KCNC1 (potassium voltage-gated channel subfamily C member 1)

2014-11-01  

Identity

HGNC
LOCATION
11p15.1
LOCUSID
ALIAS
EPM7,KV3.1,KV4,NGK2

Other Information

Locus ID:

NCBI: 3746
MIM: 176258
HGNC: 6233
Ensembl: ENSG00000129159

Variants:

dbSNP: 3746
ClinVar: 3746
TCGA: ENSG00000129159
COSMIC: KCNC1

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000129159ENST00000265969P48547
ENSG00000129159ENST00000379472P48547
ENSG00000129159ENST00000638366A0A1W2PNN0
ENSG00000129159ENST00000638825A0A1W2PPN9
ENSG00000129159ENST00000639325A0A1W2PRL7
ENSG00000129159ENST00000639495A0A1W2PPT0
ENSG00000129159ENST00000640318A0A1W2PNZ3
ENSG00000129159ENST00000640461A0A1W2PP60
ENSG00000129159ENST00000640909A0A1W2PPX0

Expression (GTEx)

0
10
20
30
40
50
60
70
80
90
100

Pathways

PathwaySourceExternal ID
Neuronal SystemREACTOMER-HSA-112316
Potassium ChannelsREACTOMER-HSA-1296071
Voltage gated Potassium channelsREACTOMER-HSA-1296072

Protein levels (Protein atlas)

Not detected
Low
Medium
High

References

Pubmed IDYearTitleCitations
364193482023A KCNC1-related neurological disorder due to gain of Kv3.1 function.4
364193482023A KCNC1-related neurological disorder due to gain of Kv3.1 function.4
358405802022Cryo-EM structure of the human Kv3.1 channel reveals gating control by the cytoplasmic T1 domain.14
358405802022Cryo-EM structure of the human Kv3.1 channel reveals gating control by the cytoplasmic T1 domain.14
333499182021Genetic diagnosis of infantile-onset epilepsy in the clinic: Application of whole-exome sequencing following epilepsy gene panel testing.11
337355262021Progressive myoclonus epilepsy KCNC1 variant causes a developmental dendritopathy.5
341057342021Methylation gene KCNC1 is associated with overall survival in patients with seminoma.3
342327912021A KCNC1 mutation in epilepsy of infancy with focal migrating seizures produces functional channels that fail to be regulated by PKC phosphorylation.3
348301722021Cross Pharmacological, Biochemical and Computational Studies of a Human Kv3.1b Inhibitor from Androctonus australis Venom.0
333499182021Genetic diagnosis of infantile-onset epilepsy in the clinic: Application of whole-exome sequencing following epilepsy gene panel testing.11
337355262021Progressive myoclonus epilepsy KCNC1 variant causes a developmental dendritopathy.5
341057342021Methylation gene KCNC1 is associated with overall survival in patients with seminoma.3
342327912021A KCNC1 mutation in epilepsy of infancy with focal migrating seizures produces functional channels that fail to be regulated by PKC phosphorylation.3
348301722021Cross Pharmacological, Biochemical and Computational Studies of a Human Kv3.1b Inhibitor from Androctonus australis Venom.0
317321082020Mechanisms Underlying the Hyperexcitability of CA3 and Dentate Gyrus Hippocampal Neurons Derived From Patients With Bipolar Disorder.22

Citation

Dessen P

KCNC1 (potassium voltage-gated channel subfamily C member 1)

Atlas Genet Cytogenet Oncol Haematol. 2014-11-01

Online version: http://atlasgeneticsoncology.org/gene/64766/kcnc1-(potassium-voltage-gated-channel-subfamily-c-member-1)