RPGRIP1 (RPGR interacting protein 1)

2016-10-01  

Identity

HGNC
LOCATION
14q11.2
LOCUSID
ALIAS
CORD13,LCA6,RGI1,RGRIP,RPGRIP,RPGRIP1d

Other Information

Locus ID:

NCBI: 57096
MIM: 605446
HGNC: 13436
Ensembl: ENSG00000092200

Variants:

dbSNP: 57096
ClinVar: 57096
TCGA: ENSG00000092200
COSMIC: RPGRIP1

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000092200ENST00000382933Q96KN7
ENSG00000092200ENST00000400017Q96KN7
ENSG00000092200ENST00000554303H0YIY1
ENSG00000092200ENST00000555322H0YJ18
ENSG00000092200ENST00000555489H0YJ99
ENSG00000092200ENST00000555587G3V3I7
ENSG00000092200ENST00000556336G3V236
ENSG00000092200ENST00000557351G3V577
ENSG00000092200ENST00000557606H0YJK6
ENSG00000092200ENST00000557771G3V3F7

Expression (GTEx)

0
5
10
15
20
25
30
35
40
45

Protein levels (Protein atlas)

Not detected
Low
Medium
High

References

Pubmed IDYearTitleCitations
367629972023RPGRIP1-related retinal disease presenting as isolated cone dysfunction.1
367629972023RPGRIP1-related retinal disease presenting as isolated cone dysfunction.1
336708322021Whole Locus Sequencing Identifies a Prevalent Founder Deep Intronic RPGRIP1 Pathologic Variant in the French Leber Congenital Amaurosis Cohort.4
339073652021Noncoding mutation in RPGRIP1 contributes to inherited retinal degenerations.7
339707602021Molecular genetics with clinical characteristics of Leber congenital amaurosis in the Han population of western China.5
336708322021Whole Locus Sequencing Identifies a Prevalent Founder Deep Intronic RPGRIP1 Pathologic Variant in the French Leber Congenital Amaurosis Cohort.4
339073652021Noncoding mutation in RPGRIP1 contributes to inherited retinal degenerations.7
339707602021Molecular genetics with clinical characteristics of Leber congenital amaurosis in the Han population of western China.5
328653132020Clinical and molecular findings in a cohort of 152 Brazilian severe early onset inherited retinal dystrophy patients.11
328653132020Clinical and molecular findings in a cohort of 152 Brazilian severe early onset inherited retinal dystrophy patients.11
304989072019Thumb duplication: molecular analysis of different clinical types.2
304989072019Thumb duplication: molecular analysis of different clinical types.2
291937632018Identification of a novel RPGRIP1 mutation in an Iranian family with leber congenital amaurosis by exome sequencing.15
296506802018Cell type-specific regulation of ciliary transition zone assembly in vertebrates.36
291937632018Identification of a novel RPGRIP1 mutation in an Iranian family with leber congenital amaurosis by exome sequencing.15

Citation

Dessen P

RPGRIP1 (RPGR interacting protein 1)

Atlas Genet Cytogenet Oncol Haematol. 2016-10-01

Online version: http://atlasgeneticsoncology.org/gene/56179/rpgrip1-(rpgr-interacting-protein-1)