JPH2 (junctophilin 2)

2014-11-01  

Identity

HGNC
LOCATION
20q13.12
LOCUSID
ALIAS
CMH17,JP-2,JP2

Other Information

Locus ID:

NCBI: 57158
MIM: 605267
HGNC: 14202
Ensembl: ENSG00000149596

Variants:

dbSNP: 57158
ClinVar: 57158
TCGA: ENSG00000149596
COSMIC: JPH2

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000149596ENST00000342272Q9BR39
ENSG00000149596ENST00000372980Q9BR39

Expression (GTEx)

0
50
100
150

Protein levels (Protein atlas)

Not detected
Low
Medium
High

References

Pubmed IDYearTitleCitations
348613822023One gene, two modes of inheritance, four diseases: A systematic review of the cardiac manifestation of pathogenic variants in JPH2-encoded junctophilin-2.4
349654742023Editorial commentary: Genomic and precision medicine provides deeper insights into the genetic basis of diverse JPH2-mediated phenotypes.0
348613822023One gene, two modes of inheritance, four diseases: A systematic review of the cardiac manifestation of pathogenic variants in JPH2-encoded junctophilin-2.4
349654742023Editorial commentary: Genomic and precision medicine provides deeper insights into the genetic basis of diverse JPH2-mediated phenotypes.0
350893222022Junctophilins 1, 2, and 3 all support voltage-induced Ca2+ release despite considerable divergence.7
352386592022Structures of the junctophilin/voltage-gated calcium channel interface reveal hot spot for cardiomyopathy mutations.12
350893222022Junctophilins 1, 2, and 3 all support voltage-induced Ca2+ release despite considerable divergence.7
352386592022Structures of the junctophilin/voltage-gated calcium channel interface reveal hot spot for cardiomyopathy mutations.12
330924642021Interaction of the Joining Region in Junctophilin-2 With the L-Type Ca(2+) Channel Is Pivotal for Cardiac Dyad Assembly and Intracellular Ca(2+) Dynamics.34
340623902021Sequence determinants of human junctophilin-2 protein nuclear localization and phase separation.4
330924642021Interaction of the Joining Region in Junctophilin-2 With the L-Type Ca(2+) Channel Is Pivotal for Cardiac Dyad Assembly and Intracellular Ca(2+) Dynamics.34
340623902021Sequence determinants of human junctophilin-2 protein nuclear localization and phase separation.4
325921072020Nuclear localization of a novel calpain-2 mediated junctophilin-2 C-terminal cleavage peptide promotes cardiomyocyte remodeling.29
325921072020Nuclear localization of a novel calpain-2 mediated junctophilin-2 C-terminal cleavage peptide promotes cardiomyocyte remodeling.29
312173592019Junctophilin-2 expression rescues atrial dysfunction through polyadic junctional membrane complex biogenesis.16

Citation

Dessen P

JPH2 (junctophilin 2)

Atlas Genet Cytogenet Oncol Haematol. 2014-11-01

Online version: http://atlasgeneticsoncology.org/gene/64725/jph2-(junctophilin-2)