000184156

Variants:

dbSNP: 3786
ClinVar: 3786
TCGA: ENSG00000184156
COSMIC: KCNQ3

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000184156ENST00000388996O43525
ENSG00000184156ENST00000519445E7ET42
ENSG00000184156ENST00000521134O43525
ENSG00000184156ENST00000621976A0A087WZB4
ENSG00000184156ENST00000638588A0A1W2PQ71
ENSG00000184156ENST00000639358A0A1W2PRN8
ENSG00000184156ENST00000639496A0A1W2PNZ2

Expression (GTEx)

0
5
10
15
20
25

Pathways

PathwaySourceExternal ID
Cholinergic synapseKEGGhsa04725
Neuronal SystemREACTOMER-HSA-112316
Potassium ChannelsREACTOMER-HSA-1296071
Voltage gated Potassium channelsREACTOMER-HSA-1296072
Developmental BiologyREACTOMER-HSA-1266738
Axon guidanceREACTOMER-HSA-422475
L1CAM interactionsREACTOMER-HSA-373760
Interaction between L1 and AnkyrinsREACTOMER-HSA-445095

PharmGKB

Entity IDNameTypeEvidenceAssociationPKPDPMIDs
PA448871celecoxibChemicalPathwayassociated22336956

References

Pubmed IDYearTitleCitations
376480392024SMAD4 and KCNQ3 alterations are associated with lymph node metastases in oesophageal adenocarcinoma.0
380499722024Impacted spike frequency adaptation associated with reduction of KCNQ2/3 exacerbates seizure activity in temporal lobe epilepsy.0
376480392024SMAD4 and KCNQ3 alterations are associated with lymph node metastases in oesophageal adenocarcinoma.0
380499722024Impacted spike frequency adaptation associated with reduction of KCNQ2/3 exacerbates seizure activity in temporal lobe epilepsy.0
353847802022Phenotypic Spectrum in a Family Sharing a Heterozygous KCNQ3 Variant.0
353847802022Phenotypic Spectrum in a Family Sharing a Heterozygous KCNQ3 Variant.0
330373902021The identification of two pathogenic variants in a family with mild and severe forms of developmental delay.1
330373902021The identification of two pathogenic variants in a family with mild and severe forms of developmental delay.1
325809972020Heteromeric Assembly of Truncated Neuronal Kv7 Channels: Implications for Neurologic Disease and Pharmacotherapy.4
325809972020Heteromeric Assembly of Truncated Neuronal Kv7 Channels: Implications for Neurologic Disease and Pharmacotherapy.4
305783302019Epilepsy-associated mutations in the voltage sensor of KCNQ3 affect voltage dependence of channel opening.4
308856092019Identification of potassium channel proteins Kv7.2/7.3 as common partners of the dopamine and glutamate transporters DAT and GLT-1.7
311775782019Autism and developmental disability caused by KCNQ3 gain-of-function variants.47
305783302019Epilepsy-associated mutations in the voltage sensor of KCNQ3 affect voltage dependence of channel opening.4
308856092019Identification of potassium channel proteins Kv7.2/7.3 as common partners of the dopamine and glutamate transporters DAT and GLT-1.7

Citation

Dessen P

KCNQ3 (potassium voltage-gated channel subfamily Q member 3)

Atlas Genet Cytogenet Oncol Haematol. 2003-05-01

Online version: http://atlasgeneticsoncology.org/gene/41052/kcnq3