NPC2 (NPC intracellular cholesterol transporter 2)

2016-10-01  

Identity

HGNC
LOCATION
14q24.3
LOCUSID
ALIAS
EDDM1,HE1
FUSION GENES

Other Information

Locus ID:

NCBI: 10577
MIM: 601015
HGNC: 14537
Ensembl: ENSG00000119655

Variants:

dbSNP: 10577
ClinVar: 10577
TCGA: ENSG00000119655
COSMIC: NPC2

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000119655ENST00000238633J3KMY5
ENSG00000119655ENST00000434013E7EMS2
ENSG00000119655ENST00000541064P61916
ENSG00000119655ENST00000553490G3V3D1
ENSG00000119655ENST00000554482H0YJE2
ENSG00000119655ENST00000555592G3V2V8
ENSG00000119655ENST00000555619P61916
ENSG00000119655ENST00000555619A0A024R6C0
ENSG00000119655ENST00000556009H0YIZ1
ENSG00000119655ENST00000557510G3V3E8

Expression (GTEx)

0
50
100
150
200
250

Pathways

PathwaySourceExternal ID
LysosomeKEGGko04142
LysosomeKEGGhsa04142
Immune SystemREACTOMER-HSA-168256
Innate Immune SystemREACTOMER-HSA-168249
MetabolismREACTOMER-HSA-1430728
Metabolism of lipids and lipoproteinsREACTOMER-HSA-556833
Lipid digestion, mobilization, and transportREACTOMER-HSA-73923
Lipoprotein metabolismREACTOMER-HSA-174824
LDL-mediated lipid transportREACTOMER-HSA-171052
Neutrophil degranulationREACTOMER-HSA-6798695

Protein levels (Protein atlas)

Not detected
Low
Medium
High

References

Pubmed IDYearTitleCitations
334225482021Niemann Pick C2 protein enables cholesterol transfer from endo-lysosomes to the plasma membrane for efflux by shedding of extracellular vesicles.8
337233312021Increase in plasma Niemann-Pick disease type C2 protein is associated with poor prognosis of sepsis.1
339906402021Identification and Classification of Rare Variants in NPC1 and NPC2 in Quebec.2
344209592021Niemann-Pick Type C 1 (NPC1) and NPC2 Gene Variability in Demented Patients with Evidence of Brain Amyloid Deposition.3
344452792021Secretory NPC2 Protein-Mediated Free Cholesterol Levels Were Correlated with the Sorafenib Response in Hepatocellular Carcinoma.4
346856832021Transcriptomic Biomarkers for Tuberculosis: Validation of NPC2 as a Single mRNA Biomarker to Diagnose TB, Predict Disease Progression, and Monitor Treatment Response.3
334225482021Niemann Pick C2 protein enables cholesterol transfer from endo-lysosomes to the plasma membrane for efflux by shedding of extracellular vesicles.8
337233312021Increase in plasma Niemann-Pick disease type C2 protein is associated with poor prognosis of sepsis.1
339906402021Identification and Classification of Rare Variants in NPC1 and NPC2 in Quebec.2
344209592021Niemann-Pick Type C 1 (NPC1) and NPC2 Gene Variability in Demented Patients with Evidence of Brain Amyloid Deposition.3
344452792021Secretory NPC2 Protein-Mediated Free Cholesterol Levels Were Correlated with the Sorafenib Response in Hepatocellular Carcinoma.4
346856832021Transcriptomic Biomarkers for Tuberculosis: Validation of NPC2 as a Single mRNA Biomarker to Diagnose TB, Predict Disease Progression, and Monitor Treatment Response.3
288659472020New variant associated with Niemann-Pick disease type C: Neurological manifestations and biochemical, molecular, and cellular characterisation.0
315216312020Binding and intracellular transport of 25-hydroxycholesterol by Niemann-Pick C2 protein.5
325443842020Structural Basis of Low-pH-Dependent Lysosomal Cholesterol Egress by NPC1 and NPC2.59

Citation

Dessen P

NPC2 (NPC intracellular cholesterol transporter 2)

Atlas Genet Cytogenet Oncol Haematol. 2016-10-01

Online version: http://atlasgeneticsoncology.org/gene/56443/npc2-(npc-intracellular-cholesterol-transporter-2)