C9orf72 (C9orf72-SMCR8 complex subunit)

2019-04-01  

Identity

HGNC
LOCATION
9p21.2
LOCUSID
ALIAS
ALSFTD,DENND9,DENNL72,FTDALS,FTDALS1
FUSION GENES

Other Information

Locus ID:

NCBI: 203228
MIM: 614260
HGNC: 28337
Ensembl: ENSG00000147894

Variants:

dbSNP: 203228
ClinVar: 203228
TCGA: ENSG00000147894
COSMIC: C9orf72

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000147894ENST00000379995Q96LT7
ENSG00000147894ENST00000379997Q96LT7
ENSG00000147894ENST00000380003Q96LT7
ENSG00000147894ENST00000619707Q96LT7
ENSG00000147894ENST00000644136A0A2R8Y5K2
ENSG00000147894ENST00000647196A0A2R8Y5U5

Expression (GTEx)

0
5
10
15
20
25
30
35
40
45
50

Protein levels (Protein atlas)

Not detected
Low
Medium
High

PharmGKB

Entity IDNameTypeEvidenceAssociationPKPDPMIDs
PA164713366Tumor necrosis factor alpha (TNF-alpha) inhibitorsChemicalClinicalAnnotationassociatedPD
PA443434Arthritis, RheumatoidDiseaseClinicalAnnotationassociatedPD

References

Pubmed IDYearTitleCitations
375254972024Pathogenesis underlying hexanucleotide repeat expansions in C9orf72 gene in amyotrophic lateral sclerosis.0
377523462024Artificial microRNA suppresses C9ORF72 variants and decreases toxic dipeptide repeat proteins in vivo.2
378612032024Assessment of risk of ALS conferred by the GGGGCC hexanucleotide repeat expansion in C9orf72 among first-degree relatives of patients with ALS carrying the repeat expansion.1
380996052024Analysis of normal C9orf72 repeat length as possible disease modifier in amyotrophic lateral sclerosis.0
382478692024ALS' Perfect Storm: C9orf72-Associated Toxic Dipeptide Repeats as Potential Multipotent Disruptors of Protein Homeostasis.0
382541092024Beyond C9orf72: repeat expansions and copy number variations as risk factors of amyotrophic lateral sclerosis across various populations.1
384318412024Neuromuscular organoids model spinal neuromuscular pathologies in C9orf72 amyotrophic lateral sclerosis.0
384699752024Distinct neural signatures of pulvinar in C9orf72 amyotrophic lateral sclerosis mutation carriers and noncarriers.1
385976822024Somatic and intergenerational G4C2 hexanucleotide repeat instability in a human C9orf72 knock-in mouse model.0
386417152024Abundant transcriptomic alterations in the human cerebellum of patients with a C9orf72 repeat expansion.0
387386372024Antisense RNA C9orf72 hexanucleotide repeat associated with amyotrophic lateral sclerosis and frontotemporal dementia forms a triplex-like structure and binds small synthetic ligand.0
375254972024Pathogenesis underlying hexanucleotide repeat expansions in C9orf72 gene in amyotrophic lateral sclerosis.0
377523462024Artificial microRNA suppresses C9ORF72 variants and decreases toxic dipeptide repeat proteins in vivo.2
378612032024Assessment of risk of ALS conferred by the GGGGCC hexanucleotide repeat expansion in C9orf72 among first-degree relatives of patients with ALS carrying the repeat expansion.1
380996052024Analysis of normal C9orf72 repeat length as possible disease modifier in amyotrophic lateral sclerosis.0

Citation

Dessen P

C9orf72 (C9orf72-SMCR8 complex subunit)

Atlas Genet Cytogenet Oncol Haematol. 2019-04-01

Online version: http://atlasgeneticsoncology.org/gene/57902/