DGUOK (deoxyguanosine kinase)

2014-11-01  

Identity

HGNC
LOCATION
2p13.1
LOCUSID
ALIAS
MTDPS3,NCPH,PEOB4,dGK
FUSION GENES

Other Information

Locus ID:

NCBI: 1716
MIM: 601465
HGNC: 2858
Ensembl: ENSG00000114956

Variants:

dbSNP: 1716
ClinVar: 1716
TCGA: ENSG00000114956
COSMIC: DGUOK

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000114956ENST00000264093Q16854
ENSG00000114956ENST00000264093E5KSL5
ENSG00000114956ENST00000348222Q16854
ENSG00000114956ENST00000348222E5KSL6
ENSG00000114956ENST00000418996Q16854
ENSG00000114956ENST00000418996A0A0S2Z3N1
ENSG00000114956ENST00000629438Q16854
ENSG00000114956ENST00000629438A0A0S2Z3N1

Expression (GTEx)

0
10
20
30
40
50
60
70
80

Pathways

PathwaySourceExternal ID
Purine metabolismKEGGko00230
Purine metabolismKEGGhsa00230
Metabolic pathwaysKEGGhsa01100
MetabolismREACTOMER-HSA-1430728
Metabolism of nucleotidesREACTOMER-HSA-15869
Purine metabolismREACTOMER-HSA-73847
Purine salvageREACTOMER-HSA-74217

Protein levels (Protein atlas)

Not detected
Low
Medium
High

References

Pubmed IDYearTitleCitations
380270952023Case report: Two unexpected cases of DGUOK-related mitochondrial DNA depletion syndrome presenting with hyperinsulinemic hypoglycemia.0
380270952023Case report: Two unexpected cases of DGUOK-related mitochondrial DNA depletion syndrome presenting with hyperinsulinemic hypoglycemia.0
284938202017Deoxyguanosine kinase deficiency: a report of four patients.5
284938202017Deoxyguanosine kinase deficiency: a report of four patients.5
267735912016Potentially diagnostic electron paramagnetic resonance spectra elucidate the underlying mechanism of mitochondrial dysfunction in the deoxyguanosine kinase deficient rat model of a genetic mitochondrial DNA depletion syndrome.13
268746532016Recurrent recessive mutation in deoxyguanosine kinase causes idiopathic noncirrhotic portal hypertension.18
273245452016[Clinical features and DGUOK mutations of an infant with mitochondrial DNA depletion syndrome].2
267735912016Potentially diagnostic electron paramagnetic resonance spectra elucidate the underlying mechanism of mitochondrial dysfunction in the deoxyguanosine kinase deficient rat model of a genetic mitochondrial DNA depletion syndrome.13
268746532016Recurrent recessive mutation in deoxyguanosine kinase causes idiopathic noncirrhotic portal hypertension.18
273245452016[Clinical features and DGUOK mutations of an infant with mitochondrial DNA depletion syndrome].2
249406802014Mitochondrial thymidine kinase 2 but not deoxyguanosine kinase is up-regulated during the stationary growth phase of cultured cells.3
249406802014Mitochondrial thymidine kinase 2 but not deoxyguanosine kinase is up-regulated during the stationary growth phase of cultured cells.3
230431442012Next-generation sequencing reveals DGUOK mutations in adult patients with mitochondrial DNA multiple deletions.43
230431442012Next-generation sequencing reveals DGUOK mutations in adult patients with mitochondrial DNA multiple deletions.43
211077802011Post mortem identification of deoxyguanosine kinase (DGUOK) gene mutations combined with impaired glucose homeostasis and iron overload features in four infants with severe progressive liver failure.18

Citation

Dessen P

DGUOK (deoxyguanosine kinase)

Atlas Genet Cytogenet Oncol Haematol. 2014-11-01

Online version: http://atlasgeneticsoncology.org/gene/62459/dguok-(deoxyguanosine-kinase)