GFM1 (G elongation factor mitochondrial 1)

2017-01-01  

Identity

HGNC
LOCATION
3q25.32
LOCUSID
ALIAS
COXPD1,EFG,EFG1,EFGM,EGF1,GFM,hEFG1,mtEF-G1
FUSION GENES

Other Information

Locus ID:

NCBI: 85476
MIM: 606639
HGNC: 13780
Ensembl: ENSG00000168827

Variants:

dbSNP: 85476
ClinVar: 85476
TCGA: ENSG00000168827
COSMIC: GFM1

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000168827ENST00000264263Q96RP9
ENSG00000168827ENST00000464732C9JA25
ENSG00000168827ENST00000472383H7C5M4
ENSG00000168827ENST00000478254F8WAU4
ENSG00000168827ENST00000478576C9IZ01
ENSG00000168827ENST00000486715Q96RP9
ENSG00000168827ENST00000486715E5KND5

Expression (GTEx)

0
5
10
15
20
25
30
35
40
45
50

Pathways

PathwaySourceExternal ID
Organelle biogenesis and maintenanceREACTOMER-HSA-1852241
Mitochondrial translationREACTOMER-HSA-5368287
Mitochondrial translation elongationREACTOMER-HSA-5389840

Protein levels (Protein atlas)

Not detected
Low
Medium
High

References

Pubmed IDYearTitleCitations
357030692022Whole exome sequencing identifies a novel compound heterozygous GFM1 variant underlying developmental delay, dystonia, polymicrogyria, and severe intellectual disability in a Pakhtun family.4
357030692022Whole exome sequencing identifies a novel compound heterozygous GFM1 variant underlying developmental delay, dystonia, polymicrogyria, and severe intellectual disability in a Pakhtun family.4
316803802020Clinical, neuroimaging and biochemical findings in patients and patient fibroblasts expressing ten novel GFM1 mutations.10
326025802020Structural insights into mammalian mitochondrial translation elongation catalyzed by mtEFG1.20
327373132020Structures of the human mitochondrial ribosome bound to EF-G1 reveal distinct features of mitochondrial translation elongation.22
332104822020[Analysis of GFM1 gene mutations in a family with combined oxidative phosphorylation deficiency 1].0
316803802020Clinical, neuroimaging and biochemical findings in patients and patient fibroblasts expressing ten novel GFM1 mutations.10
326025802020Structural insights into mammalian mitochondrial translation elongation catalyzed by mtEFG1.20
327373132020Structures of the human mitochondrial ribosome bound to EF-G1 reveal distinct features of mitochondrial translation elongation.22
332104822020[Analysis of GFM1 gene mutations in a family with combined oxidative phosphorylation deficiency 1].0
282162302017Activation of a cryptic splice site in the mitochondrial elongation factor GFM1 causes combined OXPHOS deficiency.12
282162302017Activation of a cryptic splice site in the mitochondrial elongation factor GFM1 causes combined OXPHOS deficiency.12
268909912016Enhanced Antitumor Activity of EGFP-EGF1-Conjugated Nanoparticles by a Multitargeting Strategy.8
268909912016Enhanced Antitumor Activity of EGFP-EGF1-Conjugated Nanoparticles by a Multitargeting Strategy.8
219865552012Toward genotype phenotype correlations in GFM1 mutations.9

Citation

Dessen P

GFM1 (G elongation factor mitochondrial 1)

Atlas Genet Cytogenet Oncol Haematol. 2017-01-01

Online version: http://atlasgeneticsoncology.org/gene/56719/gfm1-(g-elongation-factor-mitochondrial-1)