LDLRAP1 (low density lipoprotein receptor adaptor protein 1)

2016-10-01  

Identity

HGNC
LOCATION
1p36.11
LOCUSID
ALIAS
ARH,ARH1,ARH2,FHCB1,FHCB2,FHCL4
FUSION GENES

Other Information

Locus ID:

NCBI: 26119
MIM: 605747
HGNC: 18640
Ensembl: ENSG00000157978

Variants:

dbSNP: 26119
ClinVar: 26119
TCGA: ENSG00000157978
COSMIC: LDLRAP1

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000157978ENST00000374338Q5SW96

Expression (GTEx)

0
50
100
150

Pathways

PathwaySourceExternal ID
EndocytosisKEGGko04144
EndocytosisKEGGhsa04144
Vesicle-mediated transportREACTOMER-HSA-5653656
Membrane TraffickingREACTOMER-HSA-199991
MetabolismREACTOMER-HSA-1430728
Metabolism of lipids and lipoproteinsREACTOMER-HSA-556833
Lipid digestion, mobilization, and transportREACTOMER-HSA-73923
Lipoprotein metabolismREACTOMER-HSA-174824
Chylomicron-mediated lipid transportREACTOMER-HSA-174800
LDL-mediated lipid transportREACTOMER-HSA-171052
Clathrin-mediated endocytosisREACTOMER-HSA-8856828
Cargo recognition for clathrin-mediated endocytosisREACTOMER-HSA-8856825

Protein levels (Protein atlas)

Not detected
Low
Medium
High

References

Pubmed IDYearTitleCitations
344256702021A Novel Splice Site Variant in the LDLRAP1 Gene Causes Familial Hypercholesterolemia.1
344256702021A Novel Splice Site Variant in the LDLRAP1 Gene Causes Familial Hypercholesterolemia.1
320731922020Molecular insights into the coding region mutations of low-density lipoprotein receptor adaptor protein 1 (LDLRAP1) linked to familial hypercholesterolemia.4
320731922020Molecular insights into the coding region mutations of low-density lipoprotein receptor adaptor protein 1 (LDLRAP1) linked to familial hypercholesterolemia.4
308768772019A case of autosomal recessive hypercholesterolemia caused by a new variant in the LDL receptor adaptor protein 1 gene.2
309712882019Effects of familial hypercholesterolemia-associated genes on the phenotype of premature myocardial infarction.4
308768772019A case of autosomal recessive hypercholesterolemia caused by a new variant in the LDL receptor adaptor protein 1 gene.2
309712882019Effects of familial hypercholesterolemia-associated genes on the phenotype of premature myocardial infarction.4
302700812018Novel combined variants of LDLR and LDLRAP1 genes causing severe familial hypercholesterolemia.6
302700812018Novel combined variants of LDLR and LDLRAP1 genes causing severe familial hypercholesterolemia.6
289583302017Genetically Confirmed Familial Hypercholesterolemia in Patients With Acute Coronary Syndrome.51
289634842017Understanding the differences of the ligand binding/unbinding pathways between phosphorylated and non-phosphorylated ARH1 using molecular dynamics simulations.9
289583302017Genetically Confirmed Familial Hypercholesterolemia in Patients With Acute Coronary Syndrome.51
289634842017Understanding the differences of the ligand binding/unbinding pathways between phosphorylated and non-phosphorylated ARH1 using molecular dynamics simulations.9
252251282015The history of Autosomal Recessive Hypercholesterolemia (ARH). From clinical observations to gene identification.17

Citation

Dessen P

LDLRAP1 (low density lipoprotein receptor adaptor protein 1)

Atlas Genet Cytogenet Oncol Haematol. 2016-10-01

Online version: http://atlasgeneticsoncology.org/gene/56131/ldlrap1-(low-density-lipoprotein-receptor-adaptor-protein-1)