EXOSC8 (exosome component 8)

2014-11-01  

Identity

HGNC
LOCATION
13q13.3
LOCUSID
ALIAS
CIP3,EAP2,OIP2,PCH1C,RRP43,Rrp43p,bA421P11.3,p9

Other Information

Locus ID:

NCBI: 11340
MIM: 606019
HGNC: 17035
Ensembl: ENSG00000120699

Variants:

dbSNP: 11340
ClinVar: 11340
TCGA: ENSG00000120699
COSMIC: EXOSC8

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000120699ENST00000239893H7C5Z2
ENSG00000120699ENST00000389704Q96B26
ENSG00000120699ENST00000481013H7C581

Expression (GTEx)

0
10
20
30
40
50
60
70

Pathways

PathwaySourceExternal ID
RNA degradationKEGGko03018
RNA degradationKEGGhsa03018
Exosome, eukaryotesKEGGhsa_M00391
Exosome, eukaryotesKEGGM00391
Metabolism of proteinsREACTOMER-HSA-392499
Unfolded Protein Response (UPR)REACTOMER-HSA-381119
PERK regulates gene expressionREACTOMER-HSA-381042
ATF4 activates genesREACTOMER-HSA-380994
Gene ExpressionREACTOMER-HSA-74160
Deadenylation-dependent mRNA decayREACTOMER-HSA-429914
mRNA decay by 3' to 5' exoribonucleaseREACTOMER-HSA-429958
Regulation of mRNA stability by proteins that bind AU-rich elementsREACTOMER-HSA-450531
Butyrate Response Factor 1 (BRF1) binds and destabilizes mRNAREACTOMER-HSA-450385
Tristetraprolin (TTP, ZFP36) binds and destabilizes mRNAREACTOMER-HSA-450513
KSRP (KHSRP) binds and destabilizes mRNAREACTOMER-HSA-450604
rRNA processingREACTOMER-HSA-72312
Major pathway of rRNA processing in the nucleolus and cytosolREACTOMER-HSA-6791226
rRNA processing in the nucleus and cytosolREACTOMER-HSA-8868773

Protein levels (Protein atlas)

Not detected
Low
Medium
High

References

Pubmed IDYearTitleCitations
380172812024A missense variant in EXOSC8 causes exon skipping and expands the phenotypic spectrum of pontocerebellar hypoplasia type 1C.0
380172812024A missense variant in EXOSC8 causes exon skipping and expands the phenotypic spectrum of pontocerebellar hypoplasia type 1C.0
363480122022EXOSC8 promotes colorectal cancer tumorigenesis via regulating ribosome biogenesis-related processes.2
363480122022EXOSC8 promotes colorectal cancer tumorigenesis via regulating ribosome biogenesis-related processes.2
315486132020Comprehensive characterization of the rRNA metabolism-related genes in human cancer.33
315486132020Comprehensive characterization of the rRNA metabolism-related genes in human cancer.33
271931682016Altered RNA metabolism due to a homozygous RBM7 mutation in a patient with spinal motor neuropathy.26
271931682016Altered RNA metabolism due to a homozygous RBM7 mutation in a patient with spinal motor neuropathy.26
249894512014EXOSC8 mutations alter mRNA metabolism and cause hypomyelination with spinal muscular atrophy and cerebellar hypoplasia.70
249894512014EXOSC8 mutations alter mRNA metabolism and cause hypomyelination with spinal muscular atrophy and cerebellar hypoplasia.70
119299722002A protein subunit of human RNase P, Rpp14, and its interacting partner, OIP2, have 3'-->5' exoribonuclease activity.9
124192562002Protein-protein interactions between human exosome components support the assembly of RNase PH-type subunits into a six-membered PNPase-like ring.28
119299722002A protein subunit of human RNase P, Rpp14, and its interacting partner, OIP2, have 3'-->5' exoribonuclease activity.9
124192562002Protein-protein interactions between human exosome components support the assembly of RNase PH-type subunits into a six-membered PNPase-like ring.28

Citation

Dessen P

EXOSC8 (exosome component 8)

Atlas Genet Cytogenet Oncol Haematol. 2014-11-01

Online version: http://atlasgeneticsoncology.org/gene/62954/exosc8-(exosome-component-8)