HPS4 (HPS4 biogenesis of lysosomal organelles complex 3 subunit 2)

2014-11-01  

Identity

HGNC
LOCATION
22q12.1
LOCUSID
ALIAS
BLOC3S2,LE
FUSION GENES

Other Information

Locus ID:

NCBI: 89781
MIM: 606682
HGNC: 15844
Ensembl: ENSG00000100099

Variants:

dbSNP: 89781
ClinVar: 89781
TCGA: ENSG00000100099
COSMIC: HPS4

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000100099ENST00000336873Q9NQG7
ENSG00000100099ENST00000398145Q9NQG7
ENSG00000100099ENST00000402105Q9NQG7
ENSG00000100099ENST00000422379F1LLU8
ENSG00000100099ENST00000429411F8VYA9
ENSG00000100099ENST00000439453F8WC53
ENSG00000100099ENST00000464362E5RG08

Expression (GTEx)

0
10
20
30
40
50
60
70

Pathways

PathwaySourceExternal ID
Vesicle-mediated transportREACTOMER-HSA-5653656
Membrane TraffickingREACTOMER-HSA-199991
RAB GEFs exchange GTP for GDP on RABsREACTOMER-HSA-8876198

Protein levels (Protein atlas)

Not detected
Low
Medium
High

References

Pubmed IDYearTitleCitations
235635892013An association study of the Hermansky-Pudlak syndrome type 4 gene in schizophrenic patients.5
241682252013Association of the Hermansky-Pudlak syndrome type 4 (HPS4) gene variants with cognitive function in patients with schizophrenia and healthy subjects.5
235635892013An association study of the Hermansky-Pudlak syndrome type 4 gene in schizophrenic patients.5
241682252013Association of the Hermansky-Pudlak syndrome type 4 (HPS4) gene variants with cognitive function in patients with schizophrenia and healthy subjects.5
230849912012BLOC-3 mutated in Hermansky-Pudlak syndrome is a Rab32/38 guanine nucleotide exchange factor.148
230849912012BLOC-3 mutated in Hermansky-Pudlak syndrome is a Rab32/38 guanine nucleotide exchange factor.148
218330172011Clinical, molecular, and cellular features of non-Puerto Rican Hermansky-Pudlak syndrome patients of Hispanic descent.12
218330172011Clinical, molecular, and cellular features of non-Puerto Rican Hermansky-Pudlak syndrome patients of Hispanic descent.12
200481592010Assembly of the biogenesis of lysosome-related organelles complex-3 (BLOC-3) and its interaction with Rab9.47
200481592010Assembly of the biogenesis of lysosome-related organelles complex-3 (BLOC-3) and its interaction with Rab9.47
184636832008Comprehensive analysis of oculocutaneous albinism among non-Hispanic caucasians shows that OCA1 is the most prevalent OCA type.44
184636832008Comprehensive analysis of oculocutaneous albinism among non-Hispanic caucasians shows that OCA1 is the most prevalent OCA type.44
164313082006Intestinal disease in Hermansky-Pudlak syndrome: occurrence of colitis and relation to genotype.27
164313082006Intestinal disease in Hermansky-Pudlak syndrome: occurrence of colitis and relation to genotype.27
126636592003The Hermansky-Pudlak syndrome 1 (HPS1) and HPS4 proteins are components of two complexes, BLOC-3 and BLOC-4, involved in the biogenesis of lysosome-related organelles.38

Citation

Dessen P

HPS4 (HPS4 biogenesis of lysosomal organelles complex 3 subunit 2)

Atlas Genet Cytogenet Oncol Haematol. 2014-11-01

Online version: http://atlasgeneticsoncology.org/gene/64418/hps4-(hps4-biogenesis-of-lysosomal-organelles-complex-3-subunit-2)