GJA8 (gap junction protein alpha 8)

2014-11-01  

Identity

HGNC
LOCATION
1q21.2
LOCUSID
ALIAS
CAE,CAE1,CTRCT1,CX50,CZP1,MP70

Other Information

Locus ID:

NCBI: 2703
MIM: 600897
HGNC: 4281
Ensembl: ENSG00000121634

Variants:

dbSNP: 2703
ClinVar: 2703
TCGA: ENSG00000121634
COSMIC: GJA8

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000121634ENST00000369235P48165
ENSG00000121634ENST00000369235X5D7G1

Expression (GTEx)

0
5
10
15

Pathways

PathwaySourceExternal ID
Vesicle-mediated transportREACTOMER-HSA-5653656
Membrane TraffickingREACTOMER-HSA-199991
Gap junction trafficking and regulationREACTOMER-HSA-157858
Gap junction traffickingREACTOMER-HSA-190828
Gap junction assemblyREACTOMER-HSA-190861

Protein levels (Protein atlas)

Not detected
Low
Medium
High

References

Pubmed IDYearTitleCitations
380529062024Association of variants in GJA8 with familial acorea-microphthalmia-cataract syndrome.2
381453022024Human Cx50 Isoleucine177 prevents heterotypic docking and formation of functional gap junction channels with Cx43.1
380529062024Association of variants in GJA8 with familial acorea-microphthalmia-cataract syndrome.2
381453022024Human Cx50 Isoleucine177 prevents heterotypic docking and formation of functional gap junction channels with Cx43.1
362620712023Novel compound heterozygous variant of GJA8 gene in two siblings with congenital cataract mimics an autosomal recessive trait.0
362620712023Novel compound heterozygous variant of GJA8 gene in two siblings with congenital cataract mimics an autosomal recessive trait.0
351209232022Cataract-linked serine mutations in the gap junction protein connexin50 expose a sorting signal that promotes its lysosomal degradation.3
357265762022Identification of novel cis-mutations in the GJA8 gene in a 3-generation Iranian family with autosomal dominant congenital nuclear cataract.0
359804872022Identification and functional analysis of two GJA8 variants in Chinese families with eye anomalies.0
351209232022Cataract-linked serine mutations in the gap junction protein connexin50 expose a sorting signal that promotes its lysosomal degradation.3
357265762022Identification of novel cis-mutations in the GJA8 gene in a 3-generation Iranian family with autosomal dominant congenital nuclear cataract.0
359804872022Identification and functional analysis of two GJA8 variants in Chinese families with eye anomalies.0
342262952021Aging-dependent loss of GAP junction proteins Cx46 and Cx50 in the fiber cells of human and mouse lenses accounts for the diminished coupling conductance.8
347628672021Molecular mechanisms underlying enhanced hemichannel function of a cataract-associated Cx50 mutant.8
342262952021Aging-dependent loss of GAP junction proteins Cx46 and Cx50 in the fiber cells of human and mouse lenses accounts for the diminished coupling conductance.8

Citation

Dessen P

GJA8 (gap junction protein alpha 8)

Atlas Genet Cytogenet Oncol Haematol. 2014-11-01

Online version: http://atlasgeneticsoncology.org/gene/63795/gja8-(gap-junction-protein-alpha-8)