COL4A2 (collagen type IV alpha 2 chain)

2003-06-01  

Identity

HGNC
LOCATION
13q34
LOCUSID
ALIAS
BSVD2,ICH,POREN2
FUSION GENES

Other Information

Locus ID:

NCBI: 1284
MIM: 120090
HGNC: 2203
Ensembl: ENSG00000134871

Variants:

dbSNP: 1284
ClinVar: 1284
TCGA: ENSG00000134871
COSMIC: COL4A2

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000134871ENST00000360467P08572
ENSG00000134871ENST00000360467A0A024RDW8
ENSG00000134871ENST00000400163A2A352
ENSG00000134871ENST00000480609A0A3B3IS47
ENSG00000134871ENST00000494852A0A3B3IT80
ENSG00000134871ENST00000617564A0A087WY39
ENSG00000134871ENST00000619688A0A3B3IRV2
ENSG00000134871ENST00000649101A0A3B3ITN7
ENSG00000134871ENST00000649951A0A3B3IS04
ENSG00000134871ENST00000650540A0A3B3ITQ8

Expression (GTEx)

0
100
200
300
400
500
600

Pathways

PathwaySourceExternal ID
Focal adhesionKEGGko04510
ECM-receptor interactionKEGGko04512
Small cell lung cancerKEGGko05222
Focal adhesionKEGGhsa04510
ECM-receptor interactionKEGGhsa04512
Pathways in cancerKEGGhsa05200
Small cell lung cancerKEGGhsa05222
AmoebiasisKEGGko05146
AmoebiasisKEGGhsa05146
Protein digestion and absorptionKEGGko04974
Protein digestion and absorptionKEGGhsa04974
PI3K-Akt signaling pathwayKEGGhsa04151
PI3K-Akt signaling pathwayKEGGko04151
Signal TransductionREACTOMER-HSA-162582
Signaling by PDGFREACTOMER-HSA-186797
Vesicle-mediated transportREACTOMER-HSA-5653656
Binding and Uptake of Ligands by Scavenger ReceptorsREACTOMER-HSA-2173782
Scavenging by Class A ReceptorsREACTOMER-HSA-3000480
Extracellular matrix organizationREACTOMER-HSA-1474244
Collagen formationREACTOMER-HSA-1474290
Collagen biosynthesis and modifying enzymesREACTOMER-HSA-1650814
Assembly of collagen fibrils and other multimeric structuresREACTOMER-HSA-2022090
Integrin cell surface interactionsREACTOMER-HSA-216083
Developmental BiologyREACTOMER-HSA-1266738
Axon guidanceREACTOMER-HSA-422475
NCAM signaling for neurite out-growthREACTOMER-HSA-375165
NCAM1 interactionsREACTOMER-HSA-419037
AGE-RAGE signaling pathway in diabetic complicationsKEGGko04933
AGE-RAGE signaling pathway in diabetic complicationsKEGGhsa04933
Collagen chain trimerizationREACTOMER-HSA-8948216

Protein levels (Protein atlas)

Not detected
Low
Medium
High

PharmGKB

Entity IDNameTypeEvidenceAssociationPKPDPMIDs
PA179GP1BBGenePathwayassociated20938371
PA204ITGA2GenePathwayassociated20938371
PA26212CD36GenePathwayassociated20938371
PA28823GP5GenePathwayassociated20938371
PA28824GP6GenePathwayassociated20938371
PA28825GP9GenePathwayassociated20938371

References

Pubmed IDYearTitleCitations
361255352023Secretome analysis reveals reduced expression of COL4A2 in hypoxic cancer-associated fibroblasts with a tumor-promoting function in gastric cancer.3
376424292023Venous Tortuosity in COL4A2-Associated Gould Syndrome.0
361255352023Secretome analysis reveals reduced expression of COL4A2 in hypoxic cancer-associated fibroblasts with a tumor-promoting function in gastric cancer.3
376424292023Venous Tortuosity in COL4A2-Associated Gould Syndrome.0
342814422022Next-generation sequencing in a large pedigree segregating visceral artery aneurysms suggests potential role of COL4A1/COL4A2 in disease etiology.2
355322932022The ETS1-LINC00278 negative feedback loop plays a role in COL4A1/COL4A2 regulation in laryngeal squamous cell carcinoma.4
364038582022Lysyl hydroxylase 3-mediated post-translational modifications are required for proper biosynthesis of collagen α1α1α2(IV).1
342814422022Next-generation sequencing in a large pedigree segregating visceral artery aneurysms suggests potential role of COL4A1/COL4A2 in disease etiology.2
355322932022The ETS1-LINC00278 negative feedback loop plays a role in COL4A1/COL4A2 regulation in laryngeal squamous cell carcinoma.4
364038582022Lysyl hydroxylase 3-mediated post-translational modifications are required for proper biosynthesis of collagen α1α1α2(IV).1
325158302021Prevalence of COL4A1 and COL4A2 mutations in severe fetal multifocal hemorrhagic and/or ischemic cerebral lesions.11
327322252021Prenatal clinical manifestations in individuals with COL4A1/2 variants.11
332479882021Intracerebral hemorrhage in a neonate with an intragenic COL4A2 duplication.4
332688482021Whole-exome sequencing of Finnish patients with vascular cognitive impairment.6
335770442021Novel COL4A2 mutation causing familial malformations of cortical development.3

Citation

Dessen P

COL4A2 (collagen type IV alpha 2 chain)

Atlas Genet Cytogenet Oncol Haematol. 2003-06-01

Online version: http://atlasgeneticsoncology.org/gene/40125/col4a2-(collagen-type-iv-alpha-2-chain)