OSBPL2 (oxysterol binding protein like 2)

2018-11-01  

Identity

HGNC
LOCATION
20q13.33
LOCUSID
ALIAS
DFNA67,DNFA67,ORP-2,ORP2
FUSION GENES

Other Information

Locus ID:

NCBI: 9885
MIM: 606731
HGNC: 15761
Ensembl: ENSG00000130703

Variants:

dbSNP: 9885
ClinVar: 9885
TCGA: ENSG00000130703
COSMIC: OSBPL2

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000130703ENST00000313733Q9H1P3
ENSG00000130703ENST00000358053Q9H1P3
ENSG00000130703ENST00000439951E7ET92
ENSG00000130703ENST00000448156H0Y7X4
ENSG00000130703ENST00000618509A0A087WVV0
ENSG00000130703ENST00000622332A0A087WTV1
ENSG00000130703ENST00000642516A0A2R8Y5R1
ENSG00000130703ENST00000642714A0A2R8Y362
ENSG00000130703ENST00000642932A0A2R8YFT0
ENSG00000130703ENST00000642957A0A2R8YG53
ENSG00000130703ENST00000643174A0A2R8Y429
ENSG00000130703ENST00000643412Q9H1P3
ENSG00000130703ENST00000643981Q9H1P3
ENSG00000130703ENST00000644189A0A2R8Y690
ENSG00000130703ENST00000644535A0A2R8YG59
ENSG00000130703ENST00000644702A0A2R8YD49
ENSG00000130703ENST00000644775A0A2R8YEX0
ENSG00000130703ENST00000645426A0A2R8YG95
ENSG00000130703ENST00000645442A0A2R8YDU7
ENSG00000130703ENST00000645520E7ET92
ENSG00000130703ENST00000646834A0A2R8Y5B9
ENSG00000130703ENST00000646968A0A2R8Y703

Expression (GTEx)

0
10
20
30
40
50
60

Pathways

PathwaySourceExternal ID
MetabolismREACTOMER-HSA-1430728
Metabolism of lipids and lipoproteinsREACTOMER-HSA-556833
Bile acid and bile salt metabolismREACTOMER-HSA-194068
Synthesis of bile acids and bile saltsREACTOMER-HSA-192105

Protein levels (Protein atlas)

Not detected
Low
Medium
High

References

Pubmed IDYearTitleCitations
387019542024OSBPL2 compound heterozygous variants cause dyschromatosis, ichthyosis, deafness and atopic disease syndrome.0
387019542024OSBPL2 compound heterozygous variants cause dyschromatosis, ichthyosis, deafness and atopic disease syndrome.0
338543102021Circ-OSBPL2 Contributes to Smoke-Related Chronic Obstructive Pulmonary Disease by Targeting miR-193a-5p/BRD4 Axis.8
341247952021ORP2 couples LDL-cholesterol transport to FAK activation by endosomal cholesterol/PI(4,5)P(2) exchange.20
338543102021Circ-OSBPL2 Contributes to Smoke-Related Chronic Obstructive Pulmonary Disease by Targeting miR-193a-5p/BRD4 Axis.8
341247952021ORP2 couples LDL-cholesterol transport to FAK activation by endosomal cholesterol/PI(4,5)P(2) exchange.20
316294752020Comparative transcriptome analysis of auditory OC-1 cells and zebrafish inner ear tissues in the absence of human OSBPL2 orthologues.5
329145032020ORP2, a cholesterol transporter, regulates angiogenic signaling in endothelial cells.8
316294752020Comparative transcriptome analysis of auditory OC-1 cells and zebrafish inner ear tissues in the absence of human OSBPL2 orthologues.5
329145032020ORP2, a cholesterol transporter, regulates angiogenic signaling in endothelial cells.8
30391516201925-hydroxycholesterol down-regulates oxysterol binding protein like 2 (OSBPL2) via the p53/SREBF2/NFYA signaling pathway.5
305811482019ORP2 Delivers Cholesterol to the Plasma Membrane in Exchange for Phosphatidylinositol 4, 5-Bisphosphate (PI(4,5)P(2)).68
305900842019ORP2 interacts with phosphoinositides and controls the subcellular distribution of cholesterol.18
308941432019A novel pathogenic variant in OSBPL2 linked to hereditary late-onset deafness in a Mongolian family.7
313568172019OSBPL2 deficiency upregulate SQLE expression increasing intracellular cholesterol and cholesteryl ester by AMPK/SP1 and SREBF2 signalling pathway.16

Citation

Dessen P

OSBPL2 (oxysterol binding protein like 2)

Atlas Genet Cytogenet Oncol Haematol. 2018-11-01

Online version: http://atlasgeneticsoncology.org/gene/57733/osbpl2-(oxysterol-binding-protein-like-2)