NHLRC2 (NHL repeat containing 2)

2018-11-01  

Identity

HGNC
LOCATION
10q25.3
LOCUSID
ALIAS
FINCA

Other Information

Locus ID:

NCBI: 374354
MIM: 618277
HGNC: 24731
Ensembl: ENSG00000196865

Variants:

dbSNP: 374354
ClinVar: 374354
TCGA: ENSG00000196865
COSMIC: NHLRC2

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000196865ENST00000369301Q8NBF2

Expression (GTEx)

0
5
10
15
20

Pathways

PathwaySourceExternal ID
HemostasisREACTOMER-HSA-109582
Platelet activation, signaling and aggregationREACTOMER-HSA-76002
Response to elevated platelet cytosolic Ca2+REACTOMER-HSA-76005
Platelet degranulationREACTOMER-HSA-114608

Protein levels (Protein atlas)

Not detected
Low
Medium
High

References

Pubmed IDYearTitleCitations
371888252023Broadening the phenotypic and molecular spectrum of FINCA syndrome: Biallelic NHLRC2 variants in 15 novel individuals.1
371888252023Broadening the phenotypic and molecular spectrum of FINCA syndrome: Biallelic NHLRC2 variants in 15 novel individuals.1
359640852022NHLRC2 expression is increased in idiopathic pulmonary fibrosis.3
359640852022NHLRC2 expression is increased in idiopathic pulmonary fibrosis.3
324350552020Novel compound heterozygous variants in NHLRC2 in a patient with FINCA syndrome.8
324350552020Novel compound heterozygous variants in NHLRC2 in a patient with FINCA syndrome.8
294238772018NHLRC2 variants identified in patients with fibrosis, neurodegeneration, and cerebral angiomatosis (FINCA): characterisation of a novel cerebropulmonary disease.13
301384172018Structural analysis of human NHLRC2, mutations of which are associated with FINCA disease.10
302397522018Biallelic mutations in human NHLRC2 enhance myofibroblast differentiation in FINCA disease.11
294238772018NHLRC2 variants identified in patients with fibrosis, neurodegeneration, and cerebral angiomatosis (FINCA): characterisation of a novel cerebropulmonary disease.13
301384172018Structural analysis of human NHLRC2, mutations of which are associated with FINCA disease.10
302397522018Biallelic mutations in human NHLRC2 enhance myofibroblast differentiation in FINCA disease.11
292425622017ROS-induced cleavage of NHLRC2 by caspase-8 leads to apoptotic cell death in the HCT116 human colon cancer cell line.26
292425622017ROS-induced cleavage of NHLRC2 by caspase-8 leads to apoptotic cell death in the HCT116 human colon cancer cell line.26
163854512006A scan of chromosome 10 identifies a novel locus showing strong association with late-onset Alzheimer disease.83

Citation

Dessen P

NHLRC2 (NHL repeat containing 2)

Atlas Genet Cytogenet Oncol Haematol. 2018-11-01

Online version: http://atlasgeneticsoncology.org/gene/57729/nhlrc2-(nhl-repeat-containing-2)