PNPLA6 (patatin like phospholipase domain containing 6)

2016-10-01  

Identity

HGNC
LOCATION
19p13.2
LOCUSID
ALIAS
BNHS,LNMS,NTE,NTEMND,OMCS,SPG39,iPLA2delta,sws
FUSION GENES

Other Information

Locus ID:

NCBI: 10908
MIM: 603197
HGNC: 16268
Ensembl: ENSG00000032444

Variants:

dbSNP: 10908
ClinVar: 10908
TCGA: ENSG00000032444
COSMIC: PNPLA6

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000032444ENST00000221249Q8IY17
ENSG00000032444ENST00000414982Q8IY17
ENSG00000032444ENST00000450331Q8IY17
ENSG00000032444ENST00000545201Q8IY17
ENSG00000032444ENST00000593924M0QYF5
ENSG00000032444ENST00000594551M0QYT1
ENSG00000032444ENST00000595264M0R2C2
ENSG00000032444ENST00000596515M0QZD1
ENSG00000032444ENST00000599947M0QXH7
ENSG00000032444ENST00000600737A0A384DVU0
ENSG00000032444ENST00000600942M0R2H4
ENSG00000032444ENST00000601001M0R2K2
ENSG00000032444ENST00000601668M0QZK5
ENSG00000032444ENST00000646984A0A2R8Y7E1

Expression (GTEx)

0
10
20
30
40
50
60
70
80

Pathways

PathwaySourceExternal ID
Glycerophospholipid metabolismKEGGko00564
Glycerophospholipid metabolismKEGGhsa00564
MetabolismREACTOMER-HSA-1430728
Metabolism of lipids and lipoproteinsREACTOMER-HSA-556833
Phospholipid metabolismREACTOMER-HSA-1483257
PI MetabolismREACTOMER-HSA-1483255
Glycerophospholipid catabolismREACTOMER-HSA-6814848

Protein levels (Protein atlas)

Not detected
Low
Medium
High

References

Pubmed IDYearTitleCitations
386832452024Two case reports of a novel missense mutation in the PNPLA6 gene in two siblings with chorioretinal dystrophy, hypogonadotropic hypogonadism, and cerebellar ataxia.0
387356472024Neuropathy target esterase activity defines phenotypes among PNPLA6 disorders.0
386832452024Two case reports of a novel missense mutation in the PNPLA6 gene in two siblings with chorioretinal dystrophy, hypogonadotropic hypogonadism, and cerebellar ataxia.0
387356472024Neuropathy target esterase activity defines phenotypes among PNPLA6 disorders.0
363362122023The alteration of the expression level of neuropathy target esterase in human neuroblastoma SK-N-SH cells disrupts cellular phospholipids homeostasis.2
363362122023The alteration of the expression level of neuropathy target esterase in human neuroblastoma SK-N-SH cells disrupts cellular phospholipids homeostasis.2
300157752021CHORIORETINAL CHANGES IN A GENETICALLY CONFIRMED CASE OF BOUCHER-NEUHÄUSER SYNDROME.5
331410492021Novel variants in PNPLA6 causing syndromic retinal dystrophy.8
331849062021Reduced neuropathy target esterase in pre-eclampsia suppresses tube formation of HUVECs via dysregulation of phospholipid metabolism.1
332102272021A novel PNPLA6 mutation in a Turkish family with intractable Holmes tremor and spastic ataxia.9
336504662021Chorioretinal dystrophy, hypogonadotropic hypogonadism, and cerebellar ataxia: Boucher-Neuhauser syndrome due to a homozygous (c.3524C>G (p.Ser1175Cys)) variant in PNPLA6 gene.5
338182692021Oliver McFarlane syndrome: two new cases and a review of the literature.5
300157752021CHORIORETINAL CHANGES IN A GENETICALLY CONFIRMED CASE OF BOUCHER-NEUHÄUSER SYNDROME.5
331410492021Novel variants in PNPLA6 causing syndromic retinal dystrophy.8
331849062021Reduced neuropathy target esterase in pre-eclampsia suppresses tube formation of HUVECs via dysregulation of phospholipid metabolism.1

Citation

Dessen P

PNPLA6 (patatin like phospholipase domain containing 6)

Atlas Genet Cytogenet Oncol Haematol. 2016-10-01

Online version: http://atlasgeneticsoncology.org/gene/56457/pnpla6-(patatin-like-phospholipase-domain-containing-6)