IQSEC2 (IQ motif and Sec7 domain ArfGEF 2)

2014-11-01  

Identity

HGNC
LOCATION
Xp11.22
LOCUSID
ALIAS
BRAG1,IQ-ArfGEF,MRX1,MRX18,MRX78

Other Information

Locus ID:

NCBI: 23096
MIM: 300522
HGNC: 29059
Ensembl: ENSG00000124313

Variants:

dbSNP: 23096
ClinVar: 23096
TCGA: ENSG00000124313
COSMIC: IQSEC2

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000124313ENST00000375365Q5JU85
ENSG00000124313ENST00000485377A0A1W2PPR2
ENSG00000124313ENST00000498281A0A1W2PPD3
ENSG00000124313ENST00000638521A0A1W2PRJ5
ENSG00000124313ENST00000638583A0A1W2PQP8
ENSG00000124313ENST00000638630A0A1W2PR18
ENSG00000124313ENST00000638869A0A1W2PPU7
ENSG00000124313ENST00000639161Q5JU85
ENSG00000124313ENST00000639485A0A1W2PR10
ENSG00000124313ENST00000639642A0A1W2PQ34
ENSG00000124313ENST00000639796A0A1W2PQS2
ENSG00000124313ENST00000640005A0A1W2PPE7
ENSG00000124313ENST00000640694A0A1W2PR28
ENSG00000124313ENST00000642864Q5JU85

Expression (GTEx)

0
5
10
15
20
25
30
35
40

Pathways

PathwaySourceExternal ID
EndocytosisKEGGko04144
EndocytosisKEGGhsa04144

References

Pubmed IDYearTitleCitations
370787452024Molecular modeling of ARF6 dysregulation caused by mutations in IQSEC2.0
370787452024Molecular modeling of ARF6 dysregulation caused by mutations in IQSEC2.0
369024142023Molecular Insights into IQSEC2 Disease.3
377877652023Ca2+-induced release of IQSEC2/BRAG1 autoinhibition under physiological and pathological conditions.1
369024142023Molecular Insights into IQSEC2 Disease.3
377877652023Ca2+-induced release of IQSEC2/BRAG1 autoinhibition under physiological and pathological conditions.1
353447482022Characterization of spontaneous seizures and EEG abnormalities in a mouse model of the human A350V IQSEC2 mutation and identification of a possible target for precision medicine based therapy.4
353477022022IQSEC2-related encephalopathy in males due to missense variants in the pleckstrin homology domain.4
360127612022Differences in Expression of IQSEC2 Transcript Isoforms in Male and Female Cases with Loss of Function Variants and Neurodevelopmental Disorder.2
364444372022[Genotypes and phenotypes of IQSEC2 gene variants related epilepsy].0
353447482022Characterization of spontaneous seizures and EEG abnormalities in a mouse model of the human A350V IQSEC2 mutation and identification of a possible target for precision medicine based therapy.4
353477022022IQSEC2-related encephalopathy in males due to missense variants in the pleckstrin homology domain.4
360127612022Differences in Expression of IQSEC2 Transcript Isoforms in Male and Female Cases with Loss of Function Variants and Neurodevelopmental Disorder.2
364444372022[Genotypes and phenotypes of IQSEC2 gene variants related epilepsy].0
333681942021IQSEC2 disorder: A new disease entity or a Rett spectrum continuum?10

Citation

Dessen P

IQSEC2 (IQ motif and Sec7 domain ArfGEF 2)

Atlas Genet Cytogenet Oncol Haematol. 2014-11-01

Online version: http://atlasgeneticsoncology.org/gene/64659/iqsec2-(iq-motif-and-sec7-domain-arfgef-2)