NPRL3 (NPR3 like, GATOR1 complex subunit)

2014-11-01  

Identity

HGNC
LOCATION
16p13.3
LOCUSID
ALIAS
C16orf35,CGTHBA,FFEVF3,HS-40,MARE,NPR3,RMD11
FUSION GENES

Other Information

Locus ID:

NCBI: 8131
MIM: 600928
HGNC: 14124
Ensembl: ENSG00000103148

Variants:

dbSNP: 8131
ClinVar: 8131
TCGA: ENSG00000103148
COSMIC: NPRL3

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000103148ENST00000399953B7Z6Q0
ENSG00000103148ENST00000419636B1B1F5
ENSG00000103148ENST00000422814F8WDA5
ENSG00000103148ENST00000456528F8WEK7
ENSG00000103148ENST00000457916F8WBJ1
ENSG00000103148ENST00000468260A0A087WTD0
ENSG00000103148ENST00000483663F8WCB2
ENSG00000103148ENST00000611875Q12980
ENSG00000103148ENST00000620134Q12980
ENSG00000103148ENST00000621703A0A087WTE2
ENSG00000103148ENST00000622194A0A087WTP7

Expression (GTEx)

0
10
20
30
40
50
60

Pathways

PathwaySourceExternal ID
mTOR signaling pathwayKEGGko04150
mTOR signaling pathwayKEGGhsa04150

Protein levels (Protein atlas)

Not detected
Low
Medium
High

References

Pubmed IDYearTitleCitations
379020972024Phenotypic and genotypic characterization of NPRL3-related epilepsy: Two case reports and literature review.2
379020972024Phenotypic and genotypic characterization of NPRL3-related epilepsy: Two case reports and literature review.2
370712902023Functional characterization of novel NPRL3 mutations identified in three families with focal epilepsy.1
370995482023The clinical features of familial focal epilepsy with variable foci and NPRL3 gene variant.0
372597682023Seizure features and outcomes in 50 children with GATOR1 variants: A retrospective study, more favorable for epilepsy surgery.2
374918682023Refining the electroclinical spectrum of NPRL3-related epilepsy: A novel multiplex family and literature review.3
370712902023Functional characterization of novel NPRL3 mutations identified in three families with focal epilepsy.1
370995482023The clinical features of familial focal epilepsy with variable foci and NPRL3 gene variant.0
372597682023Seizure features and outcomes in 50 children with GATOR1 variants: A retrospective study, more favorable for epilepsy surgery.2
374918682023Refining the electroclinical spectrum of NPRL3-related epilepsy: A novel multiplex family and literature review.3
334610852021GATOR1-related focal cortical dysplasia in epilepsy surgery patients and their families: A possible gradient in severity?9
337499802021Hemimegalencephaly and intractable seizures associated with the NPRL3 gene variant in a newborn: A case report.9
334610852021GATOR1-related focal cortical dysplasia in epilepsy surgery patients and their families: A possible gradient in severity?9
337499802021Hemimegalencephaly and intractable seizures associated with the NPRL3 gene variant in a newborn: A case report.9
318988482020A human minisatellite hosts an alternative transcription start site for NPRL3 driving its expression in a repeat number-dependent manner.4

Citation

Dessen P

NPRL3 (NPR3 like, GATOR1 complex subunit)

Atlas Genet Cytogenet Oncol Haematol. 2014-11-01

Online version: http://atlasgeneticsoncology.org/gene/70949/nprl3-(npr3-like-gator1-complex-subunit)