ABHD12 (abhydrolase domain containing 12, lysophospholipase)

2014-11-01  

Identity

HGNC
LOCATION
20p11.21
LOCUSID
ALIAS
ABHD12A,BEM46L2,C20orf22,PHARC,dJ965G21.2,hABHD12
FUSION GENES

Other Information

Locus ID:

NCBI: 26090
MIM: 613599
HGNC: 15868
Ensembl: ENSG00000100997

Variants:

dbSNP: 26090
ClinVar: 26090
TCGA: ENSG00000100997
COSMIC: ABHD12

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000100997ENST00000339157Q8N2K0
ENSG00000100997ENST00000376542Q8N2K0
ENSG00000100997ENST00000450393Q5T712
ENSG00000100997ENST00000461204I3L380
ENSG00000100997ENST00000465694I3L206
ENSG00000100997ENST00000471287I3L440
ENSG00000100997ENST00000491682I3L294
ENSG00000100997ENST00000576316I3L1V0

Expression (GTEx)

0
50
100
150

Pathways

PathwaySourceExternal ID
HemostasisREACTOMER-HSA-109582
Platelet activation, signaling and aggregationREACTOMER-HSA-76002
Effects of PIP2 hydrolysisREACTOMER-HSA-114508
Arachidonate production from DAGREACTOMER-HSA-426048
Signal TransductionREACTOMER-HSA-162582
Signaling by GPCRREACTOMER-HSA-372790
GPCR downstream signalingREACTOMER-HSA-388396
G alpha (q) signalling eventsREACTOMER-HSA-416476
Gastrin-CREB signalling pathway via PKC and MAPKREACTOMER-HSA-881907

Protein levels (Protein atlas)

Not detected
Low
Medium
High

References

Pubmed IDYearTitleCitations
342237972021Expanding the clinical phenotype in patients with disease causing variants associated with atypical Usher syndrome.10
345733852021The Phenotypic Spectrum of Patients with PHARC Syndrome Due to Variants in ABHD12: An Ophthalmic Perspective.6
342237972021Expanding the clinical phenotype in patients with disease causing variants associated with atypical Usher syndrome.10
345733852021The Phenotypic Spectrum of Patients with PHARC Syndrome Due to Variants in ABHD12: An Ophthalmic Perspective.6
323664052020ABHD12 Knockdown Suppresses Breast Cancer Cell Proliferation, Migration and Invasion.8
324628742020Mapping the Neuroanatomy of ABHD16A, ABHD12, and Lysophosphatidylserines Provides New Insights into the Pathophysiology of the Human Neurological Disorder PHARC.14
323664052020ABHD12 Knockdown Suppresses Breast Cancer Cell Proliferation, Migration and Invasion.8
324628742020Mapping the Neuroanatomy of ABHD16A, ABHD12, and Lysophosphatidylserines Provides New Insights into the Pathophysiology of the Human Neurological Disorder PHARC.14
309741962019A novel ABHD12 nonsense variant in Usher syndrome type 3 family with genotype-phenotype spectrum review.10
309741962019A novel ABHD12 nonsense variant in Usher syndrome type 3 family with genotype-phenotype spectrum review.10
302371672018Biochemical characterization of the PHARC-associated serine hydrolase ABHD12 reveals its preference for very-long-chain lipids.20
302371672018Biochemical characterization of the PHARC-associated serine hydrolase ABHD12 reveals its preference for very-long-chain lipids.20
278906732017Functional validation of ABHD12 mutations in the neurodegenerative disease PHARC.18
284486922017A complex homozygous mutation in ABHD12 responsible for PHARC syndrome discovered with NGS and review of the literature.11
278906732017Functional validation of ABHD12 mutations in the neurodegenerative disease PHARC.18

Citation

Dessen P

ABHD12 (abhydrolase domain containing 12, lysophospholipase)

Atlas Genet Cytogenet Oncol Haematol. 2014-11-01

Online version: http://atlasgeneticsoncology.org/gene/60049/abhd12-(abhydrolase-domain-containing-12-lysophospholipase)