LHFPL5 (LHFPL tetraspan subfamily member 5)

2016-10-01  

Identity

HGNC
LOCATION
6p21.31
LOCUSID
ALIAS
DFNB67,TMHS,dJ510O8.8
FUSION GENES

Other Information

Locus ID:

NCBI: 222662
MIM: 609427
HGNC: 21253
Ensembl: ENSG00000197753

Variants:

dbSNP: 222662
ClinVar: 222662
TCGA: ENSG00000197753
COSMIC: LHFPL5

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000197753ENST00000360215Q8TAF8
ENSG00000197753ENST00000651132Q8TAF8
ENSG00000197753ENST00000651676Q8TAF8
ENSG00000197753ENST00000651994A0A494BZZ7
ENSG00000197753ENST00000652718A0A494C136

Expression (GTEx)

0
1
2
3

Protein levels (Protein atlas)

Not detected
Low
Medium
High

References

Pubmed IDYearTitleCitations
378375602024Panoramic variation analysis of a family with neurodevelopmental disorders caused by biallelic loss-of-function variants in TMEM141, DDHD2, and LHFPL5.0
378375602024Panoramic variation analysis of a family with neurodevelopmental disorders caused by biallelic loss-of-function variants in TMEM141, DDHD2, and LHFPL5.0
331687092020Deafness mutation D572N of TMC1 destabilizes TMC1 expression by disrupting LHFPL5 binding.18
331687092020Deafness mutation D572N of TMC1 destabilizes TMC1 expression by disrupting LHFPL5 binding.18
302986222019High prevalence of congenital deafness on Reunion Island is due to a founder variant of LHFPL5.1
304766272019LHFPL5 mutation: A rare cause of non-syndromic autosomal recessive hearing loss.1
311261772019Novel Mutations in KCNQ4, LHFPL5 and COCH Genes in Iranian Families with Hearing Impairment.7
302986222019High prevalence of congenital deafness on Reunion Island is due to a founder variant of LHFPL5.1
304766272019LHFPL5 mutation: A rare cause of non-syndromic autosomal recessive hearing loss.1
311261772019Novel Mutations in KCNQ4, LHFPL5 and COCH Genes in Iranian Families with Hearing Impairment.7
301778092018Novel missense and 3'-UTR splice site variants in LHFPL5 cause autosomal recessive nonsyndromic hearing impairment.1
301778092018Novel missense and 3'-UTR splice site variants in LHFPL5 cause autosomal recessive nonsyndromic hearing impairment.1
264378812016Clinical and molecular delineation of dysequilibrium syndrome type 2 and profound sensorineural hearing loss in an inbred Arab family.6
269649002016Novel function of LHFPL2 in female and male distal reproductive tract development.11
264378812016Clinical and molecular delineation of dysequilibrium syndrome type 2 and profound sensorineural hearing loss in an inbred Arab family.6

Citation

Dessen P

LHFPL5 (LHFPL tetraspan subfamily member 5)

Atlas Genet Cytogenet Oncol Haematol. 2016-10-01

Online version: http://atlasgeneticsoncology.org/gene/56500/lhfpl5-(lhfpl-tetraspan-subfamily-member-5)