GLRA1 (glycine receptor alpha 1)

2016-10-01  

Identity

HGNC
LOCATION
5q33.1
LOCUSID
ALIAS
HKPX1,STHE
FUSION GENES

Other Information

Locus ID:

NCBI: 2741
MIM: 138491
HGNC: 4326
Ensembl: ENSG00000145888

Variants:

dbSNP: 2741
ClinVar: 2741
TCGA: ENSG00000145888
COSMIC: GLRA1

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000145888ENST00000274576P23415
ENSG00000145888ENST00000455880P23415
ENSG00000145888ENST00000462581E5RJ70

Expression (GTEx)

0
1

Pathways

PathwaySourceExternal ID
Neuroactive ligand-receptor interactionKEGGko04080
Neuroactive ligand-receptor interactionKEGGhsa04080
Transmembrane transport of small moleculesREACTOMER-HSA-382551
Ion channel transportREACTOMER-HSA-983712
Ligand-gated ion channel transportREACTOMER-HSA-975298

Protein levels (Protein atlas)

Not detected
Low
Medium
High

References

Pubmed IDYearTitleCitations
364349172022Four Turkish families with hyperekplexia: A missense mutation and the exon 1-7 deletion in the GLRA1 gene.0
364349172022Four Turkish families with hyperekplexia: A missense mutation and the exon 1-7 deletion in the GLRA1 gene.0
317578082020The synthetic cannabinoid dehydroxylcannabidiol restores the function of a major GABA(A) receptor isoform in a cell model of hyperekplexia.3
323548532020A Novel Glycine Receptor Variant with Startle Disease Affects Syndapin I and Glycinergic Inhibition.7
324454912020The startle disease mutation α1S270T predicts shortening of glycinergic synaptic currents.2
317578082020The synthetic cannabinoid dehydroxylcannabidiol restores the function of a major GABA(A) receptor isoform in a cell model of hyperekplexia.3
323548532020A Novel Glycine Receptor Variant with Startle Disease Affects Syndapin I and Glycinergic Inhibition.7
324454912020The startle disease mutation α1S270T predicts shortening of glycinergic synaptic currents.2
307216952019Ubiquitination and inhibition of glycine receptor by HUWE1 in spinal cord dorsal horn.8
308668512019Clinical features and genetic analysis of two siblings with startle disease in an Italian family: a case report.4
307216952019Ubiquitination and inhibition of glycine receptor by HUWE1 in spinal cord dorsal horn.8
308668512019Clinical features and genetic analysis of two siblings with startle disease in an Italian family: a case report.4
287588852018Dimensional Traits of Schizotypy Associated With Glycine Receptor GLRA1 Polymorphism: An Exploratory Candidate-Gene Association Study.3
291492362018Mutations affecting glycinergic neurotransmission in hyperekplexia increase pain sensitivity.15
299414552018Multiple regions in the extracellular domain of the glycine receptor determine receptor activity.3

Citation

Dessen P

GLRA1 (glycine receptor alpha 1)

Atlas Genet Cytogenet Oncol Haematol. 2016-10-01

Online version: http://atlasgeneticsoncology.org/gene/56133/glra1-(glycine-receptor-alpha-1)