APTX (aprataxin)

2004-02-01  

Identity

HGNC
LOCATION
9p21.1
LOCUSID
ALIAS
AOA,AOA1,AXA1,EAOH,EOAHA,FHA-HIT
FUSION GENES

Other Information

Locus ID:

NCBI: 54840
MIM: 606350
HGNC: 15984
Ensembl: ENSG00000137074

Variants:

dbSNP: 54840
ClinVar: 54840
TCGA: ENSG00000137074
COSMIC: APTX

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000137074ENST00000309615Q7Z2E3
ENSG00000137074ENST00000379813A0A0A0MRW7
ENSG00000137074ENST00000379817Q7Z2E3
ENSG00000137074ENST00000379819Q7Z2E3
ENSG00000137074ENST00000379825Q7Z2E3
ENSG00000137074ENST00000397172Q7Z2E3
ENSG00000137074ENST00000436040Q7Z2E3
ENSG00000137074ENST00000460940Q7Z2E3
ENSG00000137074ENST00000463596Q7Z2E3
ENSG00000137074ENST00000464632E7EUY4
ENSG00000137074ENST00000465003Q6JV79
ENSG00000137074ENST00000467331Q7Z2E3
ENSG00000137074ENST00000468275Q7Z2E3
ENSG00000137074ENST00000472896Q7Z2E3
ENSG00000137074ENST00000474658F8WBM3
ENSG00000137074ENST00000476858Q7Z2E3
ENSG00000137074ENST00000477119C9J8U3
ENSG00000137074ENST00000478279E7EVB7
ENSG00000137074ENST00000479656Q7Z2E3
ENSG00000137074ENST00000480031F8WBD6
ENSG00000137074ENST00000482687Q7Z2E3
ENSG00000137074ENST00000483148Q6JV79
ENSG00000137074ENST00000485479Q7Z2E3
ENSG00000137074ENST00000494649Q7Z2E3
ENSG00000137074ENST00000495360Q7Z2E3

Expression (GTEx)

0
5
10
15
20
25
30

Protein levels (Protein atlas)

Not detected
Low
Medium
High

References

Pubmed IDYearTitleCitations
369407052023APTX acts in DNA double-strand break repair in a manner distinct from XRCC4.1
369407052023APTX acts in DNA double-strand break repair in a manner distinct from XRCC4.1
327500612020Identification of APTX disease-causing mutation in two unrelated Jordanian families with cerebellar ataxia and sensitivity to DNA damaging agents.2
327690662020Generation and characterization of induced pluripotent stem cell (iPSC) line (JUCTCi002-A) from a patient with ataxia with oculomotor apraxia type 1 (AOA1) harboring a homozygous mutation in the APTX gene.0
327500612020Identification of APTX disease-causing mutation in two unrelated Jordanian families with cerebellar ataxia and sensitivity to DNA damaging agents.2
327690662020Generation and characterization of induced pluripotent stem cell (iPSC) line (JUCTCi002-A) from a patient with ataxia with oculomotor apraxia type 1 (AOA1) harboring a homozygous mutation in the APTX gene.0
309868242019Diminished OPA1 expression and impaired mitochondrial morphology and homeostasis in Aprataxin-deficient cells.15
317806612019Two-tiered enforcement of high-fidelity DNA ligation.17
309868242019Diminished OPA1 expression and impaired mitochondrial morphology and homeostasis in Aprataxin-deficient cells.15
317806612019Two-tiered enforcement of high-fidelity DNA ligation.17
299342932018Mechanism of APTX nicked DNA sensing and pleiotropic inactivation in neurodegenerative disease.7
299342932018Mechanism of APTX nicked DNA sensing and pleiotropic inactivation in neurodegenerative disease.7
274709392017Neurological disorders associated with DNA strand-break processing enzymes.19
286522552017Identification of a novel mutation in the APTX gene associated with ataxia-oculomotor apraxia.2
274709392017Neurological disorders associated with DNA strand-break processing enzymes.19

Citation

Dessen P

APTX (aprataxin)

Atlas Genet Cytogenet Oncol Haematol. 2004-02-01

Online version: http://atlasgeneticsoncology.org/gene/683/aptx