TELO2 (telomere maintenance 2)

2018-02-01  

Identity

HGNC
LOCATION
16p13.3
LOCUSID
ALIAS
CLK2,TEL2,YHFS
FUSION GENES

Other Information

Locus ID:

NCBI: 9894
MIM: 611140
HGNC: 29099
Ensembl: ENSG00000100726

Variants:

dbSNP: 9894
ClinVar: 9894
TCGA: ENSG00000100726
COSMIC: TELO2

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000100726ENST00000262319Q9Y4R8
ENSG00000100726ENST00000497339H3BRS3
ENSG00000100726ENST00000567423H3BU45

Expression (GTEx)

0
10
20
30
40
50
60
70

Pathways

PathwaySourceExternal ID
mTOR signaling pathwayKEGGko04150
mTOR signaling pathwayKEGGhsa04150
Fanconi anemia pathwayKEGGko03460
Fanconi anemia pathwayKEGGhsa03460

Protein levels (Protein atlas)

Not detected
Low
Medium
High

References

Pubmed IDYearTitleCitations
367975132023TELO2-related syndrome (You-Hoover-Fong syndrome): Description of 14 new affected individuals and review of the literature.3
367975132023TELO2-related syndrome (You-Hoover-Fong syndrome): Description of 14 new affected individuals and review of the literature.3
348385212022Structure of the Human TELO2-TTI1-TTI2 Complex.6
348385212022Structure of the Human TELO2-TTI1-TTI2 Complex.6
333072812021Milder presentation of TELO2-related syndrome in two sisters homozygous for the p.Arg609His pathogenic variant.3
334161772021TELO2 induced progression of colorectal cancer by binding with RICTOR through mTORC2.30
333072812021Milder presentation of TELO2-related syndrome in two sisters homozygous for the p.Arg609His pathogenic variant.3
334161772021TELO2 induced progression of colorectal cancer by binding with RICTOR through mTORC2.30
329400982020Cataract in You-Hoover-Fong syndrome: TELO2 deficiency.3
329400982020Cataract in You-Hoover-Fong syndrome: TELO2 deficiency.3
271325932016A Syndromic Intellectual Disability Disorder Caused by Variants in TELO2, a Gene Encoding a Component of the TTT Complex.21
273295942016Overexpression of TELO2 decreases survival in human high-grade gliomas.3
271325932016A Syndromic Intellectual Disability Disorder Caused by Variants in TELO2, a Gene Encoding a Component of the TTT Complex.21
273295942016Overexpression of TELO2 decreases survival in human high-grade gliomas.3
246571682014Inositol pyrophosphates mediate the DNA-PK/ATM-p53 cell death pathway by regulating CK2 phosphorylation of Tti1/Tel2.72

Citation

Dessen P

TELO2 (telomere maintenance 2)

Atlas Genet Cytogenet Oncol Haematol. 2018-02-01

Online version: http://atlasgeneticsoncology.org/gene/57266/telo2-(telomere-maintenance-2)