NBEAL2 (neurobeachin like 2)

2014-11-01  

Identity

HGNC
LOCATION
3p21.31
LOCUSID
ALIAS
BDPLT4,GPS
FUSION GENES

Other Information

Locus ID:

NCBI: 23218
MIM: 614169
HGNC: 31928
Ensembl: ENSG00000160796

Variants:

dbSNP: 23218
ClinVar: 23218
TCGA: ENSG00000160796
COSMIC: NBEAL2

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000160796ENST00000416683H0Y764
ENSG00000160796ENST00000423436H7C408
ENSG00000160796ENST00000441027H7C354
ENSG00000160796ENST00000443829H7C3Y7
ENSG00000160796ENST00000450053Q6ZNJ1
ENSG00000160796ENST00000651747A0A494C1V1

Expression (GTEx)

0
50
100
150
200

Pathways

PathwaySourceExternal ID
Immune SystemREACTOMER-HSA-168256
Innate Immune SystemREACTOMER-HSA-168249
Neutrophil degranulationREACTOMER-HSA-6798695

Protein levels (Protein atlas)

Not detected
Low
Medium
High

References

Pubmed IDYearTitleCitations
382726772024The Neurobeachin-like 2 protein (NBEAL2) controls the homeostatic level of the ribosomal protein RPS6 in mast cells.0
382726772024The Neurobeachin-like 2 protein (NBEAL2) controls the homeostatic level of the ribosomal protein RPS6 in mast cells.0
373493392023NBEAL2 deficiency in humans leads to low CTLA-4 expression in activated conventional T cells.3
373493392023NBEAL2 deficiency in humans leads to low CTLA-4 expression in activated conventional T cells.3
333002702021Gray platelet syndrome: NBEAL2 mutations are associated with pathology beyond megakaryocyte and platelet function defects.2
333002702021Gray platelet syndrome: NBEAL2 mutations are associated with pathology beyond megakaryocyte and platelet function defects.2
323841412020The endoplasmic reticulum protein SEC22B interacts with NBEAL2 and is required for megakaryocyte α-granule biogenesis.9
323841412020The endoplasmic reticulum protein SEC22B interacts with NBEAL2 and is required for megakaryocyte α-granule biogenesis.9
311718122019Defective Zn(2+) homeostasis in mouse and human platelets with α- and δ-storage pool diseases.14
311718122019Defective Zn(2+) homeostasis in mouse and human platelets with α- and δ-storage pool diseases.14
291873802018Nbeal2 interacts with Dock7, Sec16a, and Vac14.11
298699352018NBEAL2 mutations and bleeding in patients with gray platelet syndrome.14
303542152018NBEAL2 (Neurobeachin-Like 2) Is Required for Retention of Cargo Proteins by α-Granules During Their Production by Megakaryocytes.21
291873802018Nbeal2 interacts with Dock7, Sec16a, and Vac14.11
298699352018NBEAL2 mutations and bleeding in patients with gray platelet syndrome.14

Citation

Dessen P

NBEAL2 (neurobeachin like 2)

Atlas Genet Cytogenet Oncol Haematol. 2014-11-01

Online version: http://atlasgeneticsoncology.org/gene/70708/nbeal2-(neurobeachin-like-2)