OTOF (otoferlin)

2016-10-01  

Identity

HGNC
LOCATION
2p23.3
LOCUSID
ALIAS
AUNB1,DFNB6,DFNB9,FER1L2,NSRD9

Other Information

Locus ID:

NCBI: 9381
MIM: 603681
HGNC: 8515
Ensembl: ENSG00000115155

Variants:

dbSNP: 9381
ClinVar: 9381
TCGA: ENSG00000115155
COSMIC: OTOF

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000115155ENST00000272371Q9HC10
ENSG00000115155ENST00000338581Q9HC10
ENSG00000115155ENST00000339598Q9HC10
ENSG00000115155ENST00000402415A0A2U3TZT7
ENSG00000115155ENST00000403946Q9HC10
ENSG00000115155ENST00000426958H7BZJ5

Expression (GTEx)

0
5
10
15
20

Protein levels (Protein atlas)

Not detected
Low
Medium
High

References

Pubmed IDYearTitleCitations
388111762024[The updates of the ACMG variant interpretation guidelines affect the pathogenicity determination of OTOF gene variations in patients with auditory neuropathy].0
388111762024[The updates of the ACMG variant interpretation guidelines affect the pathogenicity determination of OTOF gene variations in patients with auditory neuropathy].0
363832532023Hearing of Otof-deficient mice restored by trans-splicing of N- and C-terminal otoferlin.20
369881342023Intronic OTOF mutation causes an atypical splicing defect resulting in auditory neuropathy spectrum disorder.0
371892002023Loss-of-function mutations in MYO15A and OTOF cause non-syndromic hearing loss in two Yemeni families.2
381390692023Predicting the Impact of OTOF Gene Missense Variants on Auditory Neuropathy Spectrum Disorder.0
363832532023Hearing of Otof-deficient mice restored by trans-splicing of N- and C-terminal otoferlin.20
369881342023Intronic OTOF mutation causes an atypical splicing defect resulting in auditory neuropathy spectrum disorder.0
371892002023Loss-of-function mutations in MYO15A and OTOF cause non-syndromic hearing loss in two Yemeni families.2
381390692023Predicting the Impact of OTOF Gene Missense Variants on Auditory Neuropathy Spectrum Disorder.0
344244072022The natural history of OTOF-related auditory neuropathy spectrum disorders: a multicenter study.9
345361242022Detailed clinical features and genotype-phenotype correlation in an OTOF-related hearing loss cohort in Japan.4
358627902022Membrane Protein OTOF Is a Type I Interferon-Induced Entry Inhibitor of HIV-1 in Macrophages.4
344244072022The natural history of OTOF-related auditory neuropathy spectrum disorders: a multicenter study.9
345361242022Detailed clinical features and genotype-phenotype correlation in an OTOF-related hearing loss cohort in Japan.4

Citation

Dessen P

OTOF (otoferlin)

Atlas Genet Cytogenet Oncol Haematol. 2016-10-01

Online version: http://atlasgeneticsoncology.org/gene/56122/otof-(otoferlin)