CLN5 (CLN5 intracellular trafficking protein)

2014-08-01  

Identity

HGNC
LOCATION
13q22.3
LOCUSID
ALIAS
-
FUSION GENES

Other Information

Locus ID:

NCBI: 1203
MIM: 608102
HGNC: 2076
Ensembl: ENSG00000102805

Variants:

dbSNP: 1203
ClinVar: 1203
TCGA: ENSG00000102805
COSMIC: CLN5

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000102805ENST00000377453O75503
ENSG00000102805ENST00000485938A0A087WZY0
ENSG00000102805ENST00000616833A0A1C7CYZ2
ENSG00000102805ENST00000635915A0A1B0GVL0
ENSG00000102805ENST00000636183O75503
ENSG00000102805ENST00000636525A0A1B0GUE8
ENSG00000102805ENST00000636681A0A1B0GU14
ENSG00000102805ENST00000636705A0A1B0GWI2
ENSG00000102805ENST00000636767A0A1B0GTV7
ENSG00000102805ENST00000636780A0A1B0GTR6
ENSG00000102805ENST00000637397A0A1B0GV94
ENSG00000102805ENST00000637537A0A1B0GTR6

Expression (GTEx)

0
5
10
15

Pathways

PathwaySourceExternal ID
LysosomeKEGGko04142
LysosomeKEGGhsa04142

Protein levels (Protein atlas)

Not detected
Low
Medium
High

References

Pubmed IDYearTitleCitations
363680772023Lysosomal dysfunction, autophagic defects, and CLN5 accumulation underlie the pathogenesis of KCTD7-mutated neuronal ceroid lipofuscinoses.1
377082592023The Batten disease gene product CLN5 is the lysosomal bis(monoacylglycero)phosphate synthase.3
363680772023Lysosomal dysfunction, autophagic defects, and CLN5 accumulation underlie the pathogenesis of KCTD7-mutated neuronal ceroid lipofuscinoses.1
377082592023The Batten disease gene product CLN5 is the lysosomal bis(monoacylglycero)phosphate synthase.3
354271572022Cln5 represents a new type of cysteine-based S-depalmitoylase linked to neurodegeneration.4
354271572022Cln5 represents a new type of cysteine-based S-depalmitoylase linked to neurodegeneration.4
335072092021Association of the Recurrent Rare Variant c.415T>C p.Phe139Leu in CLN5 With a Recessively Inherited Macular Dystrophy.4
346800452021Deficiency of the Lysosomal Protein CLN5 Alters Lysosomal Function and Movement.11
335072092021Association of the Recurrent Rare Variant c.415T>C p.Phe139Leu in CLN5 With a Recessively Inherited Macular Dystrophy.4
346800452021Deficiency of the Lysosomal Protein CLN5 Alters Lysosomal Function and Movement.11
323028052020Novel likely disease-causing CLN5 variants identified in Pakistani patients with neuronal ceroid lipofuscinosis.1
323933392020A novel pathogenic frameshift variant unmasked by a large de novo deletion at 13q21.33-q31.1 in a Chinese patient with neuronal ceroid lipofuscinosis type 5.3
324871412020CLN5 in heterozygosis may protect against the development of tumors in a VHL patient.4
323028052020Novel likely disease-causing CLN5 variants identified in Pakistani patients with neuronal ceroid lipofuscinosis.1
323933392020A novel pathogenic frameshift variant unmasked by a large de novo deletion at 13q21.33-q31.1 in a Chinese patient with neuronal ceroid lipofuscinosis type 5.3

Citation

Dessen P

CLN5 (CLN5 intracellular trafficking protein)

Atlas Genet Cytogenet Oncol Haematol. 2014-08-01

Online version: http://atlasgeneticsoncology.org/gene/54219/cln5-(cln5-intracellular-trafficking-protein)