CERKL (ceramide kinase like)

2014-11-01  

Identity

HGNC
LOCATION
2q31.3
LOCUSID
ALIAS
RP26
FUSION GENES

Other Information

Locus ID:

NCBI: 375298
MIM: 608381
HGNC: 21699
Ensembl: ENSG00000188452

Variants:

dbSNP: 375298
ClinVar: 375298
TCGA: ENSG00000188452
COSMIC: CERKL

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000188452ENST00000339098Q49MI3
ENSG00000188452ENST00000374967Q49MI3
ENSG00000188452ENST00000374969Q49MI3
ENSG00000188452ENST00000374970Q49MI3
ENSG00000188452ENST00000409440Q49MI3
ENSG00000188452ENST00000410087Q49MI3
ENSG00000188452ENST00000421817Q49MI3
ENSG00000188452ENST00000452174Q49MI3

Expression (GTEx)

0
5
10
15
20
25
30

Protein levels (Protein atlas)

Not detected
Low
Medium
High

PharmGKB

Entity IDNameTypeEvidenceAssociationPKPDPMIDs
PA161199368iloperidoneChemicalClinicalAnnotationassociatedPD18521091
PA447300Acquired Long QT Syndrome (aLQTS)DiseaseClinicalAnnotationassociatedPD18521091

References

Pubmed IDYearTitleCitations
373316552023CERKL-Associated Retinal Dystrophy: Genetics, Phenotype, and Natural History.1
373316552023CERKL-Associated Retinal Dystrophy: Genetics, Phenotype, and Natural History.1
328650752020CERKL mutation causing retinitis pigmentosa(RP) in Indian population - a genotype and phenotype correlation study.5
333228282020Genetic and Clinical Findings in an Ethnically Diverse Cohort with Retinitis Pigmentosa Associated with Pathogenic Variants in CERKL.3
328650752020CERKL mutation causing retinitis pigmentosa(RP) in Indian population - a genotype and phenotype correlation study.5
333228282020Genetic and Clinical Findings in an Ethnically Diverse Cohort with Retinitis Pigmentosa Associated with Pathogenic Variants in CERKL.3
302057352019CERKL regulates autophagy via the NAD-dependent deacetylase SIRT1.26
302057352019CERKL regulates autophagy via the NAD-dependent deacetylase SIRT1.26
290681402018A founder mutation in CERKL is a major cause of retinal dystrophy in Finland.16
290681402018A founder mutation in CERKL is a major cause of retinal dystrophy in Finland.16
245479292015Rod-Cone Dystrophy with Initially Preserved Visual Acuity Despite Early Macular Involvement Suggests Recessive CERKL Mutations.7
262966572015pVHL interacts with Ceramide kinase like (CERKL) protein and ubiquitinates it for oxygen dependent proteasomal degradation.10
245479292015Rod-Cone Dystrophy with Initially Preserved Visual Acuity Despite Early Macular Involvement Suggests Recessive CERKL Mutations.7
262966572015pVHL interacts with Ceramide kinase like (CERKL) protein and ubiquitinates it for oxygen dependent proteasomal degradation.10
247359782014CERKL interacts with mitochondrial TRX2 and protects retinal cells from oxidative stress-induced apoptosis.28

Citation

Dessen P

CERKL (ceramide kinase like)

Atlas Genet Cytogenet Oncol Haematol. 2014-11-01

Online version: http://atlasgeneticsoncology.org/gene/61738/cerkl-(ceramide-kinase-like)