NHLRC1 (NHL repeat containing E3 ubiquitin protein ligase 1)

2014-11-01  

Identity

HGNC
LOCATION
6p22.3
LOCUSID
ALIAS
EPM2A,EPM2B,MALIN,bA204B7.2

Other Information

Locus ID:

NCBI: 378884
MIM: 608072
HGNC: 21576
Ensembl: ENSG00000187566

Variants:

dbSNP: 378884
ClinVar: 378884
TCGA: ENSG00000187566
COSMIC: NHLRC1

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000187566ENST00000340650Q6VVB1

Expression (GTEx)

0
1
2
3
4
5

Pathways

PathwaySourceExternal ID
Ubiquitin mediated proteolysisKEGGko04120
Ubiquitin mediated proteolysisKEGGhsa04120
MetabolismREACTOMER-HSA-1430728
Metabolism of carbohydratesREACTOMER-HSA-71387
Glucose metabolismREACTOMER-HSA-70326
Glycogen synthesisREACTOMER-HSA-3322077

References

Pubmed IDYearTitleCitations
355693912022Compound heterozygosity for novel variations of the NHLRC1 Gene in a family with Lafora disease.1
361426052022Identification of NHLRC1 as a Novel AKT Activator from a Lung Cancer Epigenome-Wide Association Study (EWAS).0
355693912022Compound heterozygosity for novel variations of the NHLRC1 Gene in a family with Lafora disease.1
361426052022Identification of NHLRC1 as a Novel AKT Activator from a Lung Cancer Epigenome-Wide Association Study (EWAS).0
341173732021The rare rs769301934 variant in NHLRC1 is a common cause of Lafora disease in Turkey.0
341173732021The rare rs769301934 variant in NHLRC1 is a common cause of Lafora disease in Turkey.0
317589572020Regulation of the autophagic PI3KC3 complex by laforin/malin E3-ubiquitin ligase, two proteins involved in Lafora disease.15
317589572020Regulation of the autophagic PI3KC3 complex by laforin/malin E3-ubiquitin ligase, two proteins involved in Lafora disease.15
261020342015Lafora disease proteins laforin and malin negatively regulate the HIPK2-p53 cell death pathway.4
264932152015The laforin/malin E3-ubiquitin ligase complex ubiquitinates pyruvate kinase M1/M2.13
266480322015Interdependence of laforin and malin proteins for their stability and functions could underlie the molecular basis of locus heterogeneity in Lafora disease.3
261020342015Lafora disease proteins laforin and malin negatively regulate the HIPK2-p53 cell death pathway.4
264932152015The laforin/malin E3-ubiquitin ligase complex ubiquitinates pyruvate kinase M1/M2.13
266480322015Interdependence of laforin and malin proteins for their stability and functions could underlie the molecular basis of locus heterogeneity in Lafora disease.3
240686152014Laforin-malin complex degrades polyglucosan bodies in concert with glycogen debranching enzyme and brain isoform glycogen phosphorylase.7

Citation

Dessen P

NHLRC1 (NHL repeat containing E3 ubiquitin protein ligase 1)

Atlas Genet Cytogenet Oncol Haematol. 2014-11-01

Online version: http://atlasgeneticsoncology.org/gene/70823/nhlrc1-(nhl-repeat-containing-e3-ubiquitin-protein-ligase-1)