GAN (gigaxonin)

2017-08-01  

Identity

HGNC
LOCATION
16q23.2
LOCUSID
ALIAS
GAN1,GIG,KLHL16
FUSION GENES

Other Information

Locus ID:

NCBI: 8139
MIM: 605379
HGNC: 4137
Ensembl: ENSG00000261609

Variants:

dbSNP: 8139
ClinVar: 8139
TCGA: ENSG00000261609
COSMIC: GAN

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000261609ENST00000648349A0A3B3ITY2
ENSG00000261609ENST00000648994Q9H2C0
ENSG00000261609ENST00000648994A0A0S2Z4W2
ENSG00000261609ENST00000650388A0A0S2Z5G5

Expression (GTEx)

0
5
10
15
20
25
30
35

Pathways

PathwaySourceExternal ID
Immune SystemREACTOMER-HSA-168256
Adaptive Immune SystemREACTOMER-HSA-1280218
Class I MHC mediated antigen processing & presentationREACTOMER-HSA-983169
Antigen processing: Ubiquitination & Proteasome degradationREACTOMER-HSA-983168

Protein levels (Protein atlas)

Not detected
Low
Medium
High

References

Pubmed IDYearTitleCitations
370433922023Gigaxonin is required for intermediate filament transport.4
370433922023Gigaxonin is required for intermediate filament transport.4
357647472022Two novel pathogenic mutations of GAN gene identified in a chinese family with giant axonal neuropathy: a case report.0
357647472022Two novel pathogenic mutations of GAN gene identified in a chinese family with giant axonal neuropathy: a case report.0
335287282021Giant axonal neuropathy with novel GAN pathogenic variant in a patient of consanguineous origin from Poonch Jammu and Kashmir-India.0
335287282021Giant axonal neuropathy with novel GAN pathogenic variant in a patient of consanguineous origin from Poonch Jammu and Kashmir-India.0
316559222020Giant axonal neuropathy: a multicenter retrospective study with genotypic spectrum expansion.5
318529842020Identification of novel pathogenic copy number variations in Charcot-Marie-Tooth disease.4
316559222020Giant axonal neuropathy: a multicenter retrospective study with genotypic spectrum expansion.5
318529842020Identification of novel pathogenic copy number variations in Charcot-Marie-Tooth disease.4
315035512019Sonic Hedgehog repression underlies gigaxonin mutation-induced motor deficits in giant axonal neuropathy.13
315035512019Sonic Hedgehog repression underlies gigaxonin mutation-induced motor deficits in giant axonal neuropathy.13
294819042018KLHL16 Degrades Epidermal Keratins.7
294819042018KLHL16 Degrades Epidermal Keratins.7
264925782016Novel mutations in genes causing hereditary spastic paraplegia and Charcot-Marie-Tooth neuropathy identified by an optimized protocol for homozygosity mapping based on whole-exome sequencing.23

Citation

Dessen P

GAN (gigaxonin)

Atlas Genet Cytogenet Oncol Haematol. 2017-08-01

Online version: http://atlasgeneticsoncology.org/gene/57035/gan-(gigaxonin)