ERLEC1 (endoplasmic reticulum lectin 1)

2014-11-01  

Identity

HGNC
LOCATION
2p16.2
LOCUSID
ALIAS
C2orf30,CIM,CL24936,CL25084,HEL117,XTP3-B,XTP3TPB

Other Information

Locus ID:

NCBI: 27248
MIM: 611229
HGNC: 25222
Ensembl: ENSG00000068912

Variants:

dbSNP: 27248
ClinVar: 27248
TCGA: ENSG00000068912
COSMIC: ERLEC1

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000068912ENST00000185150Q96DZ1
ENSG00000068912ENST00000185150V9HWD3
ENSG00000068912ENST00000378239Q96DZ1
ENSG00000068912ENST00000405123Q96DZ1

Expression (GTEx)

0
50
100
150

Pathways

PathwaySourceExternal ID
Protein processing in endoplasmic reticulumKEGGko04141
Protein processing in endoplasmic reticulumKEGGhsa04141
HRD1/SEL1 ERAD complexKEGGhsa_M00403
HRD1/SEL1 ERAD complexKEGGM00403
DiseaseREACTOMER-HSA-1643685
Diseases of signal transductionREACTOMER-HSA-5663202
Hh mutants abrogate ligand secretionREACTOMER-HSA-5387390
Hh mutants that don't undergo autocatalytic processing are degraded by ERADREACTOMER-HSA-5362768
Disorders of transmembrane transportersREACTOMER-HSA-5619115
ABC transporter disordersREACTOMER-HSA-5619084
Defective CFTR causes cystic fibrosisREACTOMER-HSA-5678895
Signal TransductionREACTOMER-HSA-162582
Signaling by HedgehogREACTOMER-HSA-5358351
Hedgehog ligand biogenesisREACTOMER-HSA-5358346
Transmembrane transport of small moleculesREACTOMER-HSA-382551
ABC-family proteins mediated transportREACTOMER-HSA-382556

Protein levels (Protein atlas)

Not detected
Low
Medium
High

References

Pubmed IDYearTitleCitations
324423522020Identification of pathogenic variants of ERLEC1 in individuals with Class III malocclusion by exome sequencing.3
324423522020Identification of pathogenic variants of ERLEC1 in individuals with Class III malocclusion by exome sequencing.3
297065352018Redundant and Antagonistic Roles of XTP3B and OS9 in Decoding Glycan and Non-glycan Degrons in ER-Associated Degradation.26
297065352018Redundant and Antagonistic Roles of XTP3B and OS9 in Decoding Glycan and Non-glycan Degrons in ER-Associated Degradation.26
233566412013Endoplasmic reticulum lectin XTP3-B inhibits endoplasmic reticulum-associated degradation of a misfolded α1-antitrypsin variant.22
233566412013Endoplasmic reticulum lectin XTP3-B inhibits endoplasmic reticulum-associated degradation of a misfolded α1-antitrypsin variant.22
230974962012Unassembled CD147 is an endogenous endoplasmic reticulum-associated degradation substrate.56
230974962012Unassembled CD147 is an endogenous endoplasmic reticulum-associated degradation substrate.56
210627432011Mannose trimming is required for delivery of a glycoprotein from EDEM1 to XTP3-B and to late endoplasmic reticulum-associated degradation steps.33
214046212011[OS-9 and XTP3-B: lectins that regulate endoplasmic reticulum-associated degradation (ERAD)].0
210627432011Mannose trimming is required for delivery of a glycoprotein from EDEM1 to XTP3-B and to late endoplasmic reticulum-associated degradation steps.33
214046212011[OS-9 and XTP3-B: lectins that regulate endoplasmic reticulum-associated degradation (ERAD)].0
199176672010Human XTP3-B binds to alpha1-antitrypsin variant null(Hong Kong) via the C-terminal MRH domain in a glycan-dependent manner.23
211189622010Novel metastasis-related gene CIM functions in the regulation of multiple cellular stress-response pathways.16
199176672010Human XTP3-B binds to alpha1-antitrypsin variant null(Hong Kong) via the C-terminal MRH domain in a glycan-dependent manner.23

Citation

Dessen P

ERLEC1 (endoplasmic reticulum lectin 1)

Atlas Genet Cytogenet Oncol Haematol. 2014-11-01

Online version: http://atlasgeneticsoncology.org/gene/62894/erlec1-(endoplasmic-reticulum-lectin-1)