KCNV2 (potassium voltage-gated channel modifier subfamily V member 2)

2014-11-01  

Identity

HGNC
LOCATION
9p24.2
LOCUSID
ALIAS
KV11.1,Kv8.2,RCD3B

Other Information

Locus ID:

NCBI: 169522
MIM: 607604
HGNC: 19698
Ensembl: ENSG00000168263

Variants:

dbSNP: 169522
ClinVar: 169522
TCGA: ENSG00000168263
COSMIC: KCNV2

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000168263ENST00000382082Q8TDN2

Expression (GTEx)

0
5
10
15

Pathways

PathwaySourceExternal ID
Neuronal SystemREACTOMER-HSA-112316
Potassium ChannelsREACTOMER-HSA-1296071
Voltage gated Potassium channelsREACTOMER-HSA-1296072

Protein levels (Protein atlas)

Not detected
Low
Medium
High

References

Pubmed IDYearTitleCitations
378527402024KCNV2-associated retinopathy: genotype-phenotype correlations - KCNV2 study group report 3.0
378527402024KCNV2-associated retinopathy: genotype-phenotype correlations - KCNV2 study group report 3.0
362784092023Initial diagnoses of patients found to be homozygous for a KCNV2 founder mutation on the Arabian Peninsula (c.427G>T; p.Glu143*).1
362784092023Initial diagnoses of patients found to be homozygous for a KCNV2 founder mutation on the Arabian Peninsula (c.427G>T; p.Glu143*).1
337065762022Cone dystrophy with supernormal rod responses: A rare KCNV2 gene variant.1
337065762022Cone dystrophy with supernormal rod responses: A rare KCNV2 gene variant.1
333098132021KCNV2-Associated Retinopathy: Genetics, Electrophysiology, and Clinical Course-KCNV2 Study Group Report 1.9
337370312021KCNV2-Associated Retinopathy: Detailed Retinal Phenotype and Structural Endpoints-KCNV2 Study Group Report 2.5
339602802021A novel KCNV2 mutation in a patient taking hydroxychloroquine associated with cone dystrophy with supernormal rod response.1
340630022021Molecular, Cellular and Functional Changes in the Retinas of Young Adult Mice Lacking the Voltage-Gated K(+) Channel Subunits Kv8.2 and K2.1.4
345359712021Compound heterozygous KCNV2 variants contribute to cone dystrophy with supernormal rod responses in a Chinese family.1
333098132021KCNV2-Associated Retinopathy: Genetics, Electrophysiology, and Clinical Course-KCNV2 Study Group Report 1.9
337370312021KCNV2-Associated Retinopathy: Detailed Retinal Phenotype and Structural Endpoints-KCNV2 Study Group Report 2.5
339602802021A novel KCNV2 mutation in a patient taking hydroxychloroquine associated with cone dystrophy with supernormal rod response.1
340630022021Molecular, Cellular and Functional Changes in the Retinas of Young Adult Mice Lacking the Voltage-Gated K(+) Channel Subunits Kv8.2 and K2.1.4

Citation

Dessen P

KCNV2 (potassium voltage-gated channel modifier subfamily V member 2)

Atlas Genet Cytogenet Oncol Haematol. 2014-11-01

Online version: http://atlasgeneticsoncology.org/gene/64815/kcnv2-(potassium-voltage-gated-channel-modifier-subfamily-v-member-2)