ADAT3 (adenosine deaminase tRNA specific 3)

2014-11-01  

Identity

HGNC
LOCATION
19p13.3
LOCUSID
ALIAS
FWP005,MRT36,MST121,MSTP121,S863-5,TAD3

Other Information

Locus ID:

NCBI: 113179
MIM: 615302
HGNC: 25151
Ensembl: ENSG00000213638

Variants:

dbSNP: 113179
ClinVar: 113179
TCGA: ENSG00000213638
COSMIC: ADAT3

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000213638ENST00000329478D6W601
ENSG00000213638ENST00000454697C9JFC1

Expression (GTEx)

0
5
10
15

Pathways

PathwaySourceExternal ID
Gene ExpressionREACTOMER-HSA-74160
tRNA processingREACTOMER-HSA-72306
tRNA modification in the nucleus and cytosolREACTOMER-HSA-6782315

Protein levels (Protein atlas)

Not detected
Low
Medium
High

References

Pubmed IDYearTitleCitations
351186592022Genetic diagnosis in Sudanese and Tunisian families with syndromic intellectual disability through exome sequencing.1
351186592022Genetic diagnosis in Sudanese and Tunisian families with syndromic intellectual disability through exome sequencing.1
327639162020Identification and rescue of a tRNA wobble inosine deficiency causing intellectual disability disorder.8
327639162020Identification and rescue of a tRNA wobble inosine deficiency causing intellectual disability disorder.8
302965932019A new case confirming and expanding the phenotype spectrum of ADAT3-related intellectual disability syndrome.13
312630002019Formation of tRNA Wobble Inosine in Humans Is Disrupted by a Millennia-Old Mutation Causing Intellectual Disability.18
302965932019A new case confirming and expanding the phenotype spectrum of ADAT3-related intellectual disability syndrome.13
312630002019Formation of tRNA Wobble Inosine in Humans Is Disrupted by a Millennia-Old Mutation Causing Intellectual Disability.18
268429632016ADAT3-related intellectual disability: Further delineation of the phenotype.24
268429632016ADAT3-related intellectual disability: Further delineation of the phenotype.24
236202202013Mutation in ADAT3, encoding adenosine deaminase acting on transfer RNA, causes intellectual disability and strabismus.57
236202202013Mutation in ADAT3, encoding adenosine deaminase acting on transfer RNA, causes intellectual disability and strabismus.57

Citation

Dessen P

ADAT3 (adenosine deaminase tRNA specific 3)

Atlas Genet Cytogenet Oncol Haematol. 2014-11-01

Online version: http://atlasgeneticsoncology.org/gene/60153/adat3-(adenosine-deaminase-trna-specific-3)