HSD17B10 (hydroxysteroid 17-beta dehydrogenase 10)

2009-09-01  

Identity

HGNC
LOCATION
Xp11.22
LOCUSID
ALIAS
17b-HSD10,ABAD,CAMR,DUPXp11.22,ERAB,HADH2,HCD2,HSD10MD,MHBD,MRPP2,MRX17,MRX31,MRXS10,SCHAD,SDR5C1
FUSION GENES

Other Information

Locus ID:

NCBI: 3028
MIM: 300256
HGNC: 4800
Ensembl: ENSG00000072506

Variants:

dbSNP: 3028
ClinVar: 3028
TCGA: ENSG00000072506
COSMIC: HSD17B10

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000072506ENST00000168216Q99714
ENSG00000072506ENST00000168216A0A0S2Z410
ENSG00000072506ENST00000375298Q5H928
ENSG00000072506ENST00000375304Q99714

Expression (GTEx)

0
50
100
150

Pathways

PathwaySourceExternal ID
Valine, leucine and isoleucine degradationKEGGko00280
Alzheimer's diseaseKEGGko05010
Valine, leucine and isoleucine degradationKEGGhsa00280
Alzheimer's diseaseKEGGhsa05010
Metabolic pathwaysKEGGhsa01100
Gene ExpressionREACTOMER-HSA-74160
MetabolismREACTOMER-HSA-1430728
Metabolism of amino acids and derivativesREACTOMER-HSA-71291
Branched-chain amino acid catabolismREACTOMER-HSA-70895
tRNA processingREACTOMER-HSA-72306
tRNA processing in the mitochondrionREACTOMER-HSA-6785470
tRNA modification in the mitochondrionREACTOMER-HSA-6787450
rRNA processingREACTOMER-HSA-72312
rRNA processing in the mitochondrionREACTOMER-HSA-8868766

Protein levels (Protein atlas)

Not detected
Low
Medium
High

References

Pubmed IDYearTitleCitations
386842972024[Clinical analysis and genetic diagnosis of three children with Isoleucine metabolic disorders due to variants of HSD17B10 and ACAT1 genes].0
386842972024[Clinical analysis and genetic diagnosis of three children with Isoleucine metabolic disorders due to variants of HSD17B10 and ACAT1 genes].0
372398332023Infantile Neurodegeneration Results from Mutants of 17β-Hydroxysteroid Dehydrogenase Type 10 Rather Than Aβ-Binding Alcohol Dehydrogenase.2
381394302023Involvement of Type 10 17β-Hydroxysteroid Dehydrogenase in the Pathogenesis of Infantile Neurodegeneration and Alzheimer's Disease.0
372398332023Infantile Neurodegeneration Results from Mutants of 17β-Hydroxysteroid Dehydrogenase Type 10 Rather Than Aβ-Binding Alcohol Dehydrogenase.2
381394302023Involvement of Type 10 17β-Hydroxysteroid Dehydrogenase in the Pathogenesis of Infantile Neurodegeneration and Alzheimer's Disease.0
362719512022ost in promiscuity? An evolutionary and biochemical evaluation of HSD10 function in cardiolipin metabolism.4
362719512022ost in promiscuity? An evolutionary and biochemical evaluation of HSD10 function in cardiolipin metabolism.4
344896092021Structural basis of RNA processing by human mitochondrial RNase P.32
344896092021Structural basis of RNA processing by human mitochondrial RNase P.32
323810892020Xp11.22 duplications in four unrelated Chinese families: delineating the genotype-phenotype relationship for HSD17B10 and FGD1.6
327039352020Deacetylation of HSD17B10 by SIRT3 regulates cell growth and cell resistance under oxidative and starvation stresses.9
323810892020Xp11.22 duplications in four unrelated Chinese families: delineating the genotype-phenotype relationship for HSD17B10 and FGD1.6
327039352020Deacetylation of HSD17B10 by SIRT3 regulates cell growth and cell resistance under oxidative and starvation stresses.9
316544902019HSD10 mitochondrial disease: p.Leu122Val variant, mild clinical phenotype, and founder effect in French-Canadian patients from Quebec.7

Citation

Dessen P

HSD17B10 (hydroxysteroid 17-beta dehydrogenase 10)

Atlas Genet Cytogenet Oncol Haematol. 2009-09-01

Online version: http://atlasgeneticsoncology.org/gene/51095/hsd17b10-(hydroxysteroid-17-beta-dehydrogenase-10)