EIF2S3 (eukaryotic translation initiation factor 2 subunit gamma)

2014-11-01  

Identity

HGNC
LOCATION
Xp22.11
LOCUSID
ALIAS
EIF2,EIF2G,EIF2gamma,MEHMO,MRXSBRK,eIF-2gA
FUSION GENES

Other Information

Locus ID:

NCBI: 1968
MIM: 300161
HGNC: 3267
Ensembl: ENSG00000130741

Variants:

dbSNP: 1968
ClinVar: 1968
TCGA: ENSG00000130741
COSMIC: EIF2S3

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000130741ENST00000253039P41091
ENSG00000130741ENST00000423068H7BZU1

Expression (GTEx)

0
50
100
150
200
250

Pathways

PathwaySourceExternal ID
RNA transportKEGGko03013
RNA transportKEGGhsa03013
Metabolism of proteinsREACTOMER-HSA-392499
TranslationREACTOMER-HSA-72766
Eukaryotic Translation InitiationREACTOMER-HSA-72613
Cap-dependent Translation InitiationREACTOMER-HSA-72737
Formation of the ternary complex, and subsequently, the 43S complexREACTOMER-HSA-72695
Activation of the mRNA upon binding of the cap-binding complex and eIFs, and subsequent binding to 43SREACTOMER-HSA-72662
Translation initiation complex formationREACTOMER-HSA-72649
Ribosomal scanning and start codon recognitionREACTOMER-HSA-72702
GTP hydrolysis and joining of the 60S ribosomal subunitREACTOMER-HSA-72706
Recycling of eIF2:GDPREACTOMER-HSA-72731
L13a-mediated translational silencing of Ceruloplasmin expressionREACTOMER-HSA-156827
Gene ExpressionREACTOMER-HSA-74160
Transmembrane transport of small moleculesREACTOMER-HSA-382551
ABC-family proteins mediated transportREACTOMER-HSA-382556

Protein levels (Protein atlas)

Not detected
Low
Medium
High

References

Pubmed IDYearTitleCitations
375070292023Binding of human Cdc123 to eIF2γ.0
375070292023Binding of human Cdc123 to eIF2γ.0
349992622022mRNA analysis revealed a novel pathogenic EIF2S3 variant causing MEHMO syndrome.0
349992622022mRNA analysis revealed a novel pathogenic EIF2S3 variant causing MEHMO syndrome.0
342323822021Eukaryotic initiation factor-2, gamma subunit, suppresses proliferation and regulates the cell cycle via the MAPK/ERK signaling pathway in acute myeloid leukemia.3
342323822021Eukaryotic initiation factor-2, gamma subunit, suppresses proliferation and regulates the cell cycle via the MAPK/ERK signaling pathway in acute myeloid leukemia.3
327993152020Novel pathogenic EIF2S3 missense variants causing clinically variable MEHMO syndrome with impaired eIF2γ translational function, and literature review.2
327993152020Novel pathogenic EIF2S3 missense variants causing clinically variable MEHMO syndrome with impaired eIF2γ translational function, and literature review.2
305176942019MEHMO syndrome mutation EIF2S3-I259M impairs initiator Met-tRNAiMet binding to eukaryotic translation initiation factor eIF2.14
308785992019Impaired EIF2S3 function associated with a novel phenotype of X-linked hypopituitarism with glucose dysregulation.19
305176942019MEHMO syndrome mutation EIF2S3-I259M impairs initiator Met-tRNAiMet binding to eukaryotic translation initiation factor eIF2.14
308785992019Impaired EIF2S3 function associated with a novel phenotype of X-linked hypopituitarism with glucose dysregulation.19
293036052018Neonatal hypoglycemia, early-onset diabetes and hypopituitarism due to the mutation in EIF2S3 gene causing MEHMO syndrome.12
293036052018Neonatal hypoglycemia, early-onset diabetes and hypopituitarism due to the mutation in EIF2S3 gene causing MEHMO syndrome.12
280551402017EIF2S3 Mutations Associated with Severe X-Linked Intellectual Disability Syndrome MEHMO.27

Citation

Dessen P

EIF2S3 (eukaryotic translation initiation factor 2 subunit gamma)

Atlas Genet Cytogenet Oncol Haematol. 2014-11-01

Online version: http://atlasgeneticsoncology.org/gene/62778/case-report-explorer/gene-explorer/