SAMHD1 (SAM and HD domain containing deoxynucleoside triphosphate triphosphohydrolase 1)

2013-05-01  

Identity

HGNC
LOCATION
20q11.23
LOCUSID
ALIAS
CHBL2,DCIP,HDDC1,MOP-5,SBBI88,hSAMHD1
FUSION GENES

Other Information

Locus ID:

NCBI: 25939
MIM: 606754
HGNC: 15925
Ensembl: ENSG00000101347

Variants:

dbSNP: 25939
ClinVar: 25939
TCGA: ENSG00000101347
COSMIC: SAMHD1

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000101347ENST00000262878Q9Y3Z3
ENSG00000101347ENST00000465985A0A2R8YF18
ENSG00000101347ENST00000642186A0A2R8Y5D2
ENSG00000101347ENST00000642246A0A2R8Y7R5
ENSG00000101347ENST00000642616A0A2R8Y586
ENSG00000101347ENST00000643078A0A2R8Y7R5
ENSG00000101347ENST00000643825A0A2R8YFV6
ENSG00000101347ENST00000643918A0A2R8YCS7
ENSG00000101347ENST00000644114A0A2R8YD90
ENSG00000101347ENST00000644250A0A2R8YDI8
ENSG00000101347ENST00000645033A0A2R8Y5D2
ENSG00000101347ENST00000645444A0A2R8Y6J9
ENSG00000101347ENST00000646066Q9Y3Z3
ENSG00000101347ENST00000646121A0A2R8YG48
ENSG00000101347ENST00000646673Q9Y3Z3
ENSG00000101347ENST00000646866A0A2R8Y755
ENSG00000101347ENST00000646869Q9Y3Z3
ENSG00000101347ENST00000646904A0A2R8YF51
ENSG00000101347ENST00000647163A0A2R8Y5D2

Expression (GTEx)

0
50
100
150
200
250
300
350
400
450
500

Pathways

PathwaySourceExternal ID
Immune SystemREACTOMER-HSA-168256
Cytokine Signaling in Immune systemREACTOMER-HSA-1280215
Interferon SignalingREACTOMER-HSA-913531
Interferon alpha/beta signalingREACTOMER-HSA-909733

Protein levels (Protein atlas)

Not detected
Low
Medium
High

PharmGKB

Entity IDNameTypeEvidenceAssociationPKPDPMIDs
PA445301Peripheral Nervous System DiseasesDiseaseClinicalAnnotationassociatedPD30273369
PA447230HIVDiseaseClinicalAnnotationassociatedPD30273369
PA451494stavudineChemicalClinicalAnnotationassociatedPD30273369

References

Pubmed IDYearTitleCitations
380412172024SAMHD1 compound heterozygous rare variants associated with moyamoya and mitral valve disease in the absence of other features of Aicardi-Goutières syndrome.0
383673012024SAMHD1 dysfunction induces IL-34 expression via NF-κB p65 in neuronal SH-SY5Y cells.0
380412172024SAMHD1 compound heterozygous rare variants associated with moyamoya and mitral valve disease in the absence of other features of Aicardi-Goutières syndrome.0
383673012024SAMHD1 dysfunction induces IL-34 expression via NF-κB p65 in neuronal SH-SY5Y cells.0
366897242023SAMHD1 single nucleotide polymorphisms impact outcome in children with newly diagnosed acute myeloid leukemia.3
368451382023SAMHD1 expression modulates innate immune activation and correlates with ovarian cancer prognosis.0
369344102023SAMHD1 restricts the deoxyguanosine triphosphate pool contributing to telomere stability in telomerase-positive cells.1
370097922023SAMHD1-induced endosomal FAK signaling promotes human renal clear cell carcinoma metastasis by activating Rac1-mediated lamellipodia protrusion.2
370373112023Purified recombinant lentiviral Vpx proteins maintain their SAMHD1 degradation efficiency in resting CD4(+) T cells.1
371002892023The host antiviral protein SAMHD1 suppresses NF-κB activation by interacting with the IKK complex during inflammatory responses and viral infection.1
372136662023Recombinant Klotho attenuates IFNγ receptor signaling and SAMHD1 expression through blocking NF-κB translocation in glomerular mesangial cells.0
372466442023Protein oxidation increases SAMHD1 binding ssDNA via its regulatory site.0
373281052023SAMHD1 impairs type I interferon induction through the MAVS, IKKε, and IRF7 signaling axis during viral infection.1
377810352023Activation of STING by SAMHD1 Deficiency Promotes PANoptosis and Enhances Efficacy of PD-L1 Blockade in Diffuse Large B-cell Lymphoma.2
378009142023Gene editing of SAMHD1 in macrophage-like cells reveals complex relationships between SAMHD1 phospho-regulation, HIV-1 restriction, and cellular dNTP levels.1

Citation

Dessen P

SAMHD1 (SAM and HD domain containing deoxynucleoside triphosphate triphosphohydrolase 1)

Atlas Genet Cytogenet Oncol Haematol. 2013-05-01

Online version: http://atlasgeneticsoncology.org/gene/53284/samhd1-(sam-and-hd-domain-containing-deoxynucleoside-triphosphate-triphosphohydrolase-1)