GM2A (GM2 ganglioside activator)

2017-04-01  

Identity

HGNC
LOCATION
5q33.1
LOCUSID
ALIAS
GM2-AP,SAP-3
FUSION GENES

Other Information

Locus ID:

NCBI: 2760
MIM: 613109
HGNC: 4367
Ensembl: ENSG00000196743

Variants:

dbSNP: 2760
ClinVar: 2760
TCGA: ENSG00000196743
COSMIC: GM2A

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000196743ENST00000357164P17900
ENSG00000196743ENST00000523004H0YBY3
ENSG00000196743ENST00000523466E5RJD0

Expression (GTEx)

0
50
100
150

Pathways

PathwaySourceExternal ID
LysosomeKEGGko04142
LysosomeKEGGhsa04142
Immune SystemREACTOMER-HSA-168256
Innate Immune SystemREACTOMER-HSA-168249
MetabolismREACTOMER-HSA-1430728
Metabolism of lipids and lipoproteinsREACTOMER-HSA-556833
Sphingolipid metabolismREACTOMER-HSA-428157
Glycosphingolipid metabolismREACTOMER-HSA-1660662
Neutrophil degranulationREACTOMER-HSA-6798695

Protein levels (Protein atlas)

Not detected
Low
Medium
High

References

Pubmed IDYearTitleCitations
338194152021Two patients from Turkey with a novel variant in the GM2A gene and review of the literature.4
338194152021Two patients from Turkey with a novel variant in the GM2A gene and review of the literature.4
315784522019GM2-GM3 gangliosides ratio is dependent on GRP94 through down-regulation of GM2-AP cofactor in brain metastasis cells.3
315784522019GM2-GM3 gangliosides ratio is dependent on GRP94 through down-regulation of GM2-AP cofactor in brain metastasis cells.3
270024802016Identification of ganglioside GM2 activator playing a role in cancer cell migration through proteomic analysis of breast cancer secretomes.16
271572702016Neuronal sphingolipidoses: Membrane lipids and sphingolipid activator proteins regulate lysosomal sphingolipid catabolism.20
274020912016GM2 gangliosidosis AB variant: novel mutation from India - a case report with a review.13
270024802016Identification of ganglioside GM2 activator playing a role in cancer cell migration through proteomic analysis of breast cancer secretomes.16
271572702016Neuronal sphingolipidoses: Membrane lipids and sphingolipid activator proteins regulate lysosomal sphingolipid catabolism.20
274020912016GM2 gangliosidosis AB variant: novel mutation from India - a case report with a review.13
258160112015Association of neonatal necrotizing enterocolitis with myeloid differentiation-2 and GM2 activator protein genetic polymorphisms.10
261754732015Membrane lipids regulate ganglioside GM2 catabolism and GM2 activator protein activity.17
258160112015Association of neonatal necrotizing enterocolitis with myeloid differentiation-2 and GM2 activator protein genetic polymorphisms.10
261754732015Membrane lipids regulate ganglioside GM2 catabolism and GM2 activator protein activity.17
234839392013In cellulo examination of a beta-alpha hybrid construct of beta-hexosaminidase A subunits, reported to interact with the GM2 activator protein and hydrolyze GM2 ganglioside.6

Citation

Dessen P

GM2A (GM2 ganglioside activator)

Atlas Genet Cytogenet Oncol Haematol. 2017-04-01

Online version: http://atlasgeneticsoncology.org/gene/56880/gm2a-(gm2-ganglioside-activator)