MCFD2 (multiple coagulation factor deficiency 2, ER cargo receptor complex subunit)

2019-04-01  

Identity

HGNC
LOCATION
2p21
LOCUSID
ALIAS
F5F8D,F5F8D2,LMAN1IP,SDNSF
FUSION GENES

Other Information

Locus ID:

NCBI: 90411
MIM: 607788
HGNC: 18451
Ensembl: ENSG00000180398

Variants:

dbSNP: 90411
ClinVar: 90411
TCGA: ENSG00000180398
COSMIC: MCFD2

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000180398ENST00000319466Q8NI22
ENSG00000180398ENST00000409105Q8NI22
ENSG00000180398ENST00000409147Q8NI22
ENSG00000180398ENST00000409207Q8NI22
ENSG00000180398ENST00000409218Q8NI22
ENSG00000180398ENST00000409800Q8NI22
ENSG00000180398ENST00000409913Q8NI22
ENSG00000180398ENST00000409973Q8NI22
ENSG00000180398ENST00000412438Q8NI22
ENSG00000180398ENST00000417180C9JTR4
ENSG00000180398ENST00000434262H7BZ18
ENSG00000180398ENST00000444761Q8NI22
ENSG00000180398ENST00000649435A0A3B3IU18

Expression (GTEx)

0
50
100
150
200

Pathways

PathwaySourceExternal ID
Metabolism of proteinsREACTOMER-HSA-392499
Post-translational protein modificationREACTOMER-HSA-597592
Asparagine N-linked glycosylationREACTOMER-HSA-446203
Transport to the Golgi and subsequent modificationREACTOMER-HSA-948021
ER to Golgi Anterograde TransportREACTOMER-HSA-199977
COPII (Coat Protein 2) Mediated Vesicle TransportREACTOMER-HSA-204005
Vesicle-mediated transportREACTOMER-HSA-5653656
Membrane TraffickingREACTOMER-HSA-199991
Cargo concentration in the ERREACTOMER-HSA-5694530

Protein levels (Protein atlas)

Not detected
Low
Medium
High

References

Pubmed IDYearTitleCitations
353228562022LMAN1-MCFD2 complex is a cargo receptor for the ER-Golgi transport of α1-antitrypsin.8
353228562022LMAN1-MCFD2 complex is a cargo receptor for the ER-Golgi transport of α1-antitrypsin.8
290825802018Combined deficiency of factors V and VIII by chance coinheritance of parahaemophilia and haemophilia A, but not by mutations of either LMAN1 or MCFD2, in a Japanese family.0
296795922018Multiple coagulation factor deficiency protein 2 as a crucial component in metastasis of human oral cancer.9
290825802018Combined deficiency of factors V and VIII by chance coinheritance of parahaemophilia and haemophilia A, but not by mutations of either LMAN1 or MCFD2, in a Japanese family.0
296795922018Multiple coagulation factor deficiency protein 2 as a crucial component in metastasis of human oral cancer.9
253547752014Combined FV and FVIII deficiency (F5F8D) in a Chinese family with a novel missense mutation in MCFD2 gene.1
253547752014Combined FV and FVIII deficiency (F5F8D) in a Chinese family with a novel missense mutation in MCFD2 gene.1
227641192013Inherited hematological disorders due to defects in coat protein (COP)II complex.9
236609672013Multiple coagulation factor deficiency protein 2 contains the ability to support stem cell self-renewal.3
237092262013Structural characterization of carbohydrate binding by LMAN1 protein provides new insight into the endoplasmic reticulum export of factors V (FV) and VIII (FVIII).35
238528242013Combined deficiency of coagulation factors V and VIII: an update.22
227641192013Inherited hematological disorders due to defects in coat protein (COP)II complex.9
236609672013Multiple coagulation factor deficiency protein 2 contains the ability to support stem cell self-renewal.3
237092262013Structural characterization of carbohydrate binding by LMAN1 protein provides new insight into the endoplasmic reticulum export of factors V (FV) and VIII (FVIII).35

Citation

Dessen P

MCFD2 (multiple coagulation factor deficiency 2, ER cargo receptor complex subunit)

Atlas Genet Cytogenet Oncol Haematol. 2019-04-01

Online version: http://atlasgeneticsoncology.org/gene/57847/mcfd2-(multiple-coagulation-factor-deficiency-2-er-cargo-receptor-complex-subunit)