CLCN1 (chloride voltage-gated channel 1)

2014-11-01  

Identity

HGNC
LOCATION
7q34
LOCUSID
ALIAS
CLC1
FUSION GENES

Other Information

Locus ID:

NCBI: 1180
MIM: 118425
HGNC: 2019
Ensembl: ENSG00000188037

Variants:

dbSNP: 1180
ClinVar: 1180
TCGA: ENSG00000188037
COSMIC: CLCN1

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000188037ENST00000343257P35523
ENSG00000188037ENST00000432192H7C0N6
ENSG00000188037ENST00000455478H7C1F4
ENSG00000188037ENST00000650516A0A3B3IU72

Expression (GTEx)

0
5
10
15

Pathways

PathwaySourceExternal ID
Transmembrane transport of small moleculesREACTOMER-HSA-382551
Ion channel transportREACTOMER-HSA-983712
Stimuli-sensing channelsREACTOMER-HSA-2672351

References

Pubmed IDYearTitleCitations
386442092024[A pedigree of myotonia congenita with a novel mutation p.F343C of the CLCN1 gene].0
387204152024Clinical and genetic characteristics of myotonia congenita in Chinese population.0
386442092024[A pedigree of myotonia congenita with a novel mutation p.F343C of the CLCN1 gene].0
387204152024Clinical and genetic characteristics of myotonia congenita in Chinese population.0
367202992023Coexistence of SCN4A and CLCN1 mutations in a family with atypical myotonic features: A clinical and functional study.1
367202992023Coexistence of SCN4A and CLCN1 mutations in a family with atypical myotonic features: A clinical and functional study.1
358667632022Sequence CLCN1 and SCN4A genes in patients with nondystrophic myotonia in Chinese people.1
358667632022Sequence CLCN1 and SCN4A genes in patients with nondystrophic myotonia in Chinese people.1
334645362021Association of Three Different Mutations in the CLCN1 Gene Modulating the Phenotype in a Consanguineous Family with Myotonia Congenita.0
335076322021Functional analysis of the F337C mutation in the CLCN1 gene associated with dominant myotonia congenita reveals an alteration of the macroscopic conductance and voltage dependence.2
336703072021Functional and Structural Characterization of ClC-1 and Na(v)1.4 Channels Resulting from CLCN1 and SCN4A Mutations Identified Alone and Coexisting in Myotonic Patients.2
345457122021Clinical and molecular characterization of five Chinese patients with autosomal recessive osteopetrosis.5
334645362021Association of Three Different Mutations in the CLCN1 Gene Modulating the Phenotype in a Consanguineous Family with Myotonia Congenita.0
335076322021Functional analysis of the F337C mutation in the CLCN1 gene associated with dominant myotonia congenita reveals an alteration of the macroscopic conductance and voltage dependence.2
336703072021Functional and Structural Characterization of ClC-1 and Na(v)1.4 Channels Resulting from CLCN1 and SCN4A Mutations Identified Alone and Coexisting in Myotonic Patients.2

Citation

Dessen P

CLCN1 (chloride voltage-gated channel 1)

Atlas Genet Cytogenet Oncol Haematol. 2014-11-01

Online version: http://atlasgeneticsoncology.org/gene/61852/meetings/haematological-explorer/