CYP27B1 (cytochrome P450 family 27 subfamily B member 1)

2007-02-01  

Identity

HGNC
LOCATION
12q14.1
LOCUSID
ALIAS
CP2B,CYP1,CYP1alpha,CYP27B,P450c1,PDDR,VDD1,VDDR,VDDRI,VDR
FUSION GENES

Other Information

Locus ID:

NCBI: 1594
MIM: 609506
HGNC: 2606
Ensembl: ENSG00000111012

Variants:

dbSNP: 1594
ClinVar: 1594
TCGA: ENSG00000111012
COSMIC: CYP27B1

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000111012ENST00000228606O15528
ENSG00000111012ENST00000546567F8VWR7
ENSG00000111012ENST00000546609V9GYP0

Expression (GTEx)

0
5
10
15

Pathways

PathwaySourceExternal ID
Steroid biosynthesisKEGGko00100
Steroid biosynthesisKEGGhsa00100
Metabolic pathwaysKEGGhsa01100
TuberculosisKEGGko05152
TuberculosisKEGGhsa05152
Cholecalciferol biosynthesisKEGGhsa_M00103
Cholecalciferol biosynthesisKEGGM00103
MetabolismREACTOMER-HSA-1430728
Vitamin D (calciferol) metabolismREACTOMER-HSA-196791
Metabolism of vitamins and cofactorsREACTOMER-HSA-196854
Biological oxidationsREACTOMER-HSA-211859
Phase 1 - Functionalization of compoundsREACTOMER-HSA-211945
Cytochrome P450 - arranged by substrate typeREACTOMER-HSA-211897
VitaminsREACTOMER-HSA-211916
Metabolism of fat-soluble vitaminsREACTOMER-HSA-6806667

PharmGKB

Entity IDNameTypeEvidenceAssociationPKPDPMIDs
PA162263533nephrotoxicityDiseaseClinicalAnnotationassociatedPD31619748
PA164760843deferasiroxChemicalClinicalAnnotationassociatedPD30651574
PA164784024peginterferon alfa-2bChemicalClinicalAnnotationassociatedPD21145801
PA166201941tenofovir disoproxil fumarateChemicalClinicalAnnotationassociatedPD31619748
PA446432beta-ThalassemiaDiseaseClinicalAnnotationassociatedPD30651574
PA446863Hepatitis C, ChronicDiseaseClinicalAnnotationassociatedPD21145801
PA447230HIV InfectionsDiseaseClinicalAnnotationassociatedPD31619748
PA451241ribavirinChemicalClinicalAnnotationassociatedPD21145801

References

Pubmed IDYearTitleCitations
363215352023Genotype-phenotype Description of Vitamin D-dependent Rickets 1A: CYP27B1 p.(Ala129Thr) Variant Induces a Milder Disease.0
365249792023Clinical spectrum and diagnostic challenges of vitamin D dependent rickets type 1A (VDDR1A) caused by CYP27B1 mutation in resource limited countries.0
372443012023Local production of active vitamin D(3) metabolites in breast cancer cells by CYP24A1 and CYP27B1.2
363215352023Genotype-phenotype Description of Vitamin D-dependent Rickets 1A: CYP27B1 p.(Ala129Thr) Variant Induces a Milder Disease.0
365249792023Clinical spectrum and diagnostic challenges of vitamin D dependent rickets type 1A (VDDR1A) caused by CYP27B1 mutation in resource limited countries.0
372443012023Local production of active vitamin D(3) metabolites in breast cancer cells by CYP24A1 and CYP27B1.2
351660422022Astrocytes expressing Vitamin D-activating enzyme identify Parkinson's disease.6
355083232022Responsible enzymes for metabolizing vitamin D in patients with acute leukemia and the relationship with treatment outcomes: a case-control study.1
363264212022The role of vitamin D-synthesizing enzyme CYP27B1 in systemic lupus erythematosus.0
351660422022Astrocytes expressing Vitamin D-activating enzyme identify Parkinson's disease.6
355083232022Responsible enzymes for metabolizing vitamin D in patients with acute leukemia and the relationship with treatment outcomes: a case-control study.1
363264212022The role of vitamin D-synthesizing enzyme CYP27B1 in systemic lupus erythematosus.0
330583072021Dysregulation of vitamin D synthesis pathway genes in colorectal cancer: A case-control study.2
333059622021Gene variants and haplotypes of Vitamin D biosynthesis, transport, and function in preeclampsia.6
335948062021Vitamin D status and CYP27B1-1260 promoter polymorphism in Tunisian patients with systemic lupus erythematosus.4

Citation

Dessen P

CYP27B1 (cytochrome P450 family 27 subfamily B member 1)

Atlas Genet Cytogenet Oncol Haematol. 2007-02-01

Online version: http://atlasgeneticsoncology.org/gene/46401/cyp27b1-(cytochrome-p450-family-27-subfamily-b-member-1)