UNC13D (unc-13 homolog D)

2011-06-01  

Identity

HGNC
LOCATION
17q25.1
LOCUSID
ALIAS
FHL3,HLH3,HPLH3,Munc13-4
FUSION GENES

Other Information

Locus ID:

NCBI: 201294
MIM: 608897
HGNC: 23147
Ensembl: ENSG00000092929

Variants:

dbSNP: 201294
ClinVar: 201294
TCGA: ENSG00000092929
COSMIC: UNC13D

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000092929ENST00000207549Q70J99
ENSG00000092929ENST00000412096Q70J99
ENSG00000092929ENST00000586108K7EIH3
ENSG00000092929ENST00000586147K7EMK8
ENSG00000092929ENST00000586519K7ELN2
ENSG00000092929ENST00000587105K7EM66
ENSG00000092929ENST00000589670K7EN29
ENSG00000092929ENST00000590762K7EQ37
ENSG00000092929ENST00000592386K7EN81

Expression (GTEx)

0
50
100
150

Pathways

PathwaySourceExternal ID
Immune SystemREACTOMER-HSA-168256
Innate Immune SystemREACTOMER-HSA-168249
Neutrophil degranulationREACTOMER-HSA-6798695

Protein levels (Protein atlas)

Not detected
Low
Medium
High

PharmGKB

Entity IDNameTypeEvidenceAssociationPKPDPMIDs
PA166182763emapalumabChemicalLabelAnnotationassociated

References

Pubmed IDYearTitleCitations
352938822022Familial Hemophagocytic Lymphohistiocytosis With Heterozygous STX11 and Homozygous UNC13D Mutations Diagnosed in the Neonatal Period.0
352938822022Familial Hemophagocytic Lymphohistiocytosis With Heterozygous STX11 and Homozygous UNC13D Mutations Diagnosed in the Neonatal Period.0
338675262021Germline variants in UNC13D and AP3B1 are enriched in COVID-19 patients experiencing severe cytokine storms.15
343395482021Spectrum mutations of PRF1, UNC13D, STX11, and STXBP2 genes in Vietnamese patients with hemophagocytic lymphohistiocytosis.3
338675262021Germline variants in UNC13D and AP3B1 are enriched in COVID-19 patients experiencing severe cytokine storms.15
343395482021Spectrum mutations of PRF1, UNC13D, STX11, and STXBP2 genes in Vietnamese patients with hemophagocytic lymphohistiocytosis.3
316517262020Different Clinical Presentation of 3 Children With Familial Hemophagocytic Lymphohistiocytosis With 2 Novel Mutations.2
322539312020Lentiviral Gene Therapy for Familial Hemophagocytic Lymphohistiocytosis Type 3, Caused by UNC13D Genetic Defects.6
325822172020Alternative UNC13D Promoter Encodes a Functional Munc13-4 Isoform Predominantly Expressed in Lymphocytes and Platelets.2
330932392020Unc-13 homolog D mediates an antiviral effect of the chromosome 19 microRNA cluster miR-517a.3
316517262020Different Clinical Presentation of 3 Children With Familial Hemophagocytic Lymphohistiocytosis With 2 Novel Mutations.2
322539312020Lentiviral Gene Therapy for Familial Hemophagocytic Lymphohistiocytosis Type 3, Caused by UNC13D Genetic Defects.6
325822172020Alternative UNC13D Promoter Encodes a Functional Munc13-4 Isoform Predominantly Expressed in Lymphocytes and Platelets.2
330932392020Unc-13 homolog D mediates an antiviral effect of the chromosome 19 microRNA cluster miR-517a.3
307588542019Haploinsufficiency of UNC13D increases the risk of lymphoma.4

Citation

Dessen P

UNC13D (unc-13 homolog D)

Atlas Genet Cytogenet Oncol Haematol. 2011-06-01

Online version: http://atlasgeneticsoncology.org/gene/52261