PTDSS1 (phosphatidylserine synthase 1)

2014-08-01  

Identity

HGNC
LOCATION
8q22.1
LOCUSID
ALIAS
LMHD,PSS1,PSSA
FUSION GENES

Other Information

Locus ID:

NCBI: 9791
MIM: 612792
HGNC: 9587
Ensembl: ENSG00000156471

Variants:

dbSNP: 9791
ClinVar: 9791
TCGA: ENSG00000156471
COSMIC: PTDSS1

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000156471ENST00000337004J3KNR6
ENSG00000156471ENST00000517309P48651
ENSG00000156471ENST00000522072P48651

Expression (GTEx)

0
10
20
30
40
50
60
70

Pathways

PathwaySourceExternal ID
Glycerophospholipid metabolismKEGGko00564
Glycerophospholipid metabolismKEGGhsa00564
Metabolic pathwaysKEGGhsa01100
MetabolismREACTOMER-HSA-1430728
Metabolism of lipids and lipoproteinsREACTOMER-HSA-556833
Phospholipid metabolismREACTOMER-HSA-1483257
Glycerophospholipid biosynthesisREACTOMER-HSA-1483206
Synthesis of PSREACTOMER-HSA-1483101

Protein levels (Protein atlas)

Not detected
Low
Medium
High

References

Pubmed IDYearTitleCitations
377144102023Disease-related PSS1 mutant impedes the formation and function of osteoclasts.0
377144102023Disease-related PSS1 mutant impedes the formation and function of osteoclasts.0
345160422021Topology of phosphatidylserine synthase 1 in the endoplasmic reticulum membrane.3
345160422021Topology of phosphatidylserine synthase 1 in the endoplasmic reticulum membrane.3
312315132019Analysis of transgenic zebrafish expressing the Lenz-Majewski syndrome gene PTDSS1 in skeletal cell lineages.4
312315132019Analysis of transgenic zebrafish expressing the Lenz-Majewski syndrome gene PTDSS1 in skeletal cell lineages.4
293414802018Cutis laxa and excessive bone growth due to de novo mutations in PTDSS1.7
293414802018Cutis laxa and excessive bone growth due to de novo mutations in PTDSS1.7
267424922016RYR2, PTDSS1 and AREG genes are implicated in a Lebanese population-based study of copy number variation in autism.17
270440992016Lenz-Majewski mutations in PTDSS1 affect phosphatidylinositol 4-phosphate metabolism at ER-PM and ER-Golgi junctions.58
267424922016RYR2, PTDSS1 and AREG genes are implicated in a Lebanese population-based study of copy number variation in autism.17
270440992016Lenz-Majewski mutations in PTDSS1 affect phosphatidylinositol 4-phosphate metabolism at ER-PM and ER-Golgi junctions.58
242415352014Gain-of-function mutations in the phosphatidylserine synthase 1 (PTDSS1) gene cause Lenz-Majewski syndrome.36
242415352014Gain-of-function mutations in the phosphatidylserine synthase 1 (PTDSS1) gene cause Lenz-Majewski syndrome.36
203796142010Personalized smoking cessation: interactions between nicotine dose, dependence and quit-success genotype score.78

Citation

Dessen P

PTDSS1 (phosphatidylserine synthase 1)

Atlas Genet Cytogenet Oncol Haematol. 2014-08-01

Online version: http://atlasgeneticsoncology.org/gene/54563/ptdss1-(phosphatidylserine-synthase-1)