GP1BB (glycoprotein Ib platelet subunit beta)

2014-11-01  

Identity

HGNC
LOCATION
22q11.21
LOCUSID
ALIAS
BDPLT1,BS,CD42C,GPIBB,GPIbbeta

Other Information

Locus ID:

NCBI: 2812
MIM: 138720
HGNC: 4440
Ensembl: ENSG00000203618

Variants:

dbSNP: 2812
ClinVar: 2812
TCGA: ENSG00000203618
COSMIC: GP1BB

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000203618ENST00000366425P13224

Pathways

PathwaySourceExternal ID
ECM-receptor interactionKEGGko04512
Hematopoietic cell lineageKEGGko04640
ECM-receptor interactionKEGGhsa04512
Hematopoietic cell lineageKEGGhsa04640
Platelet activationKEGGhsa04611
HemostasisREACTOMER-HSA-109582
Platelet Adhesion to exposed collagenREACTOMER-HSA-75892
Platelet activation, signaling and aggregationREACTOMER-HSA-76002
GP1b-IX-V activation signallingREACTOMER-HSA-430116
Platelet Aggregation (Plug Formation)REACTOMER-HSA-76009
Formation of Fibrin Clot (Clotting Cascade)REACTOMER-HSA-140877
Intrinsic Pathway of Fibrin Clot FormationREACTOMER-HSA-140837

PharmGKB

Entity IDNameTypeEvidenceAssociationPKPDPMIDs
PA26716COL3A1GenePathwayassociated20938371
PA26717COL4A1GenePathwayassociated20938371
PA26718COL4A2GenePathwayassociated20938371
PA33384PLCB1GenePathwayassociated20938371
PA33393PLCG2GenePathwayassociated20938371
PA35041COL1A1GenePathwayassociated20938371
PA35042COL1A2GenePathwayassociated20938371

References

Pubmed IDYearTitleCitations
365396142023GP1BB c.179C > T is the most frequent cause of monoallelic Bernard-Soulier syndrome in the Italian population after the Bolzano variant: a report of two new families.0
365396142023GP1BB c.179C > T is the most frequent cause of monoallelic Bernard-Soulier syndrome in the Italian population after the Bolzano variant: a report of two new families.0
338139862022A novel frameshift GP1BB mutation causes autosomal dominant macrothrombocytopenia with decreased vWF receptor expression but normal platelet aggregation.1
361730172022Biological, clinical features and modelling of heterozygous variants of glycoprotein Ib platelet subunit alpha (GP1BA) and glycoprotein Ib platelet subunit beta (GP1BB) genes responsible for constitutional thrombocytopenia.1
338139862022A novel frameshift GP1BB mutation causes autosomal dominant macrothrombocytopenia with decreased vWF receptor expression but normal platelet aggregation.1
361730172022Biological, clinical features and modelling of heterozygous variants of glycoprotein Ib platelet subunit alpha (GP1BA) and glycoprotein Ib platelet subunit beta (GP1BB) genes responsible for constitutional thrombocytopenia.1
346385292021A Novel Mutation in GP1BB Reveals the Role of the Cytoplasmic Domain of GPIbβ in the Pathophysiology of Bernard-Soulier Syndrome and GPIb-IX Complex Assembly.0
346385292021A Novel Mutation in GP1BB Reveals the Role of the Cytoplasmic Domain of GPIbβ in the Pathophysiology of Bernard-Soulier Syndrome and GPIb-IX Complex Assembly.0
319973072020High prevalence of the natural Asn89Asp mutation in the GP1BB gene associated with Bernard-Soulier syndrome in French patients from the genetic isolate of Reunion Island.2
332169772020A Sardinian founder mutation in glycoprotein Ib platelet subunit beta (GP1BB) that impacts thrombocytopenia.1
319973072020High prevalence of the natural Asn89Asp mutation in the GP1BB gene associated with Bernard-Soulier syndrome in French patients from the genetic isolate of Reunion Island.2
332169772020A Sardinian founder mutation in glycoprotein Ib platelet subunit beta (GP1BB) that impacts thrombocytopenia.1
295276742019New heterozygous variant in GP1BB gene is responsible for an inherited form of macrothrombocytopenia.2
305494032019Hemizygosity for the gene encoding glycoprotein Ibβ is not responsible for macrothrombocytopenia and bleeding in patients with 22q11 deletion syndrome.5
295276742019New heterozygous variant in GP1BB gene is responsible for an inherited form of macrothrombocytopenia.2

Citation

Dessen P

GP1BB (glycoprotein Ib platelet subunit beta)

Atlas Genet Cytogenet Oncol Haematol. 2014-11-01

Online version: http://atlasgeneticsoncology.org/gene/63916/gp1bb-(glycoprotein-ib-platelet-subunit-beta)