PGM1 (phosphoglucomutase 1)

2007-04-01  

Identity

HGNC
LOCATION
1p31.3
LOCUSID
ALIAS
CDG1T,GSD14
FUSION GENES

Other Information

Locus ID:

NCBI: 5236
MIM: 171900
HGNC: 8905
Ensembl: ENSG00000079739

Variants:

dbSNP: 5236
ClinVar: 5236
TCGA: ENSG00000079739
COSMIC: PGM1

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000079739ENST00000371083P36871
ENSG00000079739ENST00000371084P36871
ENSG00000079739ENST00000540265P36871
ENSG00000079739ENST00000650546A0A3B3ITK7

Expression (GTEx)

0
50
100
150
200
250
300
350
400
450

Pathways

PathwaySourceExternal ID
Glycolysis / GluconeogenesisKEGGko00010
Pentose phosphate pathwayKEGGko00030
Galactose metabolismKEGGko00052
Purine metabolismKEGGko00230
Starch and sucrose metabolismKEGGko00500
Amino sugar and nucleotide sugar metabolismKEGGko00520
Glycolysis / GluconeogenesisKEGGhsa00010
Pentose phosphate pathwayKEGGhsa00030
Galactose metabolismKEGGhsa00052
Purine metabolismKEGGhsa00230
Starch and sucrose metabolismKEGGhsa00500
Amino sugar and nucleotide sugar metabolismKEGGhsa00520
Metabolic pathwaysKEGGhsa01100
Nucleotide sugar biosynthesis, glucose => UDP-glucoseKEGGhsa_M00549
Nucleotide sugar biosynthesis, glucose => UDP-glucoseKEGGM00549
Immune SystemREACTOMER-HSA-168256
Innate Immune SystemREACTOMER-HSA-168249
MetabolismREACTOMER-HSA-1430728
Metabolism of carbohydratesREACTOMER-HSA-71387
Glucose metabolismREACTOMER-HSA-70326
Glycogen synthesisREACTOMER-HSA-3322077
Glycogen breakdown (glycogenolysis)REACTOMER-HSA-70221
Galactose catabolismREACTOMER-HSA-70370
Neutrophil degranulationREACTOMER-HSA-6798695

Protein levels (Protein atlas)

Not detected
Low
Medium
High

PharmGKB

Entity IDNameTypeEvidenceAssociationPKPDPMIDs
PA166186245acetaldehydeChemicalClinicalAnnotationassociatedPK31002879

References

Pubmed IDYearTitleCitations
369479652023Knock-down of PGM1 inhibits cell viability, glycolysis, and oxidative phosphorylation in glioma under low glucose condition via the Myc signaling pathway.2
369479652023Knock-down of PGM1 inhibits cell viability, glycolysis, and oxidative phosphorylation in glioma under low glucose condition via the Myc signaling pathway.2
355067652022Effects of the T337M and G391V disease-related variants on human phosphoglucomutase 1: structural disruptions large and small.0
355067652022Effects of the T337M and G391V disease-related variants on human phosphoglucomutase 1: structural disruptions large and small.0
328986482021Enzyme dysfunction at atomic resolution: Disease-associated variants of human phosphoglucomutase-1.5
328986482021Enzyme dysfunction at atomic resolution: Disease-associated variants of human phosphoglucomutase-1.5
320571192020A missense variant remote from the active site impairs stability of human phosphoglucomutase 1.1
321718582020AMPK-dependent phosphorylation of HDAC8 triggers PGM1 expression to promote lung cancer cell survival under glucose starvation.25
322213902020Structural basis for substrate and product recognition in human phosphoglucomutase-1 (PGM1) isoform 2, a member of the α-D-phosphohexomutase superfamily.7
333424672020Phosphoglucomutase-1 deficiency: Early presentation, metabolic management and detection in neonatal blood spots.12
320571192020A missense variant remote from the active site impairs stability of human phosphoglucomutase 1.1
321718582020AMPK-dependent phosphorylation of HDAC8 triggers PGM1 expression to promote lung cancer cell survival under glucose starvation.25
322213902020Structural basis for substrate and product recognition in human phosphoglucomutase-1 (PGM1) isoform 2, a member of the α-D-phosphohexomutase superfamily.7
333424672020Phosphoglucomutase-1 deficiency: Early presentation, metabolic management and detection in neonatal blood spots.12
307370792019Congenital disorder of glycosylation type 1T with a novel truncated homozygous mutation in PGM1 gene and literature review.6

Citation

Dessen P

PGM1 (phosphoglucomutase 1)

Atlas Genet Cytogenet Oncol Haematol. 2007-04-01

Online version: http://atlasgeneticsoncology.org/gene/47415/pgm1